MetaADEDB 2.0 @ LMMD
POEMS Syndrome
(UMLS:C0085404)
Definition:
A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62)
UMLS ID:
C0085404
MeSH ID:
D016878
Classification 1:
Name:
Nervous System Diseases
MeSH Tree Number(s):
C10.668.829.800.700
Classification 2:
Name:
Hemic and Lymphatic Diseases
MeSH Tree Number(s):
C15.378.147.780.750
Classification 3:
Name:
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
MeSH Tree Number(s):
C16.131.077.703
Classification 4:
Name:
Immune System Diseases
MeSH Tree Number(s):
C20.683.780.750
Synonym(s)
1.
POEMS Syndrome
2.
POEMS - Polyneuropathy organomegaly endocrinopathy monoclonal and skin changes
3.
POEMS syndrome
4.
Polyneuropathy organomegaly endocrinopathy monoclonal gammopathy and skin changes
5.
Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome
6.
Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes syndrome
7.
crow-fukase syndrome
8.
poem syndrome
9.
poems syndrome
Associated Drug(s)
NameNumber of ReportsReference(s)Data Source
1LenalidomideFAERS: 6US FAERS
2IndomethacinFAERS: 2US FAERS
3ClozapineFAERS: 1US FAERS
4FinasterideFAERS: 1US FAERS
5Fingolimod HydrochlorideFAERS: 1
Canada Vigilance: 1
Canada Vigilance
US FAERS
6GadoliniumFAERS: 1US FAERS
7PrednisoloneFAERS: 1US FAERS
8TadalafilFAERS: 1US FAERS
9ThalidomideFAERS: 1US FAERS
10ambrisentanFAERS: 1US FAERS
11Tamoxifen1548501CTD
Similar ADE(s)
NameSemantic Similarity
1Monoclonal Gammopathy of Undetermined Significance34.4%
2Heavy Chain Disease28.6%
3Cryoglobulinemia26.2%
4Multiple Myeloma25%
5Waldenstrom Macroglobulinemia22%
6Beckwith-Wiedemann Syndrome20.8%
7Wolf-Hirschhorn Syndrome20.8%
8Smith-Magenis syndrome20.4%
9Cauda Equina Syndrome19.8%
10Holoprosencephaly19.5%
11Guillain-Barre Syndrome19.1%
12Cri-du-Chat Syndrome18.9%
13Down Syndrome18.9%
14Trisomy 2118.9%
15Hypergammaglobulinemia18.8%
16Prune Belly Syndrome18.4%
17Waardenburg Syndrome18.4%
18Polyradiculoneuropathy18.4%
19Polyradiculoneuritis18.4%
20Protein S Deficiency18.4%
21Alstrom Syndrome16.9%
22Prader-Willi Syndrome16.8%
23Primary amyloidosis16.5%
24Antithrombin III Deficiency16.5%
25Protein C Deficiency16.5%
26Rubinstein-Taybi Syndrome16.4%
27CHARGE Syndrome16.2%
28Ectodermal Dysplasia16.2%
29Aplasia Cutis Congenita16.2%
30Mobius Syndrome15.4%
31Bloom Syndrome15.4%
32Brachial Plexus Neuritis15.2%
33Neuralgic Amyotrophy15.2%
34Polyradiculopathy14.7%
35Causalgia14.5%
36Complex Regional Pain Syndromes14.4%
37Transfusion Reaction14.4%
38Hypotensive Transfusion Reaction14.4%
39Agammaglobulinemia14.3%
40Charcot-Marie-Tooth Disease14.3%
41Nail-Patella Syndrome14.3%
42Hypoproteinemia13.8%
43Neuritis13.8%
44Polyneuritis13.8%
45Radiculitis13.8%
46Mononeuritis13.8%
47Mononeuropathies13.8%
48Brachial Plexus Neuropathies13.8%
49Radiculopathy13.8%
50Mononeuropathy Multiplex13.8%
51Nerve Root Compression13.8%
52Schnitzler Syndrome13.7%
53Tarsal Tunnel Syndrome13.3%
54Polycystic Kidney Diseases13.1%
55Marfan Syndrome13.1%
56Lymphoproliferative Disorders12.9%
57Lymphatic Abnormalities12.9%
58Polyradiculoneuropathy, Chronic Inflammatory Demyelinating12.9%
59Cockayne Syndrome12.9%
60Disseminated Intravascular Coagulation12.7%
61Aicardi's syndrome12.7%
62Peripheral Nerve Injuries12.5%
63Miller Fisher Syndrome12%
64Abnormalities, Drug-Induced12%
65Situs Inversus12%
66Isaacs syndrome11.7%
67Thrombocythemia, Essential11.7%
68Diabetic Neuropathies11.5%
69Diabetic Amyotrophy11.5%
70Diabetic Autonomic Neuropathy11.5%
71Thrombasthenia11.5%
72Neuralgia11.5%
73Neuropathic pain11.5%
74Kartagener Syndrome11.4%
75Carpal Tunnel Syndrome11.4%
76Stiff-Person Syndrome11.3%
77Autoimmune Lymphoproliferative Syndrome11.3%
78Sciatica11.3%
79Anencephaly11.3%
80Motor Neuron Disease11.2%
81Smith-Lemli-Opitz Syndrome11.1%
82Primary Ciliary Dyskinesia10.8%
83Dural Arteriovenous Fistula10.8%
84Acrodynia10.7%
85Eye Abnormalities10.3%
86Wiskott-Aldrich Syndrome10.3%
87Cardiovascular Abnormalities10.3%
88Hand-Arm Vibration Syndrome10.3%
89Afibrinogenemia10.2%
90Factor VII Deficiency10.2%
91Factor X Deficiency10.2%
92Factor XII Deficiency10.2%
93Hemophilia A10.2%
94Activated Protein C Resistance10.2%
95Factor II deficiency10.2%
96Factor VIII Deficiency10.2%
97Factor V deficiency10.2%
98Factor XI Deficiency10.2%
99Hypoprothrombinemias10.2%
100Refsum Disease10.2%
101Skin Abnormalities10.1%
102Congenital Microtia10.1%
103Anemia10%
104Blood Coagulation Disorders10%
105Blood Platelet Disorders10%
106Bone Marrow Diseases10%
107Hemorrhagic Disorders10%
108Leukocyte Disorders10%
109Methemoglobinemia10%
110Pancytopenia10%
111Polycythemia10%
112Sulfhemoglobinemia10%
113Thrombophilia10%
114Neuromuscular Junction Diseases10%
115Erythrocytosis10%
116Congenital diaphragmatic hernia9.9%
117Infectious Mononucleosis9.9%
118Cubital Tunnel Syndrome9.7%
119Polycystic Kidney, Autosomal Dominant9.7%
120Hydranencephaly9.4%
121Neural Tube Defects9.4%
122Tethered Cord Syndrome9.4%
123Iniencephaly9.4%
124Craniorachischisis9.4%
125Exencephaly9.4%
126Septo-Optic Dysplasia9.4%
127Cortical Dysplasia9.4%
128Malformations of Cortical Development9.4%
129Reflex Sympathetic Dystrophy9.3%
130Sciatic Neuropathy9.2%
131Ulnar Neuropathies9.2%
132Lesion of Sciatic Nerve9.2%
133Hypoalbuminemia9.2%
134Ulnar Neuritis9.2%
135Radial nerve compression9.2%
136Radial Tunnel Syndrome9.2%
137Peroneal Neuropathies9.2%
138Radial Neuropathy9.2%
139Median Neuropathy9.2%
140Sciatic Nerve Palsy9.2%
141Femoral Neuropathy9.2%
142Tibial Neuropathy9.2%
143Ulnar Nerve Palsy9.2%
144Radial nerve palsy9.2%
145Urogenital Abnormalities8.9%
146Anemia, Sickle Cell8.8%
147Thalassemia8.8%
148Autoimmune thrombocytopenia8.8%
149Immune thrombocytopenic purpura8.8%
150Maxillofacial Abnormalities8.7%
151Dandy-Walker Syndrome8.7%
152Dextrocardia8.6%
153Myopathy8.6%
154Myasthenia Gravis8.6%
155Lymphangiectasis, Intestinal8.5%
156Bone Marrow Neoplasms8.5%
157Vitamin K Deficiency8.4%
158Pregnancy Complications, Hematologic8.4%
159Hematologic Neoplasms8.4%
160Anemia, Neonatal8.3%
161Pelger-Huet Anomaly8.3%
162Myasthenic Syndromes, Congenital8.3%
163Zellweger Syndrome8.3%
164Central Nervous System Cysts8.3%
165Tumor Lysis Syndrome8.2%
166Thrombocytosis8.2%
167Neuritis, Autoimmune, Experimental8.2%
168Sezary Syndrome8.1%
169Basal Cell Nevus Syndrome8.1%
170Twins, Conjoined7.9%
171Poliomyelitis7.8%
172Hydrops Fetalis7.8%
173Chronic Fatigue Syndrome7.8%
174Thoracic Outlet Syndrome7.7%
175Anemia, Diamond-Blackfan7.7%
176Thrombocytopenic purpura7.6%
177Microcephaly7.5%
178Macrocephaly7.5%
179Xeroderma7.5%
180Classical Lissencephalies and Subcortical Band Heterotopias7.4%
181Williams Syndrome7.4%
182Polycythemia Vera7.3%
183Lymphoma7.1%
184Eosinophilia-Myalgia Syndrome7.1%
185Transfusion-Related Acute Lung Injury7.1%
186Amyloid Neuropathies, Familial7.1%
187Spinal Muscular Atrophy7.1%
188Progressive Muscular Atrophy7.1%
189Scimitar Syndrome7.1%
190Fragile X Syndrome7%
191Kernicterus7%
192Lambert-Eaton Myasthenic Syndrome7%
193Acrocephalosyndactylia6.9%
194Porencephaly6.9%
195Autoimmune Diseases6.8%
196Hypersensitivity6.8%
197Immunologic Deficiency Syndromes6.8%
198Genetic Diseases, Inborn6.8%
199Immune reconstitution syndrome6.8%
200Immune Reconstitution Inflammatory Syndrome6.8%
201Anophthalmos6.7%
202Anus, Imperforate6.7%
203Microphthalmos6.7%
204Limb Deformities, Congenital6.7%
205Craniofacial Abnormalities6.7%
206Anorectal Malformations6.7%
207Pseudoxanthoma Elasticum6.6%
208Lymphopenia6.6%
209Abnormalities, Radiation-Induced6.6%
210Tuberous Sclerosis6.6%
211Amyotrophic Lateral Sclerosis6.6%
212Progressive bulbar palsy6.6%
213Plasmacytoma6.6%
214Bulbar palsy6.6%
215Chronic granulomatous disease6.6%
216Meningomyelocele6.6%
217Spina Bifida6.6%
218Craniosynostosis6.5%
219Syndactyly6.5%
220Brachycephaly6.5%
221Hemoglobinuria, Paroxysmal6.5%
222Leukemoid Reaction6.5%
223Turner Syndrome6.5%
224Myotonic Dystrophy6.4%
225Sickle Cell Trait6.4%
226Purpura, Thrombotic Thrombocytopenic6.2%
227Cranial nerve diseases6.2%
228Demyelinating Diseases6.2%
229Demyelination6.2%
230Lymphatic Diseases6.2%
231Chronobiology Disorders6.2%
232Ichthyosis, X-Linked6%
233Retinal Dysplasia6%
234Aniridia6%
235Noonan Syndrome6%
236Anemia, Hemolytic5.9%
237Anemia, Macrocytic5.9%
238Eosinophilia5.9%
239Leukopenia5.9%
240Thrombocytopenia5.9%
241Leukostasis5.9%
242MYELODYSPLASTIC SYNDROME5.9%
243Ataxia Telangiectasia5.9%
244Epidermolysis Bullosa5.9%
245Myasthenia Gravis, Autoimmune, Experimental5.9%
246Cleft Palate5.8%
247Botulism5.8%
248neurofibroma5.8%
249Blepharophimosis5.8%
250Laryngostenosis5.8%
251Mouth Abnormalities5.8%
252Fetal Diseases5.7%
253Esophageal Atresia5.7%
254Intestinal Atresia5.7%
255Horseshoe Kidney5.7%
256Pectus excavatum5.7%
257Klippel-Feil Syndrome5.7%
258Muscular Dystrophy5.7%
259Gastroschisis5.7%
260Synostosis5.7%
261Acrodermatitis5.7%
262Gianotti-Crosti Syndrome5.7%
263Meningocele5.6%
264Encephalocele5.6%
265Jaw Abnormalities5.5%
266Job Syndrome5.5%
267Multiple System Atrophy5.4%
268Poland Syndrome5.4%
269Myotonia Congenita5.3%
270Fanconi Anemia5.3%
271Trauma, Nervous System5.3%
272Restless Legs Syndrome5.2%
273Acute Chest Syndrome5.2%
274Nervous System Neoplasms5.2%
275Neurologic Manifestations5.2%
276Neurotoxicity Syndromes5.2%
277Dermal Sinus5.1%
278Spina Bifida Cystica5.1%
279Spina Bifida Occulta5.1%
280Lissencephaly5.1%
281Polymicrogyria5.1%
282Pachygyria5.1%
283Schizencephaly5.1%
284Periventricular Nodular Heterotopia5.1%
285Klinefelter Syndrome5.1%
286Hodgkin Disease5.1%
287Lymphoma, Non-Hodgkin5.1%
288Cystic Fibrosis5.1%
289Leukemia, T-Cell5.1%
290Leukemia, B-Cell5.1%
291Muscular Dystrophy, Duchenne5.1%
292Arthrogryposis5.1%
293Choanal Atresia5.1%
294Tracheobronchomegaly5.1%
295Laryngocele5.1%
296Choledochal Cyst5%
297Hermaphroditism5%
298Disorders of Sex Development5%
299Cryptorchidism5%
300Leukocytosis5%
301Myositis5%
302Pleocytosis5%
303Myotonic Disorders5%
304Hypospadias5%
305Familial Periodic Paralysis5%
306Ocular Motility Disorders5%
307Cyclophoria5%
308Leukoencephalitis, Acute Hemorrhagic4.9%
309Amelia4.9%
310Arachnodactyly4.9%
311Ectopia Cordis4.9%
312Ectromelia4.9%
313Hemimelia4.9%
314Phocomelia4.9%
315Sirenomelia4.9%
316Polydactyly4.9%
317Brachydactyly4.9%
318Plagiocephaly4.9%
319Lower Extremity Deformities, Congenital4.9%
320Upper Extremity Deformities, Congenital4.9%
321Single umbilical artery4.9%
322Sjogren-Larsson Syndrome4.9%
323Subacute Combined Degeneration4.8%
324Glomerulonephritis, Membranoproliferative4.8%
325Neuromyelitis Optica4.8%
326Micrognathism4.6%
327Pierre Robin Syndrome4.6%
328Ophthalmoplegic Migraine4.6%
329Meconium Aspiration Syndrome4.5%
330Laryngomalacia4.5%
331Dystonia Musculorum Deformans4.5%
332Composite Lymphoma4.5%
333Sleep Wake Disorders4.5%
334Pectus carinatum4.5%
335Lymphangioleiomyomatosis4.5%
336Encephalomyelitis4.4%
337Xeroderma Pigmentosum4.4%
338Prion Diseases4.4%
339Autonomic Dysreflexia4.4%
340Bladder Exstrophy4.4%
341Epispadias4.4%
342Kallmann Syndrome4.4%
343Waterhouse-Friderichsen Syndrome4.4%
344Multicystic Dysplastic Kidney4.4%
345Myelitis, Transverse4.4%
346Hyperkeratosis, Epidermolytic4.4%
347Purpura, Hyperglobulinemic4.3%
348Antley-Bixler Syndrome Phenotype4.3%
349Fibromyalgia4.3%
350Medial Tibial Stress Syndrome4.3%
351Encephalomyelitis, Acute Disseminated4.3%
352Uveomeningoencephalitic Syndrome4.3%
353Mitochondrial Myopathies4.3%
354Hepatolenticular Degeneration4.3%
355Hemolytic-Uremic Syndrome4.3%
356Ecchymosis4.2%
357Petechiae4.2%
358Purpura4.2%
359Aortic coarctation4.2%
360Cor Triatriatum4.2%
361Coronary Vessel Anomalies4.2%
362Dental Enamel Hypoplasia4.2%
363Patent ductus arteriosus4.2%
364Ebstein Anomaly4.2%
365Heart Septal Defects4.2%
366Hypodontia4.2%
367Macrostomia4.2%
368Microstomia4.2%
369Multiple Sclerosis4.2%
370Tetralogy of Fallot4.2%
371Transposition of Great Vessels4.2%
372Hypoplastic Left Heart Syndrome4.2%
373May-Thurner Syndrome4.2%
374Retrognathia4.2%
375Craniofacial Dysostosis4.2%
376Leukemia, Plasma Cell4.2%
377Wolff-Parkinson-White Syndrome4.2%
378Lymphoma, Follicular4.2%
379T-Cell Lymphoma4.2%
380Mantle cell lymphoma4.2%
381Precursor B-Cell Lymphoblastic Leukemia-Lymphoma4.2%
382Leukemia, Large Granular Lymphocytic4.2%
383Precursor T-Cell Lymphoblastic Leukemia-Lymphoma4.2%
384Canavan Disease4.1%
385Alexander Disease4.1%
386Meningoencephalitis4.1%
387Vasculitis, Central Nervous System4.1%
388Hyperandrogenism4%
389Lupus Vasculitis, Central Nervous System4%
390Abdominal Cramps4%
391Amniotic Band Syndrome4%
392Asphyxia Neonatorum4%
393Immune Complex Diseases4%
394Infant, Premature, Diseases4%
395Parkinson Disease4%
396Antiphospholipid Syndrome4%
397Infantile Colic4%
398Latex allergy4%
399Welander Distal Myopathy4%
400Primary Myelofibrosis3.9%
401Agranulocytosis3.9%
402Anemia, Megaloblastic3.9%
403Lymphocytosis3.9%
404Myelofibrosis3.9%
405Myeloid Metaplasia3.9%
406Spinal Cord Injuries3.9%
407Hypereosinophilic syndrome3.9%
408bone marrow fibrosis3.9%
409Thrombotic Microangiopathies3.9%
410Prognathism3.9%
411Marchiafava-Bignami Disease3.9%
412Lewy Body Disease3.8%
413Asterixis3.8%
414Ballismus3.8%
415Congenital nystagmus3.8%
416Lafora Disease3.8%
417Unverricht-Lundborg Syndrome3.8%
418Adrenoleukodystrophy3.8%
419Huntington Disease3.7%
420Long QT Syndrome3.7%
421Platybasia3.7%
422Pneumocephalus3.7%
423Tricuspid Atresia3.7%
424Arrhythmogenic Right Ventricular Dysplasia3.7%
425Gonadal Dysgenesis3.7%
426Bronchomalacia3.7%
427Adrenogenital Syndrome3.7%
428Tracheomalacia3.7%
429Ovotesticular Disorders of Sex Development3.7%
430Lymphoma, T-Cell, Cutaneous3.7%
431Lymphoma, AIDS-Related3.7%
432Enteropathy-Associated T-Cell Lymphoma3.7%
433Primary Effusion Lymphoma3.7%
434Neurofibrosarcoma3.7%
435Progressive supranuclear palsy3.6%
436Toxoplasmosis, Congenital3.5%
437Angioedemas, Hereditary3.5%
438Aortopulmonary Septal Defect3.5%
439Double Outlet Right Ventricle3.5%
440Endocardial Cushion Defects3.5%
441Rett Syndrome3.5%
442Myocardial bridging3.5%
443Aorticopulmonary Septal Defect3.5%
444Menkes Kinky Hair Syndrome3.5%
445Striatonigral Degeneration3.5%
446Hypokalemic periodic paralysis3.5%
447Mycosis Fungoides3.4%
448Neoplastic Syndromes, Hereditary3.4%
449Lymphomatoid Papulosis3.4%
450Environmental Illness3.4%
451Plasmablastic lymphoma3.4%
452Neuronal Ceroid-Lipofuscinoses3.4%
453Sleep Disorders, Circadian Rhythm3.4%
454Lupus Erythematosus, Systemic3.4%
455Overlap syndrome3.4%
456Mucopolysaccharidosis II3.4%
457Addison Disease3.3%
458Adenitis3.3%
459Brain Diseases3.3%
460Dysautonomia3.3%
461Dyskinesia, Drug-Induced3.3%
462Histiocytosis3.3%
463Lymphadenitis3.3%
464Lymphangitis3.3%
465Lymphedema3.3%
466Meningitis3.3%
467Movement Disorders3.3%
468Multiple Epiphyseal Dysplasia3.3%
469Osteochondrodysplasias3.3%
470Pachymeningitis3.3%
471Pemphigus3.3%
472Persistent Fetal Circulation Syndrome3.3%
473Spinal Cord Diseases3.3%
474Splenic Diseases3.3%
475Thymus Hyperplasia3.3%
476Werner Syndrome3.3%
477Vagus Nerve Disorder3.3%
478Glossopharyngeal Neuralgia3.3%
479Pseudolymphoma3.3%
480Abducens Nerve Diseases3.3%
481Lymphadenopathy3.3%
482Heavy Metal Poisoning, Nervous System3.3%
483Autoimmune thyroiditis3.3%
484Tauopathies3.3%
485Primary Adrenal Insufficiency3.3%
486Trochlear Nerve Diseases3.3%
487Atypical Hemolytic Uremic Syndrome3.3%
488Neuroleptic Malignant Syndrome3.3%
489Myelinolysis, Central Pontine3.3%
490Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis3.3%
491Autoimmune hepatitis3.3%
492Opsoclonus-Myoclonus Syndrome3.3%
493Umbilical hernia3.3%
494Albinism3.3%
495Myelitis3.3%
496Myalgia3.3%
497Leukomalacia, Periventricular3.3%
498Polymyositis3.3%
499Epidural Abscess3.3%
500Olfactory Nerve Injuries3.3%
501Lymphomatoid Granulomatosis3.3%
502Leukemia, Myelomonocytic, Chronic3.3%
503Leukemia, Myeloid, Chronic, Atypical, BCR-ABL Negative3.3%
504MPTP Poisoning3.2%
505Truncus Arteriosus, Persistent3.1%
506Goldenhar Syndrome3.1%
507Shy-Drager Syndrome3.1%
508Friedreich Ataxia3.1%
509Mandibulofacial Dysostosis3%
510Romano-Ward Syndrome3%
511Multiple Sclerosis, Chronic Progressive3%
512Multiple Sclerosis, Relapsing-Remitting3%
513Akathisia, Drug-Induced3%
514Dermatitis, Atopic2.9%
515Duane Retraction Syndrome2.9%
516Dwarfism2.9%
517Asthma, Aspirin-Induced2.9%
518Neutropenia2.9%
519Eosinophilic Granuloma2.9%
520Facial Nerve Injuries2.9%
521Neonatal Abstinence Syndrome2.9%
522Mitochondrial Encephalomyopathies2.9%
523Horner Syndrome2.9%
524Burkitt Lymphoma2.9%
525Central Nervous System Infection2.9%
526Optic Neuropathy2.9%
527Leukoencephalopathy, Progressive Multifocal2.9%
528Latent Autoimmune Diabetes in Adults2.9%
529Dermatitis Herpetiformis2.9%
530Fetal Growth Retardation2.9%
531Serum Sickness2.9%
532Kounis Syndrome2.9%
533HIV Infections2.8%
534Osteogenesis Imperfecta2.8%
535Fetal Hypoxia2.8%
536Orbital Myositis2.8%
537Fetal Alcohol Spectrum Disorders2.8%
538Brain Injuries2.8%
539Brain Neoplasms2.8%
540Shwartzman Phenomenon2.8%
541Spinal Cord Neoplasms2.8%
542Syphilis, Congenital2.8%
543Pyomyositis2.8%
544Optic Atrophy, Hereditary, Leber2.8%
545Facial Nerve Diseases2.8%
546Craniocerebral Trauma2.8%
547Lymphocele2.8%
548Parasomnia2.8%
549Dyssomnias2.8%
550Hemangioma, Cavernous2.8%
551Scurvy2.8%
552Purpura Fulminans2.8%
553Vestibulocochlear Nerve Diseases2.8%
554Decerebrate State2.8%
555Hemiparesis2.8%
556Meningism2.8%
557Paresis2.8%
558Seizures2.8%
559Sensation Disorders2.8%
560Central Nervous System Neoplasms2.8%
561Complex partial seizures2.8%
562Monoparesis2.8%
563Neurogenic Inflammation2.8%
564Gait Disorders, Neurologic2.8%
565Neuromuscular Manifestations2.8%
566Thymus Neoplasms2.8%
567Sweating, Gustatory2.8%
568Auriculotemporal Syndrome2.8%
569Talipes2.8%
570Subdural Effusion2.7%
571Parkinsonian Disorders2.7%
572Nocturnal Myoclonus Syndrome2.7%
573Fabry Disease2.7%
574anaphylaxis2.6%
575Food Allergy2.6%
576Familial Mediterranean Fever2.6%
577Anaphylactic shock2.6%
578MELAS Syndrome2.6%
579Congenital clubfoot2.6%
580Vertical Talus2.6%
581Jet Lag Syndrome2.6%
582Limbic Encephalitis2.5%
583Rheumatoid Arthritis2.5%
584Juvenile arthritis2.5%
585Graves Disease2.5%
586Congenital Hyperinsulinism2.5%
587Brain Abscess2.5%
588Chorioamnionitis2.5%
589Ophthalmoplegia2.5%
590External Ophthalmoplegia2.5%
591Pulmonary Eosinophilia2.5%
592Eosinophilic Pneumonia2.5%
593Brain Diseases, Metabolic, Inborn2.5%
594Anti-Glomerular Basement Membrane Disease2.5%
595Pupil Disorders2.5%
596Neurobehavioral Manifestations2.5%
597Arteriovenous fistula2.4%
598Epilepsy, Post-Traumatic2.4%
599Febrile Neutropenia2.4%
600Leukemia, Myeloid, Chronic-Phase2.4%
601Galactosemias2.4%
602Urea Cycle Disorders, Inborn2.4%
603Tyrosinemias2.4%
604Anemia, Pernicious2.4%
605Paraneoplastic Encephalomyelitis2.4%
606Mucocutaneous Lymph Node Syndrome2.4%
607Scrapie2.4%
608Sturge-Weber Syndrome2.4%
609Vertigo2.4%
610Central Cord Syndrome2.4%
611Alcohol-Induced Disorders, Nervous System2.4%
612Presenile dementia2.3%
613Senile dementia2.3%
614Meningitis, Bacterial2.3%
615Meningitis, Fungal2.3%
616Glycogen storage disease type II2.3%
617Chorea2.3%
618Respiratory Hypersensitivity2.3%
619Vocal Cord Paralysis2.2%
620Paralysis, Obstetric2.2%
621Retinopathy of Prematurity2.2%
622Sick Building Syndrome2.2%
623Giant Cell Arteritis2.2%
624Multiple Chemical Sensitivity2.2%
625Temporal Arteritis2.2%
626Amino Acid Metabolism, Inborn Errors2.2%
627Carbohydrate Metabolism, Inborn Errors2.2%
628Metal Metabolism, Inborn Errors2.2%
629Progeria2.2%
630Urticaria2.2%
631Lysosomal Storage Diseases2.2%
632Vasculitis, Leukocytoclastic, Cutaneous2.2%
633Cytochrome-c Oxidase Deficiency2.2%
634Peroxisomal Disorders2.2%
635Bronchopulmonary Dysplasia2.2%
636HTLV-I Infections2.2%
637AIDS Dementia Complex2.2%
638Meige Syndrome2.2%
639Cerebral Ventriculitis2.2%
640Dementia, Vascular2.1%
641Brain Hemorrhage, Traumatic2.1%
642Voice Disorders2.1%
643Voice Disturbance2.1%
644Denys-Drash Syndrome2.1%
645Homocystinuria2.1%
646Amblyopia2.1%
647Leigh Disease2.1%
648Paraneoplastic Cerebellar Degeneration2%
649Cerebrospinal Fluid Otorrhea2%
650Cerebrospinal Fluid Rhinorrhea2%
651Gait Ataxia2%
652Niemann-Pick Disease, Type C2%
653Cerebellar Neoplasms2%
654Brain Death2%
655Coma, Post-Head Injury2%
656Akinetic Mutism2%
657Anoxic Encephalopathy2%
658Arachnoiditis2%
659Basal Ganglia Diseases2%
660Brain Damage, Chronic2%
661Cerebellar Diseases2%
662Elephantiasis2%
663Encephalitis2%
664Encephalomalacia2%
665Epilepsy2%
666Hydrocephalus2%
667Congenital Hydrocephalus2%
668Hypersplenism2%
669Hypothalamic Diseases2%
670Aseptic Meningitis2%
671Sarcoidosis2%
672Syringomyelia2%
673Thalamic Diseases2%
674Intracranial Hypertension2%
675Aura2%
676Leukoencephalopathy2%
677Essential Tremor2%
678Neuroaxonal Dystrophies2%
679Familial Tremor2%
680Headache Disorders2%
681Intracranial Hypotension2%
682Elephantiasis Nostras Verrucosa2%
683Brain Edema2%
684Brain Hypoxia2%
685Aqueductal Stenosis2%
686Pneumorrhachis2%
687Writer's Cramp2%
688Alcohol Withdrawal Seizures2%
689Ophthalmia Neonatorum2%
690Milk Allergy2%
691Wheat Hypersensitivity2%
692Carotid Artery Injuries2%
693Gaucher Disease1.9%
694Respiratory Distress Syndrome, Newborn1.9%
695Cutis Laxa1.9%
696Posterior Leukoencephalopathy Syndrome1.9%
697Posterior reversible encephalopathy syndrome1.9%
698Mastocytosis1.9%
699Retinitis Pigmentosa1.9%
700Pigmentary retinopathy1.9%
701Drug Eruptions1.9%
702Porokeratosis1.9%
703Keratoderma, Palmoplantar1.9%
704Granulomatosis with polyangiitis1.9%
705Dermatomyositis1.9%
706Creutzfeldt-Jakob disease1.9%
707Dermatitis, Allergic Contact1.9%
708Basal Ganglia Cerebrovascular Disease1.9%
709HIV Seropositivity1.9%
710Brain Injuries, Diffuse1.9%
711Traumatic Brain Injury1.9%
712Cerebellar Ataxia1.9%
713Supratentorial Neoplasms1.9%
714Torticollis1.9%
715Reflex, Abnormal1.8%
716Hyporeflexia1.8%
717Hyperreflexia1.8%
718Carbamoyl-Phosphate Synthase I Deficiency Disease1.8%
719Akathisia1.8%
720Restlessness1.8%
721Psychomotor Agitation1.8%
722Tuberculosis, Meningeal1.8%
723Mucopolysaccharidosis III1.8%
724Hyperphosphaturia1.8%
725Tay-Sachs Disease1.8%
726Kearns-Sayre syndrome1.7%
727Optic Nerve Glioma1.7%
728Alice in Wonderland Syndrome1.7%
729Brain Diseases, Metabolic1.7%
730Cerebrovascular Disorders1.7%
731Granuloma1.7%
732Histiocytic Disorders, Malignant1.7%
733Optic Atrophy1.7%
734Optic Neuritis1.7%
735Papilledema1.7%
736Splenic Infarction1.7%
737Splenic Neoplasms1.7%
738Strabismus1.7%
739Tolosa-Hunt Syndrome1.7%
740Porphyrias, Hepatic1.7%
741Cerebrovascular Insufficiency1.7%
742Arsenic Poisoning1.7%
743Dementia1.7%
744Central Nervous System Fungal Infections1.7%
745Conus Medullaris Syndrome1.7%
746Spinal Cord Vascular Diseases1.7%
747Acquired Immunodeficiency Syndrome1.6%
748AIDS related complex1.6%
749Facial Injuries1.6%
750Facial Neuralgia1.6%
751Histiocytosis, Langerhans-Cell1.6%
752Sleep Talking1.6%
753Manganese Poisoning1.6%
754Sleep Disorders, Intrinsic1.6%
755Orthostatic intolerance1.6%
756Peutz-Jeghers Syndrome1.6%
757Anosmia1.6%
758Ataxia1.6%
759Athetosis1.6%
760Catalepsy1.6%
761Dystonia1.6%
762Felty Syndrome1.6%
763Hemiplegia1.6%
764Locked-In Syndrome1.6%
765Meningeal Neoplasms1.6%
766Muscle Hypertonia1.6%
767Muscle hypotonia1.6%
768Myoclonus1.6%
769Myotonia1.6%
770Paraplegia1.6%
771Pseudobulbar Palsy1.6%
772Quadriplegia1.6%
773Spasm1.6%
774Spastic Paraplegia1.6%
775Status Epilepticus1.6%
776Taste Disorders1.6%
777Tremor1.6%
778Monoplegia1.6%
779Hypokinesia1.6%
780Paraparesis1.6%
781Bradykinesia1.6%
782Waxy flexibility1.6%
783Action Tremor1.6%
784Resting Tremor1.6%
785Dysosmia1.6%
786Quadriparesis1.6%
787Mercury Poisoning, Nervous System1.6%
788Olfaction Disorders1.6%
789Myokymia1.6%
790Lead Poisoning, Nervous System1.6%
791Vestibular Neuronitis1.6%
792Somatosensory Disorders1.6%
793Hyperkinesia1.6%
794Intention tremor1.6%
795Vertebral Artery Dissection1.6%
796Nesidioblastosis1.6%
797Vascular Headaches1.6%
798Lupus Nephritis1.6%
799Alkaptonuria1.6%
800Glycogen Storage Disease1.6%
801Hypophosphatasia1.6%
802Propionic acidemia1.6%
803Dihydropyrimidine Dehydrogenase Deficiency1.6%
804Cystinosis1.6%
805Amnesia, Transient Global1.6%
806Toxoplasmosis, Cerebral1.6%
807Mastocytosis, Systemic1.6%
808Hypoxia-Ischemia, Brain1.6%
809Gait Apraxia1.6%
810Myoclonic Epilepsy1.6%
811Epilepsy, Temporal Lobe1.6%
812Epilepsy, Rolandic1.6%
813Benign Rolandic Epilepsy1.6%
814Brain Concussion1.6%
815Tardive Dyskinesia1.6%
816Persistent Vegetative State1.6%
817Acoustic Neuroma1.5%
818Multiple Endocrine Neoplasia1.5%
819Pituitary Adenoma1.5%
820Pituitary Neoplasms1.5%
821AIDS-Related Opportunistic Infections1.5%
822Congenital Hypothyroidism1.5%
823HIV Wasting Syndrome1.5%
824Rheumatoid Vasculitis1.5%
825AIDS-Associated Nephropathy1.5%
826Vision Disorders1.4%
827Metamorphopsia1.4%
828Visual Impairment1.4%
829Splenic Rupture1.4%
830Optic Neuropathy, Ischemic1.4%
831Anterior Ischemic Optic Neuropathy1.4%
832Central Nervous System Bacterial Infections1.4%
833Facial Hemiatrophy1.4%
834Melkersson-Rosenthal Syndrome1.4%
835Meningitis, Cryptococcal1.4%
836Anisocoria1.4%
837Confusion1.4%
838Facial paralysis1.4%
839Lethargy1.4%
840Memory Disorders1.4%
841Muscle Cramp1.4%
842Perceptual Disorders1.4%
843Psychomotor Disorders1.4%
844Tonic Pupil1.4%
845Anhedonia1.4%
846Disorientation1.4%
847Facial Paresis1.4%
848Memory Loss1.4%
849Hemisensory Neglect1.4%
850Dysacusis1.4%
851Meningitis, Listeria1.4%
852Meningitis, Haemophilus1.4%
853Meningitis, Pneumococcal1.4%
854Frontotemporal dementia1.4%
855Angioedema1.4%
856Sleep Bruxism1.4%
857Hyaline Membrane Disease1.4%
858Muscular Atrophy1.4%
859Respiratory Paralysis1.4%
860Thymoma1.4%
861Tetany1.4%
862Hypolipoproteinemias1.4%
863Papillon-Lefevre Disease1.4%
864Acute Generalized Exanthematous Pustulosis1.4%
865Hyperlipidemia, Familial Combined1.4%
866Hyperlipoproteinemia Type III1.4%
867Diffuse Axonal Injury1.4%
868Brain Stem Neoplasms1.4%
869Basal Ganglia Hemorrhage1.4%
870Glycogen Storage Disease Type I1.4%
871Glycogen Storage Disease Type V1.4%
872Juvenile Myoclonic Epilepsy1.3%
873Myoclonic Epilepsies, Progressive1.3%
874Behcet Syndrome1.3%
875Subarachnoid Hemorrhage, Traumatic1.3%
876Carotid Artery, Internal, Dissection1.3%
877Sicca Syndrome1.3%
878Sjogren's Syndrome1.3%
879Cerebral Palsy1.3%
880Epilepsies, Partial1.3%
881Epilepsy, Generalized1.3%
882Lymphohistiocytosis, Hemophagocytic1.3%
883Pseudotumor Cerebri1.3%
884Hypertensive Encephalopathy1.3%
885Simple Partial Seizures1.3%
886Epilepsy, Reflex1.3%
887Erdheim-Chester Disease1.3%
888Postural Orthostatic Tachycardia Syndrome1.3%
889Headache Disorders, Primary1.3%
890Headache Disorders, Secondary1.3%
891Medication overuse headache1.3%
892Auditory Perceptual Disorders1.3%
893HIV-Associated Lipodystrophy Syndrome1.3%
894Subacute Sclerosing Panencephalitis1.3%
895Asthma1.3%
896Consciousness Disorders1.3%
897Mental Retardation1.3%
898Muscle Weakness1.3%
899Depressed Level of Consciousness1.3%
900Mental deficiency1.3%
901Intellectual Disability1.3%
902Bell Palsy1.3%
903Catatonia1.2%
904Herpes Zoster Oticus1.2%
905Aphonia1.2%
906Sleep Deprivation1.2%
907Dysphonia1.2%
908Pituitary Apoplexy1.2%
909Erythema Nodosum1.2%
910Lactose Intolerance1.2%
911Variegate Porphyria1.2%
912Acute intermittent porphyria1.2%
913Porphyria Cutanea Tarda1.2%
914Hyperhomocysteinemia1.2%
915Dermatitis, Photoallergic1.2%
916Renal Aminoacidurias1.2%
917Fanconi Syndrome1.2%
918Pseudohypoaldosteronism1.2%
919Brain Contusion1.2%
920Liddle Syndrome1.2%
921Brain Infarction1.2%
922Hyperlipoproteinemia Type IV1.2%
923Hyperlipoproteinemia Type V1.2%
924Asthma, Exercise-Induced1.2%
925Status Asthmaticus1.2%
926Putaminal Hemorrhage1.2%
927Hypoalphalipoproteinemias1.2%
928Choroid Plexus Papilloma1.2%
929Pituitary Diseases1.1%
930Infarction, Middle Cerebral Artery1.1%
931Infarction, Anterior Cerebral Artery1.1%
932Infarction, Posterior Cerebral Artery1.1%
933Gout1.1%
934Aspergillosis, Allergic Bronchopulmonary1.1%
935Multiple Endocrine Neoplasia Type 11.1%
936Pseudohypoparathyroidism1.1%
937Carotid Artery Diseases1.1%
938Brain Ischemia1.1%
939Esotropia1.1%
940Exotropia1.1%
941Malignant histiocytosis1.1%
942Hypotension, Orthostatic1.1%
943Sarcoidosis, Pulmonary1.1%
944Sleep Apnea Syndromes1.1%
945Cerebrovascular accident1.1%
946Kluver-Bucy Syndrome1.1%
947Histiocytic sarcoma1.1%
948Vasospasm, Intracranial1.1%
949Spinal Cord Ischemia1.1%
950Intracranial Arterial Diseases1.1%
951Post-Exercise Hypotension1.1%
952Nephroblastoma1.1%
953Disorders of Excessive Somnolence1.1%
954Sleep Initiation and Maintenance Disorders1.1%
955Night Terrors1.1%
956Somnambulism1.1%
957Trigeminal Nerve Disorder1.1%
958Transient Insomnia1.1%
959Sleep Paralysis1.1%
960Chronic Insomnia1.1%
961REM Sleep Behavior Disorder1.1%
962Hypersomnia1.1%
963Dysgeusia1.1%
964Formication1.1%
965Hyperalgesia1.1%
966Hyperesthesia1.1%
967Hypesthesia1.1%
968Language Disorders1.1%
969Numbness1.1%
970Paresthesia1.1%
971Paraparesis, Spastic1.1%
972Trismus1.1%
973Epilepsia Partialis Continua1.1%
974Hypogeusia1.1%
975Meningeal Carcinomatosis1.1%
976Brown-Sequard Syndrome1.1%
977Lockjaw1.1%
978Allodynia1.1%
979Lead Poisoning, Nervous System, Childhood1.1%
980Lead Poisoning, Nervous System, Adult1.1%
981Ageusia1.1%
982Tuberculosis, Central Nervous System1.1%
983Renal tubular acidosis1.1%
984Alexia1.1%
985Dyslexia1.1%
986Asthma, Occupational1.1%
987Hematoma, Subdural1.1%
988Hematoma, Epidural, Cranial1.1%
989Hereditary Angioedema Type III1%
990Hereditary Angioedema Types I and II1%
991Farmer's Lung1%
992Hay fever1%
993Rhinitis, Allergic, Perennial1%
994Cystinuria1%
995Cerebral Infarction1%
996Brain Stem Infarctions1%
997Adenomatous Polyposis Coli1%
998Familial Hypophosphatemic Rickets1%
999Hoarseness1%
1000Moyamoya Disease1%
1001Alcohol Withdrawal Delirium1%
1002West Nile Fever1%
1003Toxic Epidermal Necrolysis1%
1004Post-Traumatic Headache1%
1005Tension Headache1%
1006Stevens-Johnson Syndrome1%
1007Epilepsy, Complex Partial1%
1008Migraine Disorders1%
1009Abdominal Migraine1%
1010Status Migrainosus1%
1011Cervicogenic Headache1%
1012Eye Injuries1%
1013Diplopia0.9%
1014Muscle Rigidity0.9%
1015Muscle Spasticity0.9%
1016Scotoma0.9%
1017Photophobia0.9%
1018Cogwheel Rigidity0.9%
1019Hemifacial Spasm0.9%
1020Amaurosis0.9%
1021Blindness0.9%
1022Nuchal Rigidity0.9%
1023Reye Syndrome0.9%
1024Splenosis0.9%
1025Neuroaspergillosis0.9%
1026Intracranial Embolism and Thrombosis0.9%
1027Hepatic Encephalopathy0.9%
1028Agnosia0.9%
1029Apraxias0.9%
1030Hallucinations0.9%
1031Hemianopsia0.9%
1032Hyperacusis0.9%
1033Tinnitus0.9%
1034Visual Agnosia0.9%
1035Anosognosia0.9%
1036Wernicke-Korsakoff Syndrome0.9%
1037Phonophobia0.9%
1038Hearing Loss0.9%
1039Sarcopenia0.9%
1040Lateral Medullary Syndrome0.9%
1041Arthritis, Gouty0.9%
1042Glycosuria, Renal0.9%
1043Pseudorabies0.9%
1044Hematoma, Subdural, Intracranial0.8%
1045Hematoma, Subdural, Chronic0.8%
1046Hematoma, Subdural, Acute0.8%
1047Empty Sella Syndrome0.8%
1048Hyperpituitarism0.8%
1049Hypopituitarism0.8%
1050Hypophysitis0.8%
1051Amnesia0.8%
1052Delirium0.8%
1053Dissociative Amnesia0.8%
1054Color blindness0.8%
1055Global Amnesia0.8%
1056Meningioma0.8%
1057Cerebral Arterial Diseases0.8%
1058Cluster Headache0.8%
1059Neurosyphilis0.8%
1060Vertebrobasilar Insufficiency0.8%
1061Migraine with Aura0.8%
1062Anterior Spinal Artery Syndrome0.8%
1063Basilar Artery Stenosis0.8%
1064Vertebral Artery Stenosis0.8%
1065Familial Hemiplegic Migraine0.8%
1066Chronic Paroxysmal Hemicrania0.8%
1067Sleep Apnea, Obstructive0.8%
1068Sleep Apnea, Central0.8%
1069Intracranial Hemorrhage, Hypertensive0.8%
1070Transient Cerebral Ischemia0.8%
1071SUNCT Syndrome0.8%
1072Paroxysmal Hemicrania0.8%
1073Narcolepsy0.8%
1074Trigeminal Neuralgia0.8%
1075Kleine-Levin Syndrome0.8%
1076Agraphia0.8%
1077Anomia0.8%
1078Cluttering0.8%
1079Language Development Disorders0.8%
1080Speech Disorders0.8%
1081Syncope0.8%
1082Stupor0.8%
1083Dysgraphia0.8%
1084Presyncope0.8%
1085Dyslalia0.8%
1086Wernicke Encephalopathy0.7%
1087Phantom pain0.7%
1088Phantom Limb Pain0.7%
1089Lyme Neuroborreliosis0.7%
1090Eye Burns0.7%
1091Malaria, Cerebral0.7%
1092Carotid Stenosis0.7%
1093Intracranial Aneurysm0.7%
1094Neurocysticercosis0.7%
1095Amaurosis Fugax0.7%
1096Blindness, Cortical0.7%
1097Dyscalculia0.7%
1098Intracranial Arteriosclerosis0.7%
1099Cerebral Atherosclerosis0.7%
1100Subarachnoid Hemorrhage0.7%
1101Cerebral Arteriosclerosis0.7%
1102Cerebral Hemorrhage0.7%
1103Cerebral Thrombosis0.7%
1104Intracranial Embolism0.7%
1105Intracranial Thrombosis0.7%
1106Deafness0.7%
1107Hearing Loss, Sudden0.7%
1108Gerstmann Syndrome0.7%
1109Hearing Loss, Bilateral0.7%
1110Hearing Loss, High-Frequency0.7%
1111Hearing Loss, Mixed Conductive-Sensorineural0.7%
1112Prosopagnosia0.7%
1113Apraxia, Ideomotor0.7%
1114Charles Bonnet Syndrome0.7%
1115Hearing Loss, Unilateral0.7%
1116Complete Hearing Loss0.7%
1117Alien Hand Syndrome0.7%
1118Deaf Mutism0.7%
1119Hyperprolactinemia0.7%
1120Subclavian Steal Syndrome0.7%
1121Pick Disease of the Brain0.7%
1122Cataplexy0.7%
1123Aphasia0.7%
1124Articulation Disorders0.7%
1125Echolalia0.7%
1126Stuttering0.7%
1127Dysphasia0.7%
1128Corneal Scar0.6%
1129Retrograde amnesia0.6%
1130Amnesia, Anterograde0.6%
1131Carotid Artery Thrombosis0.6%
1132Dysarthria0.6%
1133Mutism0.6%
1134Selective Mutism0.6%
1135Acromegaly0.6%
1136Cerebral Amyloid Angiopathy0.6%
1137Sinus Thrombosis, Intracranial0.6%
1138Alexia, Pure0.5%
1139Cavernous Sinus Thrombosis0.5%
1140Sagittal Sinus Thrombosis0.5%
1141Corneal Perforation0.5%
1142Nelson Syndrome0.5%
1143Prolactinoma0.5%
1144Growth Hormone-Secreting Pituitary Adenoma0.5%
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