MetaADEDB 2.0 @ LMMD
Anencephaly
(UMLS:C0002902)
Definition:
A malformation of the nervous system caused by failure of the anterior neuropore to close. Infants are born with intact spinal cords, cerebellums, and brainstems, but lack formation of neural structures above this level. The skull is only partially formed but the eyes are usually normal. This condition may be associated with folate deficiency. Affected infants are only capable of primitive (brain stem) reflexes and usually do not survive for more than two weeks. (From Menkes, Textbook of Child Neurology, 5th ed, p247)
UMLS ID:
C0002902
MeSH ID:
D000757
Classification 1:
Name:
Nervous System Diseases
MeSH Tree Number(s):
C10.500.680.196
Classification 2:
Name:
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
MeSH Tree Number(s):
C16.131.085.197|C16.131.666.680.196
Synonym(s)
1.
Anencephaly
2.
ANENCEPHALUS
3.
ANENCEPHALY
4.
Agenesis of brain
5.
Anencephalic monster
6.
Anencephalus
Associated Drug(s)
NameNumber of ReportsReference(s)Data Source
1LamotrigineFAERS: 24OFFSIDES
US FAERS
2FluoxetineFAERS: 20US FAERS
3LevetiracetamFAERS: 18US FAERS
4CitalopramFAERS: 17US FAERS
5ParoxetineFAERS: 14US FAERS
6SertralineFAERS: 14US FAERS
7Folic AcidFAERS: 1212397633
15846825
CTD
US FAERS
8SertralineFAERS: 10
Canada Vigilance: 1
Canada Vigilance
US FAERS
9CitalopramFAERS: 7US FAERS
10tazaroteneFAERS: 7OFFSIDES
US FAERS
11IsotretinoinFAERS: 6US FAERS
122-(Tert-butylamino)-1-(3-chlorophenyl)propan-1-one;hydron;chlorideFAERS: 4US FAERS
13Medroxyprogesterone AcetateFAERS: 4US FAERS
14OndansetronFAERS: 4US FAERS
15OseltamivirFAERS: 4US FAERS
16FluoxetineFAERS: 3US FAERS
17Imatinib MesylateFAERS: 3US FAERS
18NaproxenFAERS: 3US FAERS
19NorgestrelFAERS: 3
Canada Vigilance: 1
Canada Vigilance
US FAERS
20TriumeqFAERS: 3US FAERS
21entecavirFAERS: 3US FAERS
22AtorvastatinFAERS: 2US FAERS
23FamotidineFAERS: 2US FAERS
24Glatiramer AcetateFAERS: 2US FAERS
25ItraconazoleFAERS: 2US FAERS
26OxcarbazepineFAERS: 2US FAERS
27ParoxetineFAERS: 2US FAERS
28AspirinFAERS: 1US FAERS
29Atomoxetine HydrochlorideFAERS: 1US FAERS
30BetamethasoneFAERS: 1US FAERS
31BromocriptineFAERS: 1US FAERS
32CabergolineFAERS: 1US FAERS
33CarbamazepineFAERS: 1US FAERS
34CetirizineFAERS: 1US FAERS
35ClomipheneFAERS: 1US FAERS
36CopperFAERS: 1US FAERS
37Duloxetine HydrochlorideFAERS: 1US FAERS
38FluconazoleFAERS: 1US FAERS
39FluticasoneFAERS: 1US FAERS
40IndomethacinFAERS: 1US FAERS
41Insulin DetemirFAERS: 1US FAERS
42LeflunomideFAERS: 1US FAERS
43Lithium CarbonateFAERS: 1US FAERS
44LopinavirFAERS: 1US FAERS
45MefloquineFAERS: 1US FAERS
46MesalamineFAERS: 1US FAERS
47MetforminFAERS: 1US FAERS
48MethotrexateFAERS: 1US FAERS
49NevirapineFAERS: 1US FAERS
50NitrofurantoinFAERS: 1US FAERS
51NuvaRingFAERS: 1US FAERS
52OrlistatFAERS: 1US FAERS
53TenofovirFAERS: 1US FAERS
54TerbinafineFAERS: 1US FAERS
55TopiramateFAERS: 1US FAERS
56Trimethoprim, Sulfamethoxazole Drug CombinationFAERS: 1US FAERS
57Valproic AcidFAERS: 1US FAERS
58Valproic AcidFAERS: 1US FAERS
59Vardenafil DihydrochlorideFAERS: 1US FAERS
60VareniclineFAERS: 1US FAERS
61Venlafaxine HydrochlorideFAERS: 1US FAERS
62VerapamilFAERS: 1US FAERS
63dolutegravirFAERS: 1US FAERS
64ecallantideFAERS: 1US FAERS
65Atomoxetine HydrochlorideOFFSIDES
66Azacitidine11875660CTD
67ClomipheneSIDER
68FelbamateSIDER
69Lithium15830831CTD
70MedroxyprogesteroneSIDER
71Methadone4586767CTD
72Naled16495467CTD
73OseltamivirOFFSIDES
74Thalidomide21505091CTD
75cetrorelixSIDER
76efavirenzSIDER
77lamivudine, zidovudine drug combinationOFFSIDES
78methyl demeton16495467CTD
79phenethicillinOFFSIDES
Similar ADE(s)
NameSemantic Similarity
1Meningomyelocele44.1%
2Spina Bifida44.1%
3Meningocele36.8%
4Encephalocele36.8%
5Hydranencephaly34.2%
6Septo-Optic Dysplasia34.2%
7Cortical Dysplasia34.2%
8Malformations of Cortical Development34.2%
9Dermal Sinus33.2%
10Spina Bifida Cystica33.2%
11Spina Bifida Occulta33.2%
12Holoprosencephaly32.7%
13Dural Arteriovenous Fistula31.4%
14Aicardi's syndrome30.6%
15Twins, Conjoined30.6%
16Abnormalities, Drug-Induced27.7%
17Situs Inversus27.7%
18Beckwith-Wiedemann Syndrome27.1%
19Wolf-Hirschhorn Syndrome27.1%
20Dandy-Walker Syndrome27%
21Smith-Magenis syndrome26.3%
22Central Nervous System Cysts26.2%
23Cri-du-Chat Syndrome24.5%
24Down Syndrome24.5%
25Trisomy 2124.5%
26Eye Abnormalities23.1%
27Cardiovascular Abnormalities23.1%
28Skin Abnormalities22.4%
29Lymphatic Abnormalities22.4%
30Congenital Microtia22.4%
31Classical Lissencephalies and Subcortical Band Heterotopias22.2%
32Rubinstein-Taybi Syndrome22%
33Congenital diaphragmatic hernia22%
34Prader-Willi Syndrome21.4%
35Ectodermal Dysplasia20.3%
36Aplasia Cutis Congenita20.3%
37Alstrom Syndrome19.7%
38Microcephaly19.6%
39Macrocephaly19.6%
40Urogenital Abnormalities19.3%
41Charcot-Marie-Tooth Disease18.5%
42Porencephaly18.1%
43CHARGE Syndrome17.9%
44Lissencephaly17.6%
45Polymicrogyria17.6%
46Pachygyria17.6%
47Schizencephaly17.6%
48Periventricular Nodular Heterotopia17.6%
49Prune Belly Syndrome17.4%
50Waardenburg Syndrome17.4%
51Mobius Syndrome17.2%
52Maxillofacial Abnormalities17.1%
53Dextrocardia17%
54Kartagener Syndrome16.9%
55Genetic Diseases, Inborn16.5%
56Marfan Syndrome15.8%
57Nail-Patella Syndrome15.5%
58Xeroderma15.3%
59Williams Syndrome14.5%
60Tuberous Sclerosis14.3%
61Cockayne Syndrome14.3%
62Anophthalmos14.1%
63Anus, Imperforate14.1%
64Microphthalmos14.1%
65Limb Deformities, Congenital14.1%
66Craniofacial Abnormalities14.1%
67Anorectal Malformations14.1%
68Bloom Syndrome13.9%
69Abnormalities, Radiation-Induced13.7%
70Scimitar Syndrome13.5%
71Refsum Disease13.4%
72Fetal Diseases13.3%
73Fragile X Syndrome13.2%
74Polycystic Kidney Diseases13.1%
75Craniosynostosis12.3%
76Syndactyly12.3%
77Brachycephaly12.3%
78Retinal Dysplasia11.9%
79Acrocephalosyndactylia11.9%
80Blepharophimosis11.9%
81Laryngostenosis11.9%
82Mouth Abnormalities11.9%
83Aniridia11.8%
84Esophageal Atresia11.7%
85Intestinal Atresia11.7%
86Horseshoe Kidney11.7%
87Pectus excavatum11.7%
88Klippel-Feil Syndrome11.7%
89Gastroschisis11.7%
90Synostosis11.7%
91Epidermolysis Bullosa11.6%
92Acrodermatitis11.6%
93Lymphangiectasis, Intestinal11.6%
94Gianotti-Crosti Syndrome11.6%
95POEMS Syndrome11.3%
96Smith-Lemli-Opitz Syndrome11.2%
97Ichthyosis, X-Linked11.2%
98Turner Syndrome11.1%
99Noonan Syndrome11.1%
100Primary Ciliary Dyskinesia11%
101Cystic Fibrosis10.8%
102Arthrogryposis10.2%
103Choanal Atresia10.2%
104Tracheobronchomegaly10.2%
105Laryngocele10.2%
106Cleft Palate10.2%
107Choledochal Cyst10.1%
108Hermaphroditism10.1%
109Disorders of Sex Development10.1%
110Myasthenic Syndromes, Congenital10.1%
111Cryptorchidism10%
112Hypospadias10%
113Jaw Abnormalities10%
114Anencephaly9.9%
115Amelia9.9%
116Arachnodactyly9.9%
117Ectopia Cordis9.9%
118Ectromelia9.9%
119Hemimelia9.9%
120Phocomelia9.9%
121Sirenomelia9.9%
122Polydactyly9.9%
123Brachydactyly9.9%
124Plagiocephaly9.9%
125Lower Extremity Deformities, Congenital9.9%
126Upper Extremity Deformities, Congenital9.9%
127Single umbilical artery9.9%
128Poland Syndrome9.7%
129Meconium Aspiration Syndrome9.4%
130Pseudoxanthoma Elasticum9.3%
131Polycystic Kidney, Autosomal Dominant9.2%
132Abdominal Cramps9.2%
133Amniotic Band Syndrome9.2%
134Asphyxia Neonatorum9.2%
135Infant, Premature, Diseases9.2%
136Infantile Colic9.2%
137Klinefelter Syndrome9.1%
138Sjogren-Larsson Syndrome9%
139Laryngomalacia8.9%
140Pectus carinatum8.9%
141Bladder Exstrophy8.7%
142Epispadias8.7%
143Cranial nerve diseases8.7%
144Demyelinating Diseases8.7%
145Demyelination8.7%
146Neuromuscular Diseases8.7%
147Chronobiology Disorders8.7%
148Multicystic Dysplastic Kidney8.7%
149Xeroderma Pigmentosum8.5%
150Zellweger Syndrome8.4%
151Kallmann Syndrome8.4%
152Aortic coarctation8.2%
153Cor Triatriatum8.2%
154Coronary Vessel Anomalies8.2%
155Dental Enamel Hypoplasia8.2%
156Patent ductus arteriosus8.2%
157Ebstein Anomaly8.2%
158Heart Septal Defects8.2%
159Hypodontia8.2%
160Macrostomia8.2%
161Microstomia8.2%
162Tetralogy of Fallot8.2%
163Transposition of Great Vessels8.2%
164Hypoplastic Left Heart Syndrome8.2%
165May-Thurner Syndrome8.2%
166Craniofacial Dysostosis8.2%
167Motor Neuron Disease8.2%
168Wolff-Parkinson-White Syndrome8.2%
169Antley-Bixler Syndrome Phenotype8.1%
170Micrognathism8.1%
171Pierre Robin Syndrome8.1%
172Multiple System Atrophy8.1%
173Neural Tube Defects8.1%
174Tethered Cord Syndrome8.1%
175Iniencephaly8.1%
176Craniorachischisis8.1%
177Exencephaly8.1%
178Dystonia Musculorum Deformans8%
179Hyperkeratosis, Epidermolytic7.9%
180Muscular Dystrophy7.8%
181Congenital nystagmus7.8%
182Stiff-Person Syndrome7.7%
183Muscular Dystrophy, Duchenne7.7%
184Myotonic Dystrophy7.7%
185Neoplastic Syndromes, Hereditary7.7%
186Basal Cell Nevus Syndrome7.7%
187Toxoplasmosis, Congenital7.4%
188Anemia, Neonatal7.4%
189Multiple Epiphyseal Dysplasia7.4%
190Osteochondrodysplasias7.4%
191Pelger-Huet Anomaly7.4%
192Persistent Fetal Circulation Syndrome7.4%
193Werner Syndrome7.4%
194Retrognathia7.3%
195Umbilical hernia7.3%
196Polyradiculoneuropathy7.2%
197Polyradiculoneuritis7.2%
198Ataxia Telangiectasia7.2%
199Trauma, Nervous System7.2%
200Restless Legs Syndrome7.2%
201Hepatolenticular Degeneration7.2%
202Lafora Disease7.1%
203Unverricht-Lundborg Syndrome7.1%
204Long QT Syndrome7.1%
205Platybasia7.1%
206Tricuspid Atresia7.1%
207Arrhythmogenic Right Ventricular Dysplasia7.1%
208Gonadal Dysgenesis7%
209Bronchomalacia7%
210Adrenogenital Syndrome7%
211Tracheomalacia7%
212Ovotesticular Disorders of Sex Development7%
213Hyperandrogenism7%
214Ocular Motility Disorders7%
215Cyclophoria7%
216Canavan Disease7%
217Alexander Disease7%
218Nervous System Neoplasms7%
219Neurologic Manifestations7%
220Neurotoxicity Syndromes7%
221Rett Syndrome6.8%
222Encephalomyelitis6.7%
223Prion Diseases6.7%
224Autonomic Dysreflexia6.7%
225Complex Regional Pain Syndromes6.7%
226Ophthalmoplegic Migraine6.7%
227Subacute Combined Degeneration6.7%
228Prognathism6.7%
229Spinal Muscular Atrophy6.6%
230Progressive Muscular Atrophy6.6%
231Amyotrophic Lateral Sclerosis6.6%
232Myotonia Congenita6.6%
233Anemia, Sickle Cell6.6%
234Thalassemia6.6%
235Meningoencephalitis6.6%
236Aortopulmonary Septal Defect6.5%
237Double Outlet Right Ventricle6.5%
238Endocardial Cushion Defects6.5%
239Myocardial bridging6.5%
240Aorticopulmonary Septal Defect6.5%
241Adrenoleukodystrophy6.4%
242Huntington Disease6.4%
243Dwarfism6.4%
244Parkinson Disease6.3%
245Albinism6.3%
246Neonatal Abstinence Syndrome6.3%
247Menkes Kinky Hair Syndrome6.2%
248Amyloid Neuropathies, Familial6.2%
249Fetal Growth Retardation6.1%
250Neuronal Ceroid-Lipofuscinoses6.1%
251Osteogenesis Imperfecta6.1%
252Fetal Hypoxia6.1%
253Fetal Alcohol Spectrum Disorders6.1%
254Leukomalacia, Periventricular6.1%
255Syphilis, Congenital6%
256Mucopolysaccharidosis II6%
257Marchiafava-Bignami Disease6%
258Lewy Body Disease6%
259Guillain-Barre Syndrome6%
260Sleep Wake Disorders5.9%
261Striatonigral Degeneration5.8%
262Familial Mediterranean Fever5.8%
263Spinal Cord Injuries5.8%
264Pneumocephalus5.7%
265Poliomyelitis5.7%
266Truncus Arteriosus, Persistent5.7%
267Peripheral Nerve Injuries5.6%
268Goldenhar Syndrome5.6%
269Myasthenia Gravis5.6%
270Asterixis5.6%
271Ballismus5.6%
272Mandibulofacial Dysostosis5.6%
273Romano-Ward Syndrome5.6%
274Progressive supranuclear palsy5.6%
275Leukoencephalitis, Acute Hemorrhagic5.5%
276Friedreich Ataxia5.5%
277Causalgia5.5%
278Miller Fisher Syndrome5.4%
279Myelitis, Transverse5.4%
280Duane Retraction Syndrome5.3%
281Autoimmune Lymphoproliferative Syndrome5.3%
282Myelitis5.3%
283Progressive bulbar palsy5.3%
284Bulbar palsy5.3%
285Congenital Hyperinsulinism5.3%
286Chorioamnionitis5.2%
287Angioedemas, Hereditary5.2%
288Lambert-Eaton Myasthenic Syndrome5.2%
289Welander Distal Myopathy5.2%
290Epidural Abscess5.2%
291Olfactory Nerve Injuries5.2%
292Wiskott-Aldrich Syndrome5.1%
293Shy-Drager Syndrome5.1%
294MPTP Poisoning5.1%
295Optic Atrophy, Hereditary, Leber5.1%
296Neuromyelitis Optica5.1%
297Brain Diseases5%
298Dysautonomia5%
299Meningitis5%
300Movement Disorders5%
301Pachymeningitis5%
302Spinal Cord Diseases5%
303Vagus Nerve Disorder5%
304Glossopharyngeal Neuralgia5%
305Abducens Nerve Diseases5%
306Heavy Metal Poisoning, Nervous System5%
307Neuromuscular Junction Diseases5%
308Tauopathies5%
309Trochlear Nerve Diseases5%
310Peripheral Nervous System Diseases5%
311Neuroleptic Malignant Syndrome5%
312Myelinolysis, Central Pontine5%
313Opsoclonus-Myoclonus Syndrome5%
314Chronic Fatigue Syndrome5%
315Sleep Disorders, Circadian Rhythm4.9%
316Encephalomyelitis, Acute Disseminated4.9%
317Polyradiculoneuropathy, Chronic Inflammatory Demyelinating4.9%
318Talipes4.9%
319Dyskinesia, Drug-Induced4.8%
320Botulism4.8%
321Brain Diseases, Metabolic, Inborn4.7%
322Fabry Disease4.7%
323Paralysis, Obstetric4.7%
324Retinopathy of Prematurity4.7%
325Amino Acid Metabolism, Inborn Errors4.6%
326Carbohydrate Metabolism, Inborn Errors4.6%
327Metal Metabolism, Inborn Errors4.6%
328Progeria4.6%
329Lysosomal Storage Diseases4.6%
330Cytochrome-c Oxidase Deficiency4.6%
331Peroxisomal Disorders4.6%
332Sickle Cell Trait4.6%
333Bronchopulmonary Dysplasia4.6%
334Reflex Sympathetic Dystrophy4.6%
335Subdural Effusion4.6%
336Parkinsonian Disorders4.6%
337Nocturnal Myoclonus Syndrome4.6%
338Facial Nerve Injuries4.5%
339Galactosemias4.5%
340Leukoencephalopathy, Progressive Multifocal4.5%
341Urea Cycle Disorders, Inborn4.5%
342Tyrosinemias4.5%
343Congenital clubfoot4.5%
344Vertical Talus4.5%
345Brain Injuries4.4%
346Brain Neoplasms4.4%
347Multiple Sclerosis4.4%
348Spinal Cord Neoplasms4.4%
349Arteriovenous fistula4.4%
350Familial Periodic Paralysis4.3%
351Horner Syndrome4.3%
352Central Nervous System Infection4.2%
353Myopathy4.2%
354Optic Neuropathy4.2%
355Akathisia, Drug-Induced4.2%
356Epilepsy, Post-Traumatic4.2%
357Glycogen storage disease type II4.2%
358Limbic Encephalitis4.1%
359Facial Nerve Diseases4.1%
360Craniocerebral Trauma4.1%
361Parasomnia4.1%
362Dyssomnias4.1%
363Lupus Vasculitis, Central Nervous System4.1%
364Vestibulocochlear Nerve Diseases4%
365Decerebrate State4%
366Hemiparesis4%
367Meningism4%
368Paresis4%
369Seizures4%
370Sensation Disorders4%
371Central Nervous System Neoplasms4%
372Complex partial seizures4%
373Monoparesis4%
374Neurogenic Inflammation4%
375Gait Disorders, Neurologic4%
376Neuromuscular Manifestations4%
377Ophthalmia Neonatorum4%
378Sweating, Gustatory4%
379Auriculotemporal Syndrome4%
380Myasthenia Gravis, Autoimmune, Experimental4%
381Respiratory Distress Syndrome, Newborn4%
382Meige Syndrome3.9%
383Brachial Plexus Neuritis3.9%
384Neuralgic Amyotrophy3.9%
385Cerebral Ventriculitis3.9%
386Cutis Laxa3.9%
387Retinitis Pigmentosa3.9%
388Scrapie3.9%
389Central Cord Syndrome3.9%
390Pigmentary retinopathy3.9%
391Porokeratosis3.9%
392Keratoderma, Palmoplantar3.9%
393Presenile dementia3.8%
394Senile dementia3.8%
395Chronic granulomatous disease3.8%
396Meningitis, Bacterial3.8%
397Meningitis, Fungal3.8%
398Chorea3.8%
399Acrodynia3.8%
400Brain Abscess3.8%
401Ophthalmoplegia3.8%
402External Ophthalmoplegia3.8%
403Homocystinuria3.8%
404Vasculitis, Central Nervous System3.7%
405Jet Lag Syndrome3.7%
406Leigh Disease3.7%
407Kernicterus3.7%
408Cerebellar Neoplasms3.7%
409Acute Chest Syndrome3.7%
410Denys-Drash Syndrome3.6%
411Dementia, Vascular3.6%
412Brain Hemorrhage, Traumatic3.6%
413Hydrops Fetalis3.6%
414Tarsal Tunnel Syndrome3.6%
415Cauda Equina Syndrome3.6%
416Posterior Leukoencephalopathy Syndrome3.6%
417Posterior reversible encephalopathy syndrome3.6%
418Pupil Disorders3.5%
419Neurobehavioral Manifestations3.5%
420Brain Death3.4%
421Coma, Post-Head Injury3.4%
422Paraneoplastic Encephalomyelitis3.4%
423Vocal Cord Paralysis3.4%
424MELAS Syndrome3.4%
425Gaucher Disease3.4%
426Uveomeningoencephalitic Syndrome3.4%
427Porphyrias, Hepatic3.3%
428Sturge-Weber Syndrome3.3%
429Vertigo3.3%
430Alcohol-Induced Disorders, Nervous System3.3%
431Amblyopia3.3%
432Akinetic Mutism3.3%
433Anoxic Encephalopathy3.3%
434Arachnoiditis3.3%
435Basal Ganglia Diseases3.3%
436Brain Damage, Chronic3.3%
437Cerebellar Diseases3.3%
438Encephalitis3.3%
439Encephalomalacia3.3%
440Epilepsy3.3%
441Hydrocephalus3.3%
442Congenital Hydrocephalus3.3%
443Hypothalamic Diseases3.3%
444Aseptic Meningitis3.3%
445Neuritis3.3%
446Peutz-Jeghers Syndrome3.3%
447Polyneuritis3.3%
448Radiculitis3.3%
449Syringomyelia3.3%
450Thalamic Diseases3.3%
451Intracranial Hypertension3.3%
452Polyneuropathy3.3%
453Mononeuritis3.3%
454Aura3.3%
455Leukoencephalopathy3.3%
456Essential Tremor3.3%
457Neuroaxonal Dystrophies3.3%
458Familial Tremor3.3%
459Headache Disorders3.3%
460Mononeuropathies3.3%
461Intracranial Hypotension3.3%
462Brachial Plexus Neuropathies3.3%
463Radiculopathy3.3%
464Mononeuropathy Multiplex3.3%
465Nerve Root Compression3.3%
466Brain Edema3.3%
467Brain Hypoxia3.3%
468Aqueductal Stenosis3.3%
469Pneumorrhachis3.3%
470Writer's Cramp3.3%
471Carbamoyl-Phosphate Synthase I Deficiency Disease3.3%
472Thrombasthenia3.3%
473Antithrombin III Deficiency3.3%
474Protein C Deficiency3.3%
475Afibrinogenemia3.3%
476Factor VII Deficiency3.3%
477Factor X Deficiency3.3%
478Factor XII Deficiency3.3%
479Hemophilia A3.3%
480Paraneoplastic Cerebellar Degeneration3.3%
481Activated Protein C Resistance3.3%
482Factor II deficiency3.3%
483Factor VIII Deficiency3.3%
484Factor V deficiency3.3%
485Factor XI Deficiency3.3%
486Hypoprothrombinemias3.3%
487Creutzfeldt-Jakob disease3.3%
488Basal Ganglia Cerebrovascular Disease3.3%
489Cerebrospinal Fluid Otorrhea3.3%
490Cerebrospinal Fluid Rhinorrhea3.3%
491Fanconi Anemia3.3%
492Nesidioblastosis3.3%
493Neuritis, Autoimmune, Experimental3.3%
494Alkaptonuria3.3%
495Glycogen Storage Disease3.3%
496Hypophosphatasia3.3%
497Propionic acidemia3.3%
498Dihydropyrimidine Dehydrogenase Deficiency3.3%
499Cystinosis3.3%
500Gait Ataxia3.3%
501Carotid Artery Injuries3.3%
502Brain Injuries, Diffuse3.3%
503Traumatic Brain Injury3.3%
504Hypokalemic periodic paralysis3.3%
505Anemia, Diamond-Blackfan3.3%
506Cerebellar Ataxia3.3%
507Supratentorial Neoplasms3.3%
508Torticollis3.3%
509Multiple Sclerosis, Chronic Progressive3.3%
510Multiple Sclerosis, Relapsing-Remitting3.3%
511Myoclonic Epilepsy3.2%
512Epilepsy, Temporal Lobe3.2%
513Epilepsy, Rolandic3.2%
514Benign Rolandic Epilepsy3.2%
515Hyperphosphaturia3.2%
516Tuberculosis, Meningeal3.2%
517Mucopolysaccharidosis III3.2%
518Tay-Sachs Disease3%
519Carpal Tunnel Syndrome3%
520Vascular Headaches3%
521neurofibroma3%
522Hypoxia-Ischemia, Brain3%
523Multiple Endocrine Neoplasia3%
524Sciatica3%
525Tardive Dyskinesia3%
526Alice in Wonderland Syndrome3%
527Persistent Vegetative State3%
528Voice Disorders2.9%
529Voice Disturbance2.9%
530Congenital Hypothyroidism2.9%
531Alcohol Withdrawal Seizures2.9%
532Juvenile Myoclonic Epilepsy2.9%
533Myoclonic Epilepsies, Progressive2.9%
534Dermatitis, Atopic2.9%
535Niemann-Pick Disease, Type C2.9%
536Brain Concussion2.9%
537Akathisia2.9%
538Restlessness2.9%
539Psychomotor Agitation2.9%
540Optic Nerve Glioma2.8%
541Pituitary Adenoma2.8%
542Pituitary Neoplasms2.8%
543Toxoplasmosis, Cerebral2.8%
544Hyaline Membrane Disease2.7%
545Hypolipoproteinemias2.7%
546Papillon-Lefevre Disease2.7%
547Hyperlipidemia, Familial Combined2.7%
548Hyperlipoproteinemia Type III2.7%
549Cubital Tunnel Syndrome2.7%
550Diffuse Axonal Injury2.7%
551Brain Stem Neoplasms2.7%
552Brain Diseases, Metabolic2.7%
553Cerebrovascular Disorders2.7%
554Myositis2.7%
555Optic Atrophy2.7%
556Optic Neuritis2.7%
557Papilledema2.7%
558Strabismus2.7%
559Tolosa-Hunt Syndrome2.7%
560Cerebrovascular Insufficiency2.7%
561Isaacs syndrome2.7%
562Arsenic Poisoning2.7%
563Dementia2.7%
564Myotonic Disorders2.7%
565Central Nervous System Fungal Infections2.7%
566Conus Medullaris Syndrome2.7%
567Spinal Cord Vascular Diseases2.7%
568Vertebral Artery Dissection2.7%
569Amnesia, Transient Global2.7%
570Diabetic Neuropathies2.6%
571Facial Injuries2.6%
572Facial Neuralgia2.6%
573Diabetic Amyotrophy2.6%
574Diabetic Autonomic Neuropathy2.6%
575Sleep Talking2.6%
576Manganese Poisoning2.6%
577Sleep Disorders, Intrinsic2.6%
578Orthostatic intolerance2.6%
579Gait Apraxia2.6%
580Anosmia2.6%
581Ataxia2.6%
582Athetosis2.6%
583Catalepsy2.6%
584Dystonia2.6%
585Hemiplegia2.6%
586Locked-In Syndrome2.6%
587Meningeal Neoplasms2.6%
588Muscle Hypertonia2.6%
589Muscle hypotonia2.6%
590Myoclonus2.6%
591Myotonia2.6%
592Neuralgia2.6%
593Paraplegia2.6%
594Pseudobulbar Palsy2.6%
595Quadriplegia2.6%
596Spasm2.6%
597Spastic Paraplegia2.6%
598Status Epilepticus2.6%
599Taste Disorders2.6%
600Tremor2.6%
601Monoplegia2.6%
602Hypokinesia2.6%
603Paraparesis2.6%
604Bradykinesia2.6%
605Waxy flexibility2.6%
606Action Tremor2.6%
607Resting Tremor2.6%
608Dysosmia2.6%
609Quadriparesis2.6%
610Mercury Poisoning, Nervous System2.6%
611Olfaction Disorders2.6%
612Myokymia2.6%
613Lead Poisoning, Nervous System2.6%
614Vestibular Neuronitis2.6%
615Somatosensory Disorders2.6%
616Neuropathic pain2.6%
617Hyperkinesia2.6%
618Intention tremor2.6%
619Glycogen Storage Disease Type I2.6%
620Glycogen Storage Disease Type V2.6%
621Basal Ganglia Hemorrhage2.6%
622Behcet Syndrome2.6%
623Meningitis, Cryptococcal2.6%
624Meningitis, Listeria2.6%
625Meningitis, Haemophilus2.5%
626Meningitis, Pneumococcal2.5%
627Frontotemporal dementia2.5%
628Reflex, Abnormal2.5%
629Hyporeflexia2.5%
630Hyperreflexia2.5%
631Cerebral Palsy2.5%
632Epilepsies, Partial2.5%
633Epilepsy, Generalized2.5%
634Pseudotumor Cerebri2.5%
635Sciatic Neuropathy2.5%
636Hypertensive Encephalopathy2.5%
637Ulnar Neuropathies2.5%
638Lesion of Sciatic Nerve2.5%
639Mitochondrial Encephalomyopathies2.5%
640Simple Partial Seizures2.5%
641Epilepsy, Reflex2.5%
642Ulnar Neuritis2.5%
643Radial nerve compression2.5%
644Radial Tunnel Syndrome2.5%
645Peroneal Neuropathies2.5%
646Radial Neuropathy2.5%
647Median Neuropathy2.5%
648Sciatic Nerve Palsy2.5%
649Femoral Neuropathy2.5%
650Tibial Neuropathy2.5%
651Ulnar Nerve Palsy2.5%
652Postural Orthostatic Tachycardia Syndrome2.5%
653Radial nerve palsy2.5%
654Headache Disorders, Primary2.5%
655Headache Disorders, Secondary2.5%
656Medication overuse headache2.5%
657Subarachnoid Hemorrhage, Traumatic2.4%
658Carotid Artery, Internal, Dissection2.4%
659Choroid Plexus Papilloma2.4%
660Subacute Sclerosing Panencephalitis2.4%
661Putaminal Hemorrhage2.4%
662Pituitary Apoplexy2.3%
663Lactose Intolerance2.3%
664Variegate Porphyria2.3%
665Acute intermittent porphyria2.3%
666Porphyria Cutanea Tarda2.3%
667Hyperhomocysteinemia2.3%
668Renal Aminoacidurias2.3%
669Fanconi Syndrome2.3%
670Pseudohypoaldosteronism2.3%
671Brain Contusion2.3%
672Liddle Syndrome2.3%
673Brain Infarction2.3%
674Hand-Arm Vibration Syndrome2.3%
675Hyperlipoproteinemia Type IV2.3%
676Hyperlipoproteinemia Type V2.3%
677Infarction, Middle Cerebral Artery2.3%
678Infarction, Anterior Cerebral Artery2.3%
679Infarction, Posterior Cerebral Artery2.3%
680Vision Disorders2.3%
681Metamorphopsia2.3%
682Visual Impairment2.3%
683Fibromyalgia2.3%
684Optic Neuropathy, Ischemic2.3%
685Anterior Ischemic Optic Neuropathy2.3%
686Central Nervous System Bacterial Infections2.3%
687Medial Tibial Stress Syndrome2.3%
688Facial Hemiatrophy2.2%
689Melkersson-Rosenthal Syndrome2.2%
690Mitochondrial Myopathies2.2%
691Anisocoria2.2%
692Confusion2.2%
693Facial paralysis2.2%
694Lethargy2.2%
695Memory Disorders2.2%
696Muscle Cramp2.2%
697Perceptual Disorders2.2%
698Psychomotor Disorders2.2%
699Tonic Pupil2.2%
700Eosinophilia-Myalgia Syndrome2.2%
701Anhedonia2.2%
702Disorientation2.2%
703Facial Paresis2.2%
704Memory Loss2.2%
705Hemisensory Neglect2.2%
706Dysacusis2.2%
707Sleep Bruxism2.2%
708Muscular Atrophy2.2%
709Respiratory Paralysis2.2%
710Tetany2.2%
711Auditory Perceptual Disorders2.2%
712Acoustic Neuroma2.2%
713Hypoalphalipoproteinemias2.2%
714Giant Cell Arteritis2.1%
715Temporal Arteritis2.1%
716Nephroblastoma2.1%
717Gout2.1%
718Cerebral Infarction2.1%
719Brain Stem Infarctions2.1%
720Multiple Endocrine Neoplasia Type 12.1%
721Pseudohypoparathyroidism2.1%
722Pituitary Diseases2.1%
723Polyradiculopathy2%
724Post-Traumatic Headache2%
725Tension Headache2%
726Epilepsy, Complex Partial2%
727Migraine Disorders2%
728Abdominal Migraine2%
729Status Migrainosus2%
730Cervicogenic Headache2%
731Renal tubular acidosis2%
732Alexia2%
733Dyslexia2%
734Thoracic Outlet Syndrome2%
735Carotid Artery Diseases2%
736Brain Ischemia2%
737Esotropia2%
738Exotropia2%
739Hypotension, Orthostatic2%
740Sleep Apnea Syndromes2%
741Cerebrovascular accident2%
742Polymyositis2%
743Kluver-Bucy Syndrome2%
744Vasospasm, Intracranial2%
745Spinal Cord Ischemia2%
746Intracranial Arterial Diseases2%
747Post-Exercise Hypotension2%
748Disorders of Excessive Somnolence2%
749Sleep Initiation and Maintenance Disorders2%
750Night Terrors2%
751Somnambulism2%
752Trigeminal Nerve Disorder2%
753Transient Insomnia2%
754Sleep Paralysis2%
755Chronic Insomnia2%
756REM Sleep Behavior Disorder2%
757Hypersomnia2%
758West Nile Fever2%
759Dysgeusia2%
760Formication2%
761Hyperalgesia2%
762Hyperesthesia2%
763Hypesthesia2%
764Language Disorders2%
765Numbness2%
766Paresthesia2%
767Paraparesis, Spastic2%
768Trismus2%
769Epilepsia Partialis Continua2%
770Hypogeusia2%
771Meningeal Carcinomatosis2%
772Brown-Sequard Syndrome2%
773Lockjaw2%
774Allodynia2%
775Lead Poisoning, Nervous System, Childhood2%
776Lead Poisoning, Nervous System, Adult2%
777Ageusia2%
778Tuberculosis, Central Nervous System2%
779Lateral Medullary Syndrome1.9%
780Moyamoya Disease1.9%
781Consciousness Disorders1.9%
782Mental Retardation1.9%
783Muscle Weakness1.9%
784Depressed Level of Consciousness1.9%
785Mental deficiency1.9%
786Intellectual Disability1.9%
787Bell Palsy1.9%
788Neurofibrosarcoma1.9%
789Catatonia1.9%
790Herpes Zoster Oticus1.9%
791Adenomatous Polyposis Coli1.9%
792Aphonia1.9%
793Hematoma, Subdural1.9%
794Sleep Deprivation1.9%
795Hematoma, Epidural, Cranial1.9%
796Dysphonia1.9%
797Kearns-Sayre syndrome1.9%
798Cystinuria1.8%
799Cluster Headache1.8%
800Migraine with Aura1.8%
801Familial Hemiplegic Migraine1.8%
802Chronic Paroxysmal Hemicrania1.8%
803SUNCT Syndrome1.8%
804Paroxysmal Hemicrania1.8%
805Familial Hypophosphatemic Rickets1.7%
806Eye Injuries1.7%
807Orbital Myositis1.7%
808Empty Sella Syndrome1.7%
809Hyperpituitarism1.7%
810Hypopituitarism1.7%
811Hypophysitis1.7%
812Diplopia1.7%
813Muscle Rigidity1.7%
814Muscle Spasticity1.7%
815Scotoma1.7%
816Photophobia1.7%
817Cogwheel Rigidity1.7%
818Hemifacial Spasm1.7%
819Amaurosis1.7%
820Blindness1.7%
821Nuchal Rigidity1.7%
822Myalgia1.6%
823Reye Syndrome1.6%
824Neuroaspergillosis1.6%
825Pyomyositis1.6%
826Hematoma, Subdural, Intracranial1.6%
827Hematoma, Subdural, Chronic1.6%
828Hematoma, Subdural, Acute1.6%
829Intracranial Embolism and Thrombosis1.6%
830Hepatic Encephalopathy1.6%
831Agnosia1.6%
832Apraxias1.6%
833Hallucinations1.6%
834Hemianopsia1.6%
835Hyperacusis1.6%
836Tinnitus1.6%
837Visual Agnosia1.6%
838Anosognosia1.6%
839Wernicke-Korsakoff Syndrome1.6%
840Phonophobia1.6%
841Hearing Loss1.6%
842Cerebral Arterial Diseases1.6%
843Vertebrobasilar Insufficiency1.6%
844Anterior Spinal Artery Syndrome1.6%
845Basilar Artery Stenosis1.6%
846Vertebral Artery Stenosis1.6%
847Sleep Apnea, Obstructive1.6%
848Sleep Apnea, Central1.6%
849Intracranial Hemorrhage, Hypertensive1.6%
850Transient Cerebral Ischemia1.6%
851Arthritis, Gouty1.6%
852Sarcopenia1.6%
853Narcolepsy1.6%
854Trigeminal Neuralgia1.6%
855Kleine-Levin Syndrome1.6%
856Agraphia1.6%
857Anomia1.6%
858Cluttering1.6%
859Language Development Disorders1.6%
860Speech Disorders1.6%
861Syncope1.6%
862Stupor1.6%
863Dysgraphia1.6%
864Presyncope1.6%
865Dyslalia1.6%
866Glycosuria, Renal1.6%
867Hoarseness1.5%
868Hyperprolactinemia1.5%
869Pseudorabies1.5%
870Alcohol Withdrawal Delirium1.5%
871Subclavian Steal Syndrome1.5%
872Pick Disease of the Brain1.5%
873Cataplexy1.5%
874Aphasia1.5%
875Articulation Disorders1.5%
876Echolalia1.5%
877Stuttering1.5%
878Dysphasia1.5%
879Amnesia1.4%
880Delirium1.4%
881Dissociative Amnesia1.4%
882Color blindness1.4%
883Global Amnesia1.4%
884Meningioma1.4%
885Neurosyphilis1.4%
886Eye Burns1.4%
887Dysarthria1.4%
888Malaria, Cerebral1.4%
889Carotid Stenosis1.4%
890Intracranial Aneurysm1.4%
891Neurocysticercosis1.4%
892Amaurosis Fugax1.4%
893Blindness, Cortical1.4%
894Dyscalculia1.4%
895Intracranial Arteriosclerosis1.4%
896Cerebral Atherosclerosis1.4%
897Subarachnoid Hemorrhage1.4%
898Cerebral Arteriosclerosis1.4%
899Cerebral Hemorrhage1.4%
900Cerebral Thrombosis1.4%
901Intracranial Embolism1.4%
902Intracranial Thrombosis1.4%
903Deafness1.3%
904Hearing Loss, Sudden1.3%
905Gerstmann Syndrome1.3%
906Hearing Loss, Bilateral1.3%
907Hearing Loss, High-Frequency1.3%
908Hearing Loss, Mixed Conductive-Sensorineural1.3%
909Prosopagnosia1.3%
910Apraxia, Ideomotor1.3%
911Charles Bonnet Syndrome1.3%
912Hearing Loss, Unilateral1.3%
913Complete Hearing Loss1.3%
914Alien Hand Syndrome1.3%
915Deaf Mutism1.3%
916Waterhouse-Friderichsen Syndrome1.3%
917Mutism1.2%
918Selective Mutism1.2%
919Acromegaly1.2%
920Wernicke Encephalopathy1.2%
921AIDS Dementia Complex1.2%
922Phantom pain1.2%
923Phantom Limb Pain1.2%
924Lyme Neuroborreliosis1.2%
925Cerebral Amyloid Angiopathy1.2%
926Sinus Thrombosis, Intracranial1.2%
927Dermatomyositis1.2%
928Corneal Scar1.2%
929Retrograde amnesia1.2%
930Amnesia, Anterograde1.2%
931Carotid Artery Thrombosis1.2%
932Alexia, Pure1.1%
933Cavernous Sinus Thrombosis1.1%
934Sagittal Sinus Thrombosis1.1%
935Corneal Perforation1%
936Nelson Syndrome1%
937Prolactinoma0.9%
938Growth Hormone-Secreting Pituitary Adenoma0.9%
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