MetaADEDB 2.0 @ LMMD
Amyotrophic Lateral Sclerosis
(UMLS:C0002736)
Definition:
A degenerative disorder affecting upper MOTOR NEURONS in the brain and lower motor neurons in the brain stem and SPINAL CORD. Disease onset is usually after the age of 50 and the process is usually fatal within 3 to 6 years. Clinical manifestations include progressive weakness, atrophy, FASCICULATION, hyperreflexia, DYSARTHRIA, dysphagia, and eventual paralysis of respiratory function. Pathologic features include the replacement of motor neurons with fibrous ASTROCYTES and atrophy of anterior SPINAL NERVE ROOTS and corticospinal tracts. (From Adams et al., Principles of Neurology, 6th ed, pp1089-94)
UMLS ID:
C0002736
MeSH ID:
D000690
Classification 1:
Name:
Nervous System Diseases
MeSH Tree Number(s):
C10.228.854.139|C10.574.562.250|C10.574.950.050|C10.668.467.250
Classification 2:
Name:
Nutritional and Metabolic Diseases
MeSH Tree Number(s):
C18.452.845.800.050
Synonym(s)
1.
Amyotrophic Lateral Sclerosis
2.
ALS
3.
ALS (amyotrophic lateral sclerosis)
4.
ALS - Amyotrophic lateral sclerosis
5.
AMYOTROPHIC LATERAL SCLEROSIS
6.
Amyotrophic Lateral Sclerosis/Progressive Muscular Atrophy
7.
Amyotrophic lateral sclerosis
8.
Bulbar motor neuron disease
9.
LOU GEHRIG DISEASE
Associated Drug(s)
NameNumber of ReportsReference(s)Data Source
1AtorvastatinFAERS: 74
Canada Vigilance: 2
Canada Vigilance
US FAERS
2SimvastatinFAERS: 31US FAERS
3Rosuvastatin CalciumFAERS: 26
Canada Vigilance: 3
Canada Vigilance
US FAERS
4EdaravoneFAERS: 2228522181CTD
US FAERS
5BaclofenFAERS: 16US FAERS
6RiluzoleFAERS: 14
Canada Vigilance: 12

View details

CTD
Canada Vigilance
US FAERS
7Zoledronic AcidFAERS: 14
Canada Vigilance: 7
Canada Vigilance
US FAERS
8Duloxetine HydrochlorideFAERS: 12US FAERS
9LovastatinFAERS: 12US FAERS
10TeriparatideFAERS: 8US FAERS
11PregabalinFAERS: 7
Canada Vigilance: 1
Canada Vigilance
US FAERS
12Quetiapine FumarateFAERS: 7US FAERS
13Glatiramer AcetateFAERS: 6US FAERS
14ClozapineFAERS: 5
Canada Vigilance: 2
Canada Vigilance
US FAERS
15EzetimibeFAERS: 5US FAERS
16Imatinib MesylateFAERS: 5
Canada Vigilance: 1
Canada Vigilance
US FAERS
17MethamphetamineFAERS: 5US FAERS
18GabapentinFAERS: 4US FAERS
19LetrozoleFAERS: 4US FAERS
20LevofloxacinFAERS: 4US FAERS
21ValsartanFAERS: 4US FAERS
224-AminopyridineFAERS: 3
Canada Vigilance: 1
Canada Vigilance
US FAERS
234-methyl-N-(3-(4-methylimidazol-1-yl)-5-(trifluoromethyl)phenyl)-3-((4-pyridin-3-ylpyrimidin-2-yl)amino)benzamideFAERS: 3US FAERS
24AmlodipineFAERS: 3US FAERS
25CelecoxibFAERS: 3US FAERS
26CiprofloxacinFAERS: 3US FAERS
27Dimethyl FumarateFAERS: 3US FAERS
28EsomeprazoleFAERS: 3US FAERS
29MefloquineFAERS: 3US FAERS
30PravastatinFAERS: 3US FAERS
31Sildenafil CitrateFAERS: 3US FAERS
32SulfasalazineFAERS: 3US FAERS
33SunitinibFAERS: 3US FAERS
34ThalidomideFAERS: 316510725
18425621
CTD
US FAERS
35Tiotropium BromideFAERS: 3US FAERS
36miglustatFAERS: 3US FAERS
37tizanidineFAERS: 3US FAERS
38vorapaxarFAERS: 3US FAERS
39AtorvastatinFAERS: 2US FAERS
40EverolimusFAERS: 2US FAERS
41FenofibrateFAERS: 2US FAERS
42Fingolimod HydrochlorideFAERS: 2US FAERS
43FractalsFAERS: 2US FAERS
44GemfibrozilFAERS: 2US FAERS
45GoserelinFAERS: 2US FAERS
46HydroxyureaFAERS: 2US FAERS
47Imatinib MesylateFAERS: 2US FAERS
48Insulin GlargineFAERS: 2US FAERS
49LCZ 696FAERS: 2US FAERS
50LevetiracetamFAERS: 2US FAERS
51Medroxyprogesterone AcetateFAERS: 2US FAERS
52Mycophenolic AcidFAERS: 2US FAERS
53OlanzapineFAERS: 2US FAERS
54Raltegravir PotassiumFAERS: 2US FAERS
55RamiprilFAERS: 2US FAERS
56RisperidoneFAERS: 2US FAERS
57RivaroxabanFAERS: 2
Canada Vigilance: 1
Canada Vigilance
US FAERS
58Rosuvastatin CalciumFAERS: 2US FAERS
59Sitagliptin PhosphateFAERS: 2US FAERS
60SunitinibFAERS: 2US FAERS
61VareniclineFAERS: 2US FAERS
62apixabanFAERS: 2US FAERS
63rofecoxibFAERS: 2US FAERS
64tofacitinibFAERS: 2US FAERS
65ziprasidoneFAERS: 2US FAERS
66ARRY-470FAERS: 1US FAERS
67AlendronateFAERS: 1US FAERS
68AnastrozoleFAERS: 1US FAERS
69Aspirin-oxycodone hydrochloride-oxycodone terephthalate combinationFAERS: 1US FAERS
70BudesonideFAERS: 1US FAERS
71ClonazepamFAERS: 1US FAERS
72DeferasiroxFAERS: 1US FAERS
73DigoxinFAERS: 1US FAERS
74Duloxetine HydrochlorideFAERS: 1US FAERS
75Ethylene GlycolFAERS: 1US FAERS
76FebuxostatFAERS: 1US FAERS
77FinasterideFAERS: 1US FAERS
78Fluticasone-Salmeterol Drug CombinationFAERS: 1US FAERS
79GefitinibFAERS: 1US FAERS
80Ibandronic AcidFAERS: 1US FAERS
81IsotretinoinFAERS: 1US FAERS
82LatanoprostFAERS: 1US FAERS
83LeuprolideFAERS: 1US FAERS
84LisinoprilFAERS: 1US FAERS
85LorazepamFAERS: 1US FAERS
86MDV 3100FAERS: 1US FAERS
87MetforminFAERS: 1US FAERS
88MetoprololFAERS: 1US FAERS
89ModafinilFAERS: 1US FAERS
90NifedipineFAERS: 1US FAERS
91OctreotideFAERS: 1US FAERS
92Olmesartan MedoxomilFAERS: 1US FAERS
93OmeprazoleFAERS: 1US FAERS
94OmeprazoleFAERS: 1US FAERS
95PCI 32765FAERS: 1US FAERS
96Paliperidone PalmitateFAERS: 1US FAERS
97PhenylephrineFAERS: 1US FAERS
98PioglitazoneFAERS: 1US FAERS
99PravastatinFAERS: 1US FAERS
100RanitidineFAERS: 1US FAERS
101RifabutinFAERS: 1US FAERS
102Risedronic AcidFAERS: 1US FAERS
103RivastigmineFAERS: 1US FAERS
104Ruxolitinib phosphateFAERS: 1US FAERS
105ScopolamineFAERS: 1US FAERS
106SuccinylcholineFAERS: 1US FAERS
107SumatriptanFAERS: 1US FAERS
108TamsulosinFAERS: 1US FAERS
109TenofovirFAERS: 1US FAERS
110TenofovirFAERS: 1US FAERS
111TerbinafineFAERS: 1US FAERS
112Tolterodine TartrateFAERS: 1
Canada Vigilance: 1
Canada Vigilance
US FAERS
113Venlafaxine HydrochlorideFAERS: 1US FAERS
114VerteporfinFAERS: 1US FAERS
115Zinc OxideFAERS: 1US FAERS
116acetaminophen, aspirin, caffeine drug combinationFAERS: 1US FAERS
117alfuzosinFAERS: 1US FAERS
118eletriptanFAERS: 1US FAERS
119eltrombopagFAERS: 1US FAERS
120exemestaneFAERS: 1US FAERS
121ledipasvir, sofosbuvir drug combinationFAERS: 1US FAERS
122lovastatin-niacin combinationFAERS: 1US FAERS
123oxybutyninFAERS: 1US FAERS
124pazopanibFAERS: 1US FAERS
125reviparinFAERS: 1US FAERS
126saxagliptinFAERS: 1US FAERS
127sofosbuvir-velpatasvir drug combinationFAERS: 1US FAERS
128venetoclaxFAERS: 1US FAERS
1292,2',4,4'-tetrabromodiphenyl ether27159543CTD
1302-(4-morpholino)ethyl-1-phenylcyclohexane-1-carboxylate24885036CTD
1312-butenal17319283CTD
1322-formyl-5-(hydroxymethyl)pyrrole-1-norleucine10965797CTD
1333-((4-(4-chlorophenyl)piperazin-1-yl)methyl)-1H-pyrrolo(2,3-b)pyridine21867702CTD
1344-hydroxy-2-nonenal10965797CTD
135Agent Orange26923711CTD
136Aluminum Chloride1933693CTD
137Aluminum1817796CTD
138Amitriptyline2108779CTD
139Bromocriptine21867702CTD
140Calcium Compounds1817796CTD
141Copper10694572CTD
142Dronabinol15204022CTD
143Lenalidomide16510725CTD
144Levodopa4743883
14962622
CTD
145Lithium18250315CTD
146M 14027159543CTD
147Magnesium;5-methoxy-2-[(4-methoxy-3,5-dimethylpyridin-2-yl)methylsulfinyl]benzimidazol-1-ide;trihydrateCanada Vigilance: 2Canada Vigilance
148Manganese Compounds1817796CTD
149Melatonin17014688CTD
150Mercury Compounds27377857CTD
151Minocycline15159491
15964487
17406652
CTD
152Nitrates18307039CTD
153Nitrites18307039CTD
154Nortriptyline17686041CTD
155OctreotideCanada Vigilance: 1Canada Vigilance
156Polychlorinated Biphenyls27159543CTD
157Polyvinyl Chloride24552493CTD
158Promethazine17686041CTD
159Pyrethrins22521219CTD
160Radium26923711CTD
161Resveratrol24252177
24885036
CTD
162Selenic Acid21134276CTD
163Selenious Acid23732511CTD
164Selenium19891121
23732511
CTD
165kenpaullone23602540CTD
166olesoxime17496168
20721828
CTD
167pentachlorobenzene27159543CTD
Similar ADE(s)
NameSemantic Similarity
1Spinal Muscular Atrophy53.1%
2Progressive Muscular Atrophy53.1%
3Progressive bulbar palsy41.7%
4Bulbar palsy41.7%
5Multiple System Atrophy39.3%
6Subacute Combined Degeneration37.9%
7Stiff-Person Syndrome37.5%
8Prion Diseases34.4%
9Parkinson Disease33.5%
10Lewy Body Disease32.7%
11Poliomyelitis30.9%
12Meningoencephalitis30.8%
13Myelitis30.3%
14Epidural Abscess30%
15Encephalomyelitis28.7%
16Myelitis, Transverse28.4%
17Striatonigral Degeneration28.1%
18Spinal Cord Injuries27.5%
19Tauopathies26.8%
20Progressive supranuclear palsy26.8%
21Frontotemporal dementia26.6%
22Ocular Motility Disorders26%
23Cyclophoria26%
24Friedreich Ataxia25.5%
25Shy-Drager Syndrome25.3%
26Dystonia Musculorum Deformans24.9%
27Polyradiculoneuropathy24.6%
28Polyradiculoneuritis24.6%
29Pneumocephalus24.3%
30Lambert-Eaton Myasthenic Syndrome24.2%
31Ophthalmoplegic Migraine23.6%
32Guillain-Barre Syndrome23.4%
33Opsoclonus-Myoclonus Syndrome23.3%
34Motor Neuron Disease23.2%
35Spinal Cord Neoplasms23.1%
36Chronic Fatigue Syndrome23%
37Complex Regional Pain Syndromes23%
38Restless Legs Syndrome22.9%
39Cranial nerve diseases22.9%
40Demyelinating Diseases22.9%
41Demyelination22.9%
42Chronobiology Disorders22.9%
43Huntington Disease22.8%
44Miller Fisher Syndrome22.6%
45Limbic Encephalitis22.4%
46Dandy-Walker Syndrome22.1%
47Syringomyelia22.1%
48Pneumorrhachis22.1%
49Hepatolenticular Degeneration22%
50Canavan Disease21.4%
51Alexander Disease21.4%
52Causalgia21.4%
53Myelinolysis, Central Pontine21.2%
54Amyotrophic Lateral Sclerosis21.2%
55Leukoencephalitis, Acute Hemorrhagic21.2%
56Amyloid Neuropathies, Familial21%
57Lafora Disease20.9%
58Unverricht-Lundborg Syndrome20.9%
59Scrapie20.8%
60Presenile dementia20.7%
61Senile dementia20.7%
62Leukoencephalopathy, Progressive Multifocal20.3%
63Peripheral Nerve Injuries20.3%
64Paraneoplastic Encephalomyelitis20.3%
65Brain Diseases20.1%
66Meningitis20.1%
67Movement Disorders20.1%
68Pachymeningitis20.1%
69Neuromuscular Junction Diseases20.1%
70Peripheral Nervous System Diseases20.1%
71Trauma, Nervous System20.1%
72Myasthenia Gravis20.1%
73Asterixis20.1%
74Ballismus20.1%
75Marchiafava-Bignami Disease20%
76Subdural Effusion19.8%
77Parkinsonian Disorders19.8%
78Lupus Vasculitis, Central Nervous System19.8%
79Nervous System Neoplasms19.7%
80Neurologic Manifestations19.7%
81Neurotoxicity Syndromes19.7%
82MPTP Poisoning19.3%
83Central Cord Syndrome19.2%
84Autonomic Dysreflexia19.1%
85Conus Medullaris Syndrome19.1%
86Spinal Cord Vascular Diseases19.1%
87Brain Diseases, Metabolic18.7%
88Myotonia Congenita18.4%
89Paraneoplastic Cerebellar Degeneration18.3%
90Dementia, Vascular18.3%
91Charcot-Marie-Tooth Disease18%
92Refsum Disease17.9%
93Myotonic Dystrophy17.8%
94Botulism17.8%
95Brain Abscess17.8%
96Central Nervous System Infection17.7%
97Myopathy17.7%
98Dyskinesia, Drug-Induced17.6%
99Neuroleptic Malignant Syndrome17.5%
100Sleep Wake Disorders17.5%
101Epilepsy, Post-Traumatic17.5%
102Meningitis, Bacterial17.4%
103Meningitis, Fungal17.4%
104Encephalomyelitis, Acute Disseminated17.2%
105Polyradiculoneuropathy, Chronic Inflammatory Demyelinating17.2%
106Neuromyelitis Optica17.2%
107Neuromuscular Diseases17.1%
108Meige Syndrome16.9%
109Brachial Plexus Neuritis16.9%
110Neuralgic Amyotrophy16.9%
111Cerebral Ventriculitis16.9%
112Mitochondrial Encephalomyopathies16.8%
113Brain Injuries16.6%
114Brain Neoplasms16.5%
115Tuberous Sclerosis16.4%
116Olfactory Nerve Injuries16.1%
117Akathisia, Drug-Induced16.1%
118Reflex Sympathetic Dystrophy16%
119Tuberculosis, Meningeal15.6%
120Cerebellar Neoplasms15.5%
121Ataxia Telangiectasia15.5%
122Tarsal Tunnel Syndrome15.5%
123Cauda Equina Syndrome15.5%
124Posterior Leukoencephalopathy Syndrome15.5%
125Posterior reversible encephalopathy syndrome15.5%
126Sleep Disorders, Circadian Rhythm15.2%
127Brain Hemorrhage, Traumatic15%
128Myasthenia Gravis, Autoimmune, Experimental14.9%
129Adrenoleukodystrophy14.9%
130Creutzfeldt-Jakob disease14.8%
131Central Nervous System Cysts14.8%
132Basal Ganglia Cerebrovascular Disease14.8%
133Acrodynia14.8%
134Facial Nerve Injuries14.5%
135MELAS Syndrome14.2%
136Spinal Cord Ischemia14.2%
137Myoclonic Epilepsy14%
138Epilepsy, Temporal Lobe14%
139Epilepsy, Rolandic14%
140Benign Rolandic Epilepsy14%
141Vasculitis, Central Nervous System14%
142Chorea14%
143Neuronal Ceroid-Lipofuscinoses13.9%
144Toxoplasmosis, Cerebral13.9%
145Mitochondrial Myopathies13.8%
146Carotid Artery Injuries13.7%
147Brain Death13.6%
148Carpal Tunnel Syndrome13.6%
149Vascular Headaches13.6%
150Hypoxia-Ischemia, Brain13.5%
151Sciatica13.5%
152Dysautonomia13.4%
153Vagus Nerve Disorder13.4%
154Glossopharyngeal Neuralgia13.4%
155Abducens Nerve Diseases13.4%
156Heavy Metal Poisoning, Nervous System13.4%
157Trochlear Nerve Diseases13.4%
158Pituitary Adenoma13.3%
159Pituitary Neoplasms13.3%
160Akinetic Mutism13.3%
161Amblyopia13.3%
162Anoxic Encephalopathy13.3%
163Arachnoiditis13.3%
164Basal Ganglia Diseases13.3%
165Brain Damage, Chronic13.3%
166Cerebellar Diseases13.3%
167Encephalitis13.3%
168Encephalomalacia13.3%
169Epilepsy13.3%
170Horner Syndrome13.3%
171Hydrocephalus13.3%
172Congenital Hydrocephalus13.3%
173Hypothalamic Diseases13.3%
174Aseptic Meningitis13.3%
175Neuritis13.3%
176Polyneuritis13.3%
177Radiculitis13.3%
178Thalamic Diseases13.3%
179Intracranial Hypertension13.3%
180Polyneuropathy13.3%
181Mononeuritis13.3%
182Aura13.3%
183Leukoencephalopathy13.3%
184Essential Tremor13.3%
185Neuroaxonal Dystrophies13.3%
186Familial Tremor13.3%
187Headache Disorders13.3%
188Mononeuropathies13.3%
189Intracranial Hypotension13.3%
190Brachial Plexus Neuropathies13.3%
191Radiculopathy13.3%
192Mononeuropathy Multiplex13.3%
193Nerve Root Compression13.3%
194Brain Edema13.3%
195Brain Hypoxia13.3%
196Aqueductal Stenosis13.3%
197Writer's Cramp13.3%
198Brain Diseases, Metabolic, Inborn13.2%
199Multiple Sclerosis13.2%
200Nocturnal Myoclonus Syndrome13.2%
201Leukomalacia, Periventricular13.2%
202Alstrom Syndrome12.9%
203Basal Ganglia Hemorrhage12.8%
204Juvenile Myoclonic Epilepsy12.6%
205Myoclonic Epilepsies, Progressive12.6%
206Neuritis, Autoimmune, Experimental12.4%
207Cockayne Syndrome12.3%
208Brain Injuries, Diffuse12.3%
209Traumatic Brain Injury12.3%
210Cerebellar Ataxia12.3%
211Supratentorial Neoplasms12.3%
212Torticollis12.3%
213Cubital Tunnel Syndrome12.2%
214Meningitis, Cryptococcal12%
215Meningitis, Listeria12%
216Subacute Sclerosing Panencephalitis12%
217Jet Lag Syndrome12%
218Meningitis, Haemophilus12%
219Meningitis, Pneumococcal12%
220Ophthalmoplegia11.9%
221External Ophthalmoplegia11.9%
222Optic Neuropathy11.8%
223Optic Atrophy, Hereditary, Leber11.7%
224Anterior Spinal Artery Syndrome11.7%
225Putaminal Hemorrhage11.6%
226Amyloidosis11.6%
227Facial Nerve Diseases11.6%
228Craniocerebral Trauma11.6%
229Parasomnia11.6%
230Dyssomnias11.6%
231Vestibulocochlear Nerve Diseases11.5%
232Cerebrovascular Disorders11.5%
233Decerebrate State11.5%
234Hemiparesis11.5%
235Hydranencephaly11.5%
236Meningism11.5%
237Myositis11.5%
238Neural Tube Defects11.5%
239Paresis11.5%
240Seizures11.5%
241Sensation Disorders11.5%
242Tethered Cord Syndrome11.5%
243Central Nervous System Neoplasms11.5%
244Complex partial seizures11.5%
245Iniencephaly11.5%
246Craniorachischisis11.5%
247Cerebrovascular Insufficiency11.5%
248Isaacs syndrome11.5%
249Exencephaly11.5%
250Monoparesis11.5%
251Septo-Optic Dysplasia11.5%
252Cortical Dysplasia11.5%
253Dementia11.5%
254Myotonic Disorders11.5%
255Neurogenic Inflammation11.5%
256Central Nervous System Fungal Infections11.5%
257Gait Disorders, Neurologic11.5%
258Myasthenic Syndromes, Congenital11.5%
259Neuromuscular Manifestations11.5%
260Malformations of Cortical Development11.5%
261Sweating, Gustatory11.4%
262Auriculotemporal Syndrome11.4%
263Infarction, Middle Cerebral Artery11.4%
264Infarction, Anterior Cerebral Artery11.4%
265Infarction, Posterior Cerebral Artery11.4%
266Persistent Vegetative State11.4%
267Diabetic Neuropathies11.4%
268Diabetic Amyotrophy11.4%
269Diabetic Autonomic Neuropathy11.4%
270Neuralgia11.3%
271Neuropathic pain11.3%
272Cerebral Amyloid Angiopathy11.2%
273Reye Syndrome11.2%
274Amnesia, Transient Global11.1%
275Hepatic Encephalopathy11.1%
276Alice in Wonderland Syndrome11.1%
277Familial Periodic Paralysis11.1%
278neurofibroma11%
279Tardive Dyskinesia11%
280Leigh Disease11%
281Pituitary Apoplexy11%
282Brain Concussion11%
283Brain Infarction10.9%
284Vocal Cord Paralysis10.7%
285Subarachnoid Hemorrhage, Traumatic10.5%
286Carotid Artery, Internal, Dissection10.5%
287Kearns-Sayre syndrome10.5%
288Pupil Disorders10.3%
289Neurobehavioral Manifestations10.3%
290Hand-Arm Vibration Syndrome10.3%
291Coma, Post-Head Injury10.3%
292Cerebrospinal Fluid Otorrhea10.2%
293Cerebrospinal Fluid Rhinorrhea10.2%
294Gait Ataxia10.2%
295Diffuse Axonal Injury10.2%
296Vertebral Artery Dissection10.2%
297Brain Stem Neoplasms10.2%
298Fibromyalgia10.1%
299Central Nervous System Bacterial Infections10.1%
300Medial Tibial Stress Syndrome10.1%
301Spinal Cord Diseases10.1%
302Uveomeningoencephalitic Syndrome10%
303Sturge-Weber Syndrome10%
304Vertigo10%
305Eosinophilia-Myalgia Syndrome10%
306Alcohol-Induced Disorders, Nervous System10%
307West Nile Fever10%
308Optic Nerve Glioma9.9%
309Cerebral Palsy9.9%
310Epilepsies, Partial9.9%
311Epilepsy, Generalized9.9%
312Pseudotumor Cerebri9.9%
313Sciatic Neuropathy9.9%
314Hypertensive Encephalopathy9.9%
315Ulnar Neuropathies9.9%
316Lesion of Sciatic Nerve9.9%
317Simple Partial Seizures9.9%
318Epilepsy, Reflex9.9%
319Ulnar Neuritis9.9%
320Radial nerve compression9.9%
321Radial Tunnel Syndrome9.9%
322Peroneal Neuropathies9.9%
323Radial Neuropathy9.9%
324Median Neuropathy9.9%
325Sciatic Nerve Palsy9.9%
326Femoral Neuropathy9.9%
327Tibial Neuropathy9.9%
328Ulnar Nerve Palsy9.9%
329Radial nerve palsy9.9%
330Headache Disorders, Primary9.9%
331Headache Disorders, Secondary9.9%
332Medication overuse headache9.9%
333Multiple Sclerosis, Chronic Progressive9.8%
334Multiple Sclerosis, Relapsing-Remitting9.8%
335Galactosemias9.8%
336Urea Cycle Disorders, Inborn9.8%
337Tyrosinemias9.8%
338Cerebral Infarction9.7%
339Brain Stem Infarctions9.7%
340Carbamoyl-Phosphate Synthase I Deficiency Disease9.7%
341Wasting Syndrome9.7%
342Alcohol Withdrawal Seizures9.6%
343Menkes Kinky Hair Syndrome9.3%
344Moyamoya Disease9.3%
345Wernicke Encephalopathy9.3%
346Akathisia9.2%
347Restlessness9.2%
348Psychomotor Agitation9.2%
349Lateral Medullary Syndrome9.2%
350Choroid Plexus Papilloma9.1%
351Brain Contusion9.1%
352Voice Disorders9.1%
353Voice Disturbance9.1%
354Tetany9.1%
355Auditory Perceptual Disorders8.9%
356Fabry Disease8.9%
357Smith-Magenis syndrome8.9%
358Dural Arteriovenous Fistula8.9%
359Pituitary Diseases8.7%
360Homocystinuria8.6%
361Thoracic Outlet Syndrome8.6%
362Hypercalcemia8.5%
363Hypocalcemia8.5%
364Milk-Alkali Syndrome8.5%
365Carotid Artery Diseases8.5%
366Brain Ischemia8.5%
367Cerebrovascular accident8.5%
368Polymyositis8.5%
369Kluver-Bucy Syndrome8.5%
370Vasospasm, Intracranial8.5%
371Intracranial Arterial Diseases8.5%
372Gait Apraxia8.5%
373Giant Cell Arteritis8.5%
374Temporal Arteritis8.5%
375Tuberculosis, Central Nervous System8.4%
376Acid-Base Imbalance8.4%
377Calcium Metabolism Disorders8.4%
378Iron Metabolism Disorders8.4%
379Phosphorus Metabolism Disorders8.4%
380Water-Electrolyte Imbalance8.4%
381Lipid Metabolism Disorders8.4%
382Mitochondrial Diseases8.4%
383Glucose Metabolism Disorders8.4%
384Polyradiculopathy8.2%
385Post-Traumatic Headache8.2%
386Tension Headache8.2%
387Epilepsy, Complex Partial8.2%
388Migraine Disorders8.2%
389Abdominal Migraine8.2%
390Status Migrainosus8.2%
391Cervicogenic Headache8.2%
392Kernicterus8.2%
393Hypokalemic periodic paralysis8.2%
394Reflex, Abnormal7.9%
395Hyporeflexia7.9%
396Hyperreflexia7.9%
397Myalgia7.9%
398Pseudohypoparathyroidism7.9%
399Glycogen storage disease type II7.8%
400Optic Atrophy7.7%
401Optic Neuritis7.7%
402Papilledema7.7%
403Strabismus7.7%
404Tolosa-Hunt Syndrome7.7%
405Arsenic Poisoning7.7%
406Neurofibrosarcoma7.6%
407Facial Injuries7.6%
408Facial Neuralgia7.6%
409Sleep Talking7.6%
410Manganese Poisoning7.6%
411Sleep Disorders, Intrinsic7.6%
412Orthostatic intolerance7.6%
413Anosmia7.5%
414Ataxia7.5%
415Athetosis7.5%
416Catalepsy7.5%
417Dystonia7.5%
418Hemiplegia7.5%
419Locked-In Syndrome7.5%
420Meningeal Neoplasms7.5%
421Meningomyelocele7.5%
422Muscle Hypertonia7.5%
423Muscle hypotonia7.5%
424Myoclonus7.5%
425Myotonia7.5%
426Paraplegia7.5%
427Pseudobulbar Palsy7.5%
428Quadriplegia7.5%
429Spasm7.5%
430Spastic Paraplegia7.5%
431Status Epilepticus7.5%
432Taste Disorders7.5%
433Tremor7.5%
434Spina Bifida7.5%
435Monoplegia7.5%
436Hypokinesia7.5%
437Paraparesis7.5%
438Bradykinesia7.5%
439Waxy flexibility7.5%
440Action Tremor7.5%
441Resting Tremor7.5%
442Dysosmia7.5%
443Quadriparesis7.5%
444Mercury Poisoning, Nervous System7.5%
445Olfaction Disorders7.5%
446Myokymia7.5%
447Lead Poisoning, Nervous System7.5%
448Vestibular Neuronitis7.5%
449Somatosensory Disorders7.5%
450Hyperkinesia7.5%
451Intention tremor7.5%
452Hematoma, Subdural7.5%
453Hematoma, Epidural, Cranial7.5%
454Muscular Dystrophy7.5%
455Orbital Myositis7.5%
456Acoustic Neuroma7.5%
457Lipodystrophy7.5%
458Neuroaspergillosis7.4%
459Pyomyositis7.4%
460Intracranial Embolism and Thrombosis7.4%
461Cluster Headache7.4%
462Migraine with Aura7.4%
463Familial Hemiplegic Migraine7.4%
464Chronic Paroxysmal Hemicrania7.4%
465SUNCT Syndrome7.4%
466Paroxysmal Hemicrania7.4%
467Gaucher Disease7.4%
468Osteopenia7.2%
469Zellweger Syndrome7.2%
470Classical Lissencephalies and Subcortical Band Heterotopias7.1%
471Empty Sella Syndrome7.1%
472Hyperpituitarism7.1%
473Hypopituitarism7.1%
474Hypophysitis7.1%
475Rickets7.1%
476Cerebral Arterial Diseases7%
477Vertebrobasilar Insufficiency7%
478Basilar Artery Stenosis7%
479Vertebral Artery Stenosis7%
480Intracranial Hemorrhage, Hypertensive7%
481Transient Cerebral Ischemia7%
482Pseudorabies6.8%
483Vision Disorders6.8%
484Metamorphopsia6.8%
485Visual Impairment6.8%
486Optic Neuropathy, Ischemic6.8%
487Anterior Ischemic Optic Neuropathy6.8%
488Facial Hemiatrophy6.7%
489Melkersson-Rosenthal Syndrome6.7%
490Hematoma, Subdural, Intracranial6.7%
491Hematoma, Subdural, Chronic6.7%
492Hematoma, Subdural, Acute6.7%
493Anisocoria6.7%
494Confusion6.7%
495Facial paralysis6.7%
496Lethargy6.7%
497Memory Disorders6.7%
498Muscle Cramp6.7%
499Perceptual Disorders6.7%
500Psychomotor Disorders6.7%
501Tonic Pupil6.7%
502Anhedonia6.7%
503Disorientation6.7%
504Facial Paresis6.7%
505Memory Loss6.7%
506Hemisensory Neglect6.7%
507Dysacusis6.7%
508Sleep Bruxism6.6%
509Waterhouse-Friderichsen Syndrome6.6%
510Anencephaly6.6%
511Meningocele6.6%
512Muscular Atrophy6.6%
513Respiratory Paralysis6.6%
514Encephalocele6.6%
515POEMS Syndrome6.6%
516Postural Orthostatic Tachycardia Syndrome6.6%
517Neurosyphilis6.5%
518Alexia6.5%
519Dyslexia6.5%
520Tay-Sachs Disease6.5%
521Hyperprolactinemia6.3%
522Niemann-Pick Disease, Type C6.3%
523Subclavian Steal Syndrome6.3%
524Pick Disease of the Brain6.3%
525Toxoplasmosis, Congenital6.2%
526Malaria, Cerebral6.2%
527Carotid Stenosis6.2%
528Intracranial Aneurysm6.2%
529Welander Distal Myopathy6.2%
530Neurocysticercosis6.1%
531Intracranial Arteriosclerosis6.1%
532Cerebral Atherosclerosis6.1%
533Subarachnoid Hemorrhage6.1%
534Cerebral Arteriosclerosis6.1%
535Cerebral Hemorrhage6.1%
536Cerebral Thrombosis6.1%
537Intracranial Embolism6.1%
538Intracranial Thrombosis6.1%
539Duane Retraction Syndrome6%
540Consciousness Disorders6%
541Mental Retardation6%
542Muscle Weakness6%
543Depressed Level of Consciousness6%
544Mental deficiency6%
545Intellectual Disability6%
546Mobius Syndrome5.9%
547Bell Palsy5.9%
548Catatonia5.9%
549Herpes Zoster Oticus5.9%
550Hyperhomocysteinemia5.9%
551AIDS Dementia Complex5.9%
552Aphonia5.9%
553Sleep Deprivation5.9%
554Dysphonia5.9%
555Lyme Neuroborreliosis5.9%
556Esotropia5.7%
557Exotropia5.7%
558Hypotension, Orthostatic5.7%
559Sleep Apnea Syndromes5.7%
560Post-Exercise Hypotension5.7%
561Disorders of Excessive Somnolence5.6%
562Sleep Initiation and Maintenance Disorders5.6%
563Night Terrors5.6%
564Somnambulism5.6%
565Trigeminal Nerve Disorder5.6%
566Transient Insomnia5.6%
567Sleep Paralysis5.6%
568Chronic Insomnia5.6%
569REM Sleep Behavior Disorder5.6%
570Hypersomnia5.6%
571Dermal Sinus5.6%
572Dysgeusia5.6%
573Formication5.6%
574Hyperalgesia5.6%
575Hyperesthesia5.6%
576Hypesthesia5.6%
577Language Disorders5.6%
578Numbness5.6%
579Paresthesia5.6%
580Paraparesis, Spastic5.6%
581Spina Bifida Cystica5.6%
582Trismus5.6%
583Spina Bifida Occulta5.6%
584Epilepsia Partialis Continua5.6%
585Hypogeusia5.6%
586Meningeal Carcinomatosis5.6%
587Brown-Sequard Syndrome5.6%
588Lissencephaly5.6%
589Polymicrogyria5.6%
590Pachygyria5.6%
591Schizencephaly5.6%
592Lockjaw5.6%
593Allodynia5.6%
594Lead Poisoning, Nervous System, Childhood5.6%
595Lead Poisoning, Nervous System, Adult5.6%
596Periventricular Nodular Heterotopia5.6%
597Ageusia5.6%
598Dermatomyositis5.6%
599Acromegaly5.6%
600Sinus Thrombosis, Intracranial5.5%
601Muscular Dystrophy, Duchenne5.5%
602Lactose Intolerance5.5%
603Carotid Artery Thrombosis5.4%
604Smith-Lemli-Opitz Syndrome5.4%
605Familial Hypophosphatemic Rickets5.3%
606Cavernous Sinus Thrombosis5.2%
607Sagittal Sinus Thrombosis5.2%
608Primary amyloidosis5.1%
609Nutrition Disorders5.1%
610Eye Injuries5.1%
611Congenital nystagmus5%
612Acidosis5%
613Alkalosis5%
614Calcinosis5%
615Hyperglycemia5%
616Hyperinsulinism5%
617Hyperkalemia5%
618Hypernatremia5%
619Hypoglycemia5%
620Hypokalemia5%
621Hyponatremia5%
622Xanthomatosis5%
623Hypophosphatemia5%
624Metabolic acidosis5%
625Dyslipidemias5%
626Iron Overload5%
627Xanthoma5%
628Diplopia5%
629Muscle Rigidity5%
630Muscle Spasticity5%
631Scotoma5%
632Photophobia5%
633Cogwheel Rigidity5%
634Hemifacial Spasm5%
635Amaurosis5%
636Blindness5%
637Nuchal Rigidity5%
638Agnosia4.9%
639Apraxias4.9%
640Hallucinations4.9%
641Hemianopsia4.9%
642Hyperacusis4.9%
643Tinnitus4.9%
644Visual Agnosia4.9%
645Anosognosia4.9%
646Wernicke-Korsakoff Syndrome4.9%
647Phonophobia4.9%
648Hearing Loss4.9%
649Hypolipoproteinemias4.9%
650Sarcopenia4.9%
651Hyperphosphaturia4.9%
652Hyperlipoproteinemia Type IV4.9%
653Hyperlipoproteinemia Type V4.9%
654Aicardi's syndrome4.9%
655Hoarseness4.8%
656Alcohol Withdrawal Delirium4.8%
657Osteomalacia4.8%
658Mucopolysaccharidosis II4.7%
659Sleep Apnea, Obstructive4.7%
660Sleep Apnea, Central4.7%
661Narcolepsy4.7%
662Trigeminal Neuralgia4.7%
663Kleine-Levin Syndrome4.7%
664Agraphia4.7%
665Anomia4.7%
666Cluttering4.7%
667Language Development Disorders4.7%
668Speech Disorders4.7%
669Syncope4.7%
670Stupor4.7%
671Dysgraphia4.7%
672Presyncope4.7%
673Dyslalia4.7%
674Prader-Willi Syndrome4.6%
675Nelson Syndrome4.6%
676Congenital Hyperinsulinism4.5%
677Prolactinoma4.4%
678Growth Hormone-Secreting Pituitary Adenoma4.4%
679Amnesia4.4%
680Delirium4.4%
681Dissociative Amnesia4.4%
682Color blindness4.4%
683Global Amnesia4.4%
684Cri-du-Chat Syndrome4.4%
685Down Syndrome4.4%
686Trisomy 214.4%
687Holoprosencephaly4.4%
688Diabetes Mellitus4.4%
689Meningioma4.4%
690Williams Syndrome4.4%
691Microcephaly4.4%
692Macrocephaly4.4%
693Porencephaly4.3%
694Diabetic Ketoacidosis4.3%
695Dehydration4.3%
696Lipomatosis4.3%
697Water Intoxication4.3%
698Werner Syndrome4.3%
699Hyperlipidemia, Familial Combined4.3%
700Achlorhydria4.3%
701Amino Acid Metabolism, Inborn Errors4.3%
702Bloom Syndrome4.3%
703Carbohydrate Metabolism, Inborn Errors4.3%
704Metal Metabolism, Inborn Errors4.3%
705Osteoporosis4.3%
706Progeria4.3%
707Lysosomal Storage Diseases4.3%
708Bone Demineralization, Pathologic4.3%
709Cytochrome-c Oxidase Deficiency4.3%
710Peroxisomal Disorders4.3%
711Post-Traumatic Osteoporosis4.3%
712Celiac Disease4.2%
713Sprue, Tropical4.2%
714Steatorrhea4.2%
715Sprue4.2%
716Cataplexy4.2%
717Aphasia4.2%
718Articulation Disorders4.2%
719Echolalia4.2%
720Stuttering4.2%
721Dysphasia4.2%
722Eye Burns4.1%
723Amaurosis Fugax4.1%
724Blindness, Cortical4.1%
725Dyscalculia4.1%
726Rett Syndrome4.1%
727Deafness4.1%
728Hearing Loss, Sudden4.1%
729Gerstmann Syndrome4.1%
730Hearing Loss, Bilateral4.1%
731Hearing Loss, High-Frequency4.1%
732Hearing Loss, Mixed Conductive-Sensorineural4.1%
733Prosopagnosia4.1%
734Apraxia, Ideomotor4.1%
735Charles Bonnet Syndrome4.1%
736Hearing Loss, Unilateral4.1%
737Complete Hearing Loss4.1%
738Alien Hand Syndrome4.1%
739Deaf Mutism4.1%
740Hyperlipoproteinemia Type III4%
741Dysarthria4%
742HIV Wasting Syndrome4%
743Phantom pain3.9%
744Phantom Limb Pain3.9%
745Renal tubular acidosis3.9%
746Glycosuria3.7%
747Mutism3.7%
748Selective Mutism3.7%
749Corneal Scar3.7%
750Hypoalphalipoproteinemias3.7%
751Retrograde amnesia3.6%
752Amnesia, Anterograde3.6%
753Renal Osteodystrophy3.6%
754Renal rickets3.6%
755HIV-Associated Lipodystrophy Syndrome3.6%
756Alexia, Pure3.5%
757Porphyrias, Hepatic3.3%
758Necrobiosis Lipoidica Diabeticorum3.3%
759Acidosis, Lactic3.3%
760Calciphylaxis3.3%
761Hemosiderosis3.3%
762Ketosis3.3%
763Rubinstein-Taybi Syndrome3.3%
764Ketonuria3.3%
765Ketoacidosis3.3%
766Ketonemia3.3%
767Vascular calcification3.3%
768Fanconi Anemia3.3%
769Nesidioblastosis3.3%
770Corneal Perforation3.3%
771Fragile X Syndrome3.3%
772Glycosuria, Renal3.3%
773Mucopolysaccharidosis III2.9%
774Acidosis, Respiratory2.8%
775Adiposis Dolorosa2.8%
776Alkalosis, Respiratory2.8%
777Alkaptonuria2.8%
778Glycogen Storage Disease2.8%
779Hypophosphatasia2.8%
780Insulin Resistance2.8%
781Osteoporosis, Postmenopausal2.8%
782Propionic acidemia2.8%
783Dihydropyrimidine Dehydrogenase Deficiency2.8%
784Cystinosis2.8%
785Child Nutrition Disorders2.8%
786Hypervitaminosis A2.8%
787Infant Nutrition Disorders2.8%
788Malnutrition2.8%
789Gestational Diabetes2.5%
790Latent Autoimmune Diabetes in Adults2.5%
791Diabetes Mellitus, Experimental2.5%
792Nephrocalcinosis2.5%
793Hypercholesterolemia2.5%
794Hyperlipoproteinemias2.5%
795Hypertriglyceridemia2.5%
796Sjogren-Larsson Syndrome2.5%
797Xeroderma Pigmentosum2.3%
798Variegate Porphyria2.2%
799Acute intermittent porphyria2.2%
800Porphyria Cutanea Tarda2.2%
801Renal Aminoacidurias2.2%
802Fanconi Syndrome2.2%
803Pseudohypoaldosteronism2.2%
804Liddle Syndrome2.2%
805Glycogen Storage Disease Type I2.1%
806Glycogen Storage Disease Type V2.1%
807Gout2%
808Antley-Bixler Syndrome Phenotype2%
809CREST Syndrome1.8%
810Albinism1.7%
811Deficiency Diseases1.7%
812Starvation1.7%
813Refeeding Syndrome1.7%
814Cystinuria1.6%
815Arthritis, Gouty1.5%
816Ichthyosis, X-Linked1.4%
817Kwashiorkor1.1%
818Magnesium Deficiency1.1%
819Potassium Deficiency1.1%
820Protein Deficiency1.1%
821Avitaminosis1.1%
822Obesity1.1%
823Ascorbic Acid Deficiency0.8%
824Vitamin A Deficiency0.8%
825Vitamin D Deficiency0.8%
826Vitamin E Deficiency0.8%
827Marasmus0.8%
828Obesity, Abdominal0.8%
829Pediatric Obesity0.7%
830Folic Acid Deficiency0.7%
831Pellagra0.7%
832Thiamine Deficiency0.7%
833Vitamin B 12 Deficiency0.7%
834Vitamin B 6 Deficiency0.7%
835Pyridoxine Deficiency0.7%
836Vitamin K Deficiency0.6%
837Beriberi0.6%
838Anemia, Pernicious0.5%
839Scurvy0.5%
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