MetaADEDB 2.0 @ LMMD
Prion Diseases
(UMLS:C0162534)
Definition:
A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature DEMENTIA; ATAXIA; and a fatal outcome. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The older literature occasionally refers to these as unconventional SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83)
UMLS ID:
C0162534
MeSH ID:
D017096
Classification:
Name:
Nervous System Diseases
MeSH Tree Number(s):
C10.228.228.800|C10.574.843
Synonym(s)
1.
Prion Diseases
2.
Prion Disease
3.
Prion disease
4.
Prion disease, NOS
5.
Prion diseases
6.
Prion protein disease
7.
disease prion
8.
disease prions
9.
diseases prion
10.
diseases prions
11.
encephalopathies spongiform
12.
prion disease
13.
prion disease of central nervous system
14.
prion diseases
15.
spongiform encephalopathy
Associated Drug(s)
Similar ADE(s)
NameSemantic Similarity
1Encephalomyelitis51.7%
2Meningoencephalitis51.1%
3Myelitis44.1%
4Epidural Abscess43.3%
5Multiple System Atrophy40.7%
6Motor Neuron Disease38.6%
7Parkinson Disease37.7%
8Subdural Effusion37%
9Tauopathies34.9%
10Amyotrophic Lateral Sclerosis34.4%
11Spinal Muscular Atrophy33.8%
12Progressive Muscular Atrophy33.8%
13Lewy Body Disease33.4%
14Cerebral Ventriculitis33.3%
15Striatonigral Degeneration30.9%
16Brain Diseases30.2%
17Meningitis30.2%
18Movement Disorders30.2%
19Pachymeningitis30.2%
20Spinal Cord Diseases30.2%
21Poliomyelitis30.2%
22Subacute Combined Degeneration30.1%
23Meningitis, Bacterial29.5%
24Meningitis, Fungal29.5%
25Limbic Encephalitis29.4%
26Brain Abscess29.4%
27Central Nervous System Fungal Infections29.3%
28Ocular Motility Disorders29%
29Cyclophoria29%
30Dystonia Musculorum Deformans27.8%
31Myelitis, Transverse27.2%
32Progressive bulbar palsy27.1%
33Bulbar palsy27.1%
34Tuberculosis, Meningeal27%
35Parkinsonian Disorders26.9%
36Cranial nerve diseases26.8%
37Demyelinating Diseases26.8%
38Demyelination26.8%
39Neuromuscular Diseases26.8%
40Chronobiology Disorders26.8%
41Pneumocephalus26.8%
42Shy-Drager Syndrome26.5%
43Stiff-Person Syndrome26.4%
44Progressive supranuclear palsy25.7%
45Leukoencephalopathy, Progressive Multifocal25.3%
46Presenile dementia24.2%
47Senile dementia24.2%
48Lupus Vasculitis, Central Nervous System24.2%
49Marchiafava-Bignami Disease23.9%
50Lafora Disease23.7%
51Unverricht-Lundborg Syndrome23.7%
52Central Nervous System Bacterial Infections23.6%
53Dandy-Walker Syndrome23.6%
54Meige Syndrome23.3%
55Spinal Cord Injuries22.9%
56Huntington Disease22.8%
57Toxoplasmosis, Cerebral22.6%
58Asterixis21.9%
59Ballismus21.9%
60Opsoclonus-Myoclonus Syndrome21.6%
61Posterior Leukoencephalopathy Syndrome21.6%
62Posterior reversible encephalopathy syndrome21.6%
63Tuberculosis, Central Nervous System21.5%
64Paraneoplastic Encephalomyelitis20.8%
65Trauma, Nervous System20.8%
66Friedreich Ataxia20.7%
67Autonomic Dysreflexia20.7%
68Complex Regional Pain Syndromes20.7%
69MPTP Poisoning20.6%
70Polyradiculoneuropathy20.6%
71Polyradiculoneuritis20.6%
72Akinetic Mutism20.5%
73Anoxic Encephalopathy20.5%
74Arachnoiditis20.5%
75Basal Ganglia Diseases20.5%
76Brain Damage, Chronic20.5%
77Cerebellar Diseases20.5%
78Encephalitis20.5%
79Encephalomalacia20.5%
80Epilepsy20.5%
81Hydrocephalus20.5%
82Congenital Hydrocephalus20.5%
83Hypothalamic Diseases20.5%
84Aseptic Meningitis20.5%
85Syringomyelia20.5%
86Thalamic Diseases20.5%
87Intracranial Hypertension20.5%
88Aura20.5%
89Leukoencephalopathy20.5%
90Essential Tremor20.5%
91Neuroaxonal Dystrophies20.5%
92Familial Tremor20.5%
93Headache Disorders20.5%
94Intracranial Hypotension20.5%
95Brain Edema20.5%
96Brain Hypoxia20.5%
97Aqueductal Stenosis20.5%
98Pneumorrhachis20.5%
99Writer's Cramp20.5%
100Ophthalmoplegic Migraine20.4%
101Subacute Sclerosing Panencephalitis20.3%
102Nervous System Neoplasms20%
103Neurologic Manifestations20%
104Neurotoxicity Syndromes20%
105Paraneoplastic Cerebellar Degeneration20%
106Myoclonic Epilepsy19.8%
107Epilepsy, Temporal Lobe19.8%
108Meningitis, Cryptococcal19.8%
109Epilepsy, Rolandic19.8%
110Benign Rolandic Epilepsy19.8%
111Epilepsy, Post-Traumatic19.8%
112Meningitis, Listeria19.7%
113Meningitis, Haemophilus19.7%
114Meningitis, Pneumococcal19.7%
115Restless Legs Syndrome19.6%
116Lambert-Eaton Myasthenic Syndrome19.4%
117Leukoencephalitis, Acute Hemorrhagic19.3%
118Dementia, Vascular19.2%
119Chronic Fatigue Syndrome19%
120Neuroleptic Malignant Syndrome19%
121Myelinolysis, Central Pontine19%
122Brain Injuries18.9%
123Brain Neoplasms18.8%
124Spinal Cord Neoplasms18.8%
125Basal Ganglia Cerebrovascular Disease18.7%
126Juvenile Myoclonic Epilepsy18.1%
127Myoclonic Epilepsies, Progressive18.1%
128Canavan Disease18%
129Alexander Disease18%
130Miller Fisher Syndrome18%
131Cerebellar Neoplasms18%
132Encephalomyelitis, Acute Disseminated17.7%
133Guillain-Barre Syndrome17.6%
134Neuroaspergillosis17.4%
135Causalgia17.3%
136Vascular Headaches17.3%
137Hypoxia-Ischemia, Brain17.2%
138Hepatolenticular Degeneration16.8%
139Myotonia Congenita16.8%
140Peripheral Nerve Injuries16.7%
141West Nile Fever16.5%
142Charcot-Marie-Tooth Disease16.5%
143Myasthenia Gravis16.4%
144Frontotemporal dementia16.4%
145Brain Death16.4%
146Central Cord Syndrome16.3%
147Dysautonomia16.3%
148Vagus Nerve Disorder16.3%
149Glossopharyngeal Neuralgia16.3%
150Abducens Nerve Diseases16.3%
151Heavy Metal Poisoning, Nervous System16.3%
152Neuromuscular Junction Diseases16.3%
153Trochlear Nerve Diseases16.3%
154Peripheral Nervous System Diseases16.3%
155Sleep Wake Disorders16.2%
156Dyskinesia, Drug-Induced16.1%
157Chorea16%
158Cerebral Palsy15.7%
159Epilepsies, Partial15.7%
160Epilepsy, Generalized15.7%
161Pseudotumor Cerebri15.7%
162Hypertensive Encephalopathy15.7%
163Simple Partial Seizures15.7%
164Epilepsy, Reflex15.7%
165Headache Disorders, Primary15.7%
166Headache Disorders, Secondary15.7%
167Medication overuse headache15.7%
168Akathisia, Drug-Induced15.6%
169Leukomalacia, Periventricular15.6%
170Olfactory Nerve Injuries15.6%
171Brain Diseases, Metabolic15.5%
172Cerebrovascular Disorders15.5%
173Cerebrovascular Insufficiency15.5%
174Dementia15.5%
175Conus Medullaris Syndrome15.5%
176Spinal Cord Vascular Diseases15.5%
177Pseudorabies15.2%
178Reflex Sympathetic Dystrophy15.1%
179Nocturnal Myoclonus Syndrome15.1%
180Polyradiculoneuropathy, Chronic Inflammatory Demyelinating15%
181Brain Hemorrhage, Traumatic14.8%
182Toxoplasmosis, Congenital14.8%
183Malaria, Cerebral14.7%
184Neurocysticercosis14.6%
185Brain Injuries, Diffuse14.6%
186Traumatic Brain Injury14.6%
187Amblyopia14.6%
188Cerebellar Ataxia14.5%
189Supratentorial Neoplasms14.5%
190Torticollis14.5%
191Neuromyelitis Optica14.5%
192Neurosyphilis14.3%
193Basal Ganglia Hemorrhage14.2%
194Sleep Disorders, Circadian Rhythm14.1%
195Carotid Artery Injuries14%
196Persistent Vegetative State13.8%
197Pituitary Adenoma13.7%
198Pituitary Neoplasms13.7%
199Tuberous Sclerosis13.6%
200Myotonic Dystrophy13.6%
201Botulism13.6%
202Central Nervous System Cysts13.6%
203Vasculitis, Central Nervous System13.5%
204Multiple Sclerosis13.4%
205Post-Traumatic Headache13.4%
206Tension Headache13.4%
207Epilepsy, Complex Partial13.4%
208Migraine Disorders13.4%
209Abdominal Migraine13.4%
210Status Migrainosus13.4%
211Cervicogenic Headache13.4%
212Pituitary Apoplexy13.3%
213Facial Nerve Injuries13.3%
214Brachial Plexus Neuritis13.3%
215Neuralgic Amyotrophy13.3%
216Tardive Dyskinesia13.2%
217Brain Infarction13.1%
218Putaminal Hemorrhage13.1%
219Infarction, Middle Cerebral Artery12.9%
220Infarction, Anterior Cerebral Artery12.9%
221Infarction, Posterior Cerebral Artery12.9%
222Myopathy12.7%
223Optic Neuropathy12.7%
224Creutzfeldt-Jakob disease12.7%
225Diffuse Axonal Injury12.5%
226Tarsal Tunnel Syndrome12.4%
227Cauda Equina Syndrome12.4%
228Brain Stem Neoplasms12.4%
229Pituitary Diseases12.4%
230Horner Syndrome12.3%
231Facial Nerve Diseases12.3%
232Craniocerebral Trauma12.3%
233Parasomnia12.3%
234Dyssomnias12.3%
235Cluster Headache12.3%
236Migraine with Aura12.3%
237Familial Hemiplegic Migraine12.3%
238Chronic Paroxysmal Hemicrania12.3%
239SUNCT Syndrome12.3%
240Paroxysmal Hemicrania12.3%
241Lyme Neuroborreliosis12.2%
242Vestibulocochlear Nerve Diseases12.1%
243Decerebrate State12.1%
244Hemiparesis12.1%
245Hydranencephaly12.1%
246Meningism12.1%
247Neural Tube Defects12.1%
248Paresis12.1%
249Seizures12.1%
250Sensation Disorders12.1%
251Tethered Cord Syndrome12.1%
252Central Nervous System Neoplasms12.1%
253Complex partial seizures12.1%
254Iniencephaly12.1%
255Craniorachischisis12.1%
256Exencephaly12.1%
257Monoparesis12.1%
258Septo-Optic Dysplasia12.1%
259Cortical Dysplasia12.1%
260Neurogenic Inflammation12.1%
261Gait Disorders, Neurologic12.1%
262Neuromuscular Manifestations12.1%
263Malformations of Cortical Development12.1%
264Sweating, Gustatory12%
265Auriculotemporal Syndrome12%
266Acrodynia12%
267Cerebral Infarction11.9%
268Brain Stem Infarctions11.9%
269Ataxia Telangiectasia11.9%
270Refsum Disease11.8%
271Amnesia, Transient Global11.8%
272Carotid Artery Diseases11.8%
273Brain Ischemia11.8%
274Cerebrovascular accident11.8%
275Kluver-Bucy Syndrome11.8%
276Vasospasm, Intracranial11.8%
277Spinal Cord Ischemia11.8%
278Intracranial Arterial Diseases11.8%
279Myasthenia Gravis, Autoimmune, Experimental11.6%
280Choroid Plexus Papilloma11.4%
281Neuritis11.4%
282Polyneuritis11.4%
283Radiculitis11.4%
284Polyneuropathy11.4%
285Mononeuritis11.4%
286Mononeuropathies11.4%
287Brachial Plexus Neuropathies11.4%
288Radiculopathy11.4%
289Mononeuropathy Multiplex11.4%
290Nerve Root Compression11.4%
291Lateral Medullary Syndrome11.3%
292Ophthalmoplegia11.3%
293External Ophthalmoplegia11.3%
294Brain Concussion11%
295Alice in Wonderland Syndrome11%
296Coma, Post-Head Injury11%
297Amyloid Neuropathies, Familial10.9%
298Subarachnoid Hemorrhage, Traumatic10.8%
299Carotid Artery, Internal, Dissection10.8%
300Moyamoya Disease10.8%
301Jet Lag Syndrome10.6%
302Multiple Sclerosis, Chronic Progressive10.6%
303Multiple Sclerosis, Relapsing-Remitting10.6%
304Alstrom Syndrome10.5%
305Mitochondrial Encephalomyopathies10.4%
306Brain Contusion10.4%
307Vertebral Artery Dissection10.4%
308Neuronal Ceroid-Lipofuscinoses10.4%
309Prion Diseases10.3%
310Empty Sella Syndrome10.2%
311Hyperpituitarism10.2%
312Hypopituitarism10.2%
313Hypophysitis10.2%
314Pupil Disorders10%
315Neurobehavioral Manifestations10%
316Carpal Tunnel Syndrome10%
317Cerebral Arterial Diseases10%
318Vertebrobasilar Insufficiency10%
319Anterior Spinal Artery Syndrome10%
320Basilar Artery Stenosis10%
321Vertebral Artery Stenosis10%
322Intracranial Hemorrhage, Hypertensive10%
323Transient Cerebral Ischemia10%
324Cerebrospinal Fluid Otorrhea9.9%
325Cerebrospinal Fluid Rhinorrhea9.9%
326Neuritis, Autoimmune, Experimental9.9%
327Gait Ataxia9.9%
328neurofibroma9.9%
329Sciatica9.9%
330Vocal Cord Paralysis9.8%
331Uveomeningoencephalitic Syndrome9.6%
332Sturge-Weber Syndrome9.5%
333Vertigo9.5%
334Alcohol-Induced Disorders, Nervous System9.5%
335Waterhouse-Friderichsen Syndrome9.5%
336Reye Syndrome9.4%
337Adrenoleukodystrophy9.4%
338Intracranial Embolism and Thrombosis9.3%
339Hepatic Encephalopathy9.3%
340Cubital Tunnel Syndrome9.2%
341Cockayne Syndrome9.2%
342Hyperprolactinemia9.2%
343MELAS Syndrome9.1%
344Optic Atrophy, Hereditary, Leber9.1%
345Auditory Perceptual Disorders9.1%
346Subclavian Steal Syndrome9.1%
347Pick Disease of the Brain9.1%
348Sciatic Neuropathy9%
349Ulnar Neuropathies9%
350Lesion of Sciatic Nerve9%
351Ulnar Neuritis9%
352Radial nerve compression9%
353Radial Tunnel Syndrome9%
354Peroneal Neuropathies9%
355Radial Neuropathy9%
356Median Neuropathy9%
357Sciatic Nerve Palsy9%
358Femoral Neuropathy9%
359Tibial Neuropathy9%
360Ulnar Nerve Palsy9%
361Postural Orthostatic Tachycardia Syndrome9%
362Radial nerve palsy9%
363Myositis8.6%
364Optic Atrophy8.6%
365Optic Neuritis8.6%
366Papilledema8.6%
367Strabismus8.6%
368Tolosa-Hunt Syndrome8.6%
369Isaacs syndrome8.6%
370Arsenic Poisoning8.6%
371Myotonic Disorders8.6%
372Myasthenic Syndromes, Congenital8.6%
373Akathisia8.5%
374Restlessness8.5%
375Psychomotor Agitation8.5%
376Diabetic Neuropathies8.5%
377Facial Injuries8.5%
378Facial Neuralgia8.5%
379Diabetic Amyotrophy8.5%
380Diabetic Autonomic Neuropathy8.5%
381Sleep Talking8.5%
382Manganese Poisoning8.5%
383Sleep Disorders, Intrinsic8.5%
384Orthostatic intolerance8.5%
385Anosmia8.4%
386Ataxia8.4%
387Athetosis8.4%
388Catalepsy8.4%
389Dystonia8.4%
390Hemiplegia8.4%
391Locked-In Syndrome8.4%
392Meningeal Neoplasms8.4%
393Meningomyelocele8.4%
394Muscle Hypertonia8.4%
395Muscle hypotonia8.4%
396Myoclonus8.4%
397Myotonia8.4%
398Neuralgia8.4%
399Paraplegia8.4%
400Pseudobulbar Palsy8.4%
401Quadriplegia8.4%
402Spasm8.4%
403Spastic Paraplegia8.4%
404Status Epilepticus8.4%
405Taste Disorders8.4%
406Tremor8.4%
407Spina Bifida8.4%
408Monoplegia8.4%
409Hypokinesia8.4%
410Paraparesis8.4%
411Bradykinesia8.4%
412Waxy flexibility8.4%
413Action Tremor8.4%
414Resting Tremor8.4%
415Dysosmia8.4%
416Quadriparesis8.4%
417Mercury Poisoning, Nervous System8.4%
418Olfaction Disorders8.4%
419Myokymia8.4%
420Lead Poisoning, Nervous System8.4%
421Vestibular Neuronitis8.4%
422Somatosensory Disorders8.4%
423Neuropathic pain8.4%
424Hyperkinesia8.4%
425Intention tremor8.4%
426Optic Nerve Glioma8.4%
427Alcohol Withdrawal Seizures8.3%
428Voice Disorders8.1%
429Voice Disturbance8.1%
430Giant Cell Arteritis8%
431Temporal Arteritis8%
432Carotid Stenosis8%
433Intracranial Aneurysm8%
434Gait Apraxia8%
435Smith-Magenis syndrome8%
436Intracranial Arteriosclerosis7.9%
437Cerebral Atherosclerosis7.9%
438Subarachnoid Hemorrhage7.9%
439Cerebral Arteriosclerosis7.9%
440Cerebral Hemorrhage7.9%
441Dural Arteriovenous Fistula7.9%
442Cerebral Thrombosis7.9%
443Intracranial Embolism7.9%
444Intracranial Thrombosis7.9%
445Polyradiculopathy7.8%
446Brain Diseases, Metabolic, Inborn7.8%
447Hematoma, Subdural7.7%
448Hematoma, Epidural, Cranial7.7%
449Acromegaly7.3%
450Central Nervous System Infection7.3%
451Cerebral Amyloid Angiopathy7.2%
452Sinus Thrombosis, Intracranial7.2%
453Hand-Arm Vibration Syndrome7.1%
454Hematoma, Subdural, Intracranial7.1%
455Hematoma, Subdural, Chronic7.1%
456Hematoma, Subdural, Acute7.1%
457Vision Disorders7%
458Metamorphopsia7%
459Visual Impairment7%
460Classical Lissencephalies and Subcortical Band Heterotopias7%
461Fibromyalgia6.9%
462Optic Neuropathy, Ischemic6.9%
463Anterior Ischemic Optic Neuropathy6.9%
464Medial Tibial Stress Syndrome6.9%
465Facial Hemiatrophy6.8%
466Melkersson-Rosenthal Syndrome6.8%
467Mitochondrial Myopathies6.8%
468Cavernous Sinus Thrombosis6.8%
469Sagittal Sinus Thrombosis6.8%
470Thoracic Outlet Syndrome6.8%
471Anisocoria6.8%
472Confusion6.8%
473Facial paralysis6.8%
474Lethargy6.8%
475Memory Disorders6.8%
476Muscle Cramp6.8%
477Perceptual Disorders6.8%
478Psychomotor Disorders6.8%
479Tonic Pupil6.8%
480Eosinophilia-Myalgia Syndrome6.8%
481Anhedonia6.8%
482Disorientation6.8%
483Facial Paresis6.8%
484Memory Loss6.8%
485Hemisensory Neglect6.8%
486Dysacusis6.8%
487Sleep Bruxism6.8%
488Esotropia6.7%
489Exotropia6.7%
490Hypotension, Orthostatic6.7%
491Sleep Apnea Syndromes6.7%
492Polymyositis6.7%
493Post-Exercise Hypotension6.7%
494Anencephaly6.7%
495Meningocele6.7%
496Muscular Atrophy6.7%
497Respiratory Paralysis6.7%
498Encephalocele6.7%
499Reflex, Abnormal6.7%
500Hyporeflexia6.7%
501Hyperreflexia6.7%
502Disorders of Excessive Somnolence6.7%
503Sleep Initiation and Maintenance Disorders6.7%
504Night Terrors6.7%
505Somnambulism6.7%
506Tetany6.7%
507Trigeminal Nerve Disorder6.7%
508Transient Insomnia6.7%
509Sleep Paralysis6.7%
510Chronic Insomnia6.7%
511REM Sleep Behavior Disorder6.7%
512Hypersomnia6.7%
513Dermal Sinus6.6%
514Dysgeusia6.6%
515Formication6.6%
516Hyperalgesia6.6%
517Hyperesthesia6.6%
518Hypesthesia6.6%
519Language Disorders6.6%
520Numbness6.6%
521Paresthesia6.6%
522Paraparesis, Spastic6.6%
523Spina Bifida Cystica6.6%
524Trismus6.6%
525Wernicke Encephalopathy6.6%
526Spina Bifida Occulta6.6%
527Epilepsia Partialis Continua6.6%
528Hypogeusia6.6%
529Meningeal Carcinomatosis6.6%
530Brown-Sequard Syndrome6.6%
531Lissencephaly6.6%
532Polymicrogyria6.6%
533Pachygyria6.6%
534Schizencephaly6.6%
535Lockjaw6.6%
536Allodynia6.6%
537Lead Poisoning, Nervous System, Childhood6.6%
538Lead Poisoning, Nervous System, Adult6.6%
539Periventricular Nodular Heterotopia6.6%
540Ageusia6.6%
541AIDS Dementia Complex6.6%
542Carotid Artery Thrombosis6.6%
543Alexia6.5%
544Dyslexia6.5%
545Neurofibrosarcoma6.2%
546Scrapie6.1%
547Acoustic Neuroma6%
548Kernicterus5.9%
549Sleep Apnea, Obstructive5.8%
550Sleep Apnea, Central5.8%
551Narcolepsy5.8%
552Trigeminal Neuralgia5.8%
553Kleine-Levin Syndrome5.8%
554Agraphia5.8%
555Anomia5.8%
556Cluttering5.8%
557Language Development Disorders5.8%
558Speech Disorders5.8%
559Syncope5.8%
560Stupor5.8%
561Dysgraphia5.8%
562Presyncope5.8%
563Dyslalia5.8%
564Duane Retraction Syndrome5.7%
565Nelson Syndrome5.7%
566Consciousness Disorders5.7%
567Mental Retardation5.7%
568Muscle Weakness5.7%
569Depressed Level of Consciousness5.7%
570Mental deficiency5.7%
571Intellectual Disability5.7%
572Kearns-Sayre syndrome5.7%
573Mobius Syndrome5.7%
574Bell Palsy5.7%
575Catatonia5.6%
576Herpes Zoster Oticus5.6%
577Familial Periodic Paralysis5.6%
578Aphonia5.6%
579Sleep Deprivation5.6%
580Dysphonia5.6%
581Eye Injuries5.6%
582Muscular Dystrophy5.4%
583Congenital nystagmus5.4%
584Orbital Myositis5.4%
585Diplopia5.4%
586Muscle Rigidity5.4%
587Muscle Spasticity5.4%
588Scotoma5.4%
589Photophobia5.4%
590Cogwheel Rigidity5.4%
591Hemifacial Spasm5.4%
592Amaurosis5.4%
593Blindness5.4%
594Nuchal Rigidity5.4%
595Pyomyositis5.4%
596Cataplexy5.3%
597Aphasia5.3%
598Articulation Disorders5.3%
599Echolalia5.3%
600Stuttering5.3%
601Dysphasia5.3%
602Agnosia5.3%
603Apraxias5.3%
604Hallucinations5.3%
605Hemianopsia5.3%
606Hyperacusis5.3%
607Tinnitus5.3%
608Visual Agnosia5.3%
609Anosognosia5.3%
610Wernicke-Korsakoff Syndrome5.3%
611Phonophobia5.3%
612Hearing Loss5.3%
613Sarcopenia5.3%
614Prolactinoma5.2%
615Growth Hormone-Secreting Pituitary Adenoma5.2%
616Menkes Kinky Hair Syndrome5.2%
617Fabry Disease5.2%
618Dysarthria5.1%
619Galactosemias4.9%
620Urea Cycle Disorders, Inborn4.9%
621Tyrosinemias4.9%
622Myalgia4.8%
623Eye Burns4.7%
624Welander Distal Myopathy4.7%
625Amaurosis Fugax4.6%
626Blindness, Cortical4.6%
627Dyscalculia4.6%
628Rett Syndrome4.6%
629Deafness4.6%
630Hearing Loss, Sudden4.6%
631Gerstmann Syndrome4.6%
632Hearing Loss, Bilateral4.6%
633Hearing Loss, High-Frequency4.6%
634Hearing Loss, Mixed Conductive-Sensorineural4.6%
635Prosopagnosia4.6%
636Apraxia, Ideomotor4.6%
637Charles Bonnet Syndrome4.6%
638Hearing Loss, Unilateral4.6%
639Complete Hearing Loss4.6%
640Alien Hand Syndrome4.6%
641Deaf Mutism4.6%
642Amnesia4.5%
643Delirium4.5%
644Dissociative Amnesia4.5%
645Color blindness4.5%
646Global Amnesia4.5%
647Cri-du-Chat Syndrome4.5%
648Down Syndrome4.5%
649Trisomy 214.5%
650POEMS Syndrome4.4%
651Meningioma4.4%
652Williams Syndrome4.4%
653Microcephaly4.4%
654Macrocephaly4.4%
655Hypokalemic periodic paralysis4.4%
656Homocystinuria4.4%
657Porencephaly4.4%
658Leigh Disease4.4%
659Mutism4.3%
660Selective Mutism4.3%
661Aicardi's syndrome4.3%
662Hoarseness4.2%
663Alcohol Withdrawal Delirium4.2%
664Alexia, Pure4.1%
665Carbamoyl-Phosphate Synthase I Deficiency Disease4%
666Dermatomyositis4%
667Corneal Scar4%
668Muscular Dystrophy, Duchenne3.9%
669Retrograde amnesia3.8%
670Amnesia, Anterograde3.8%
671Prader-Willi Syndrome3.8%
672Phantom pain3.8%
673Phantom Limb Pain3.8%
674Holoprosencephaly3.7%
675Corneal Perforation3.6%
676Glycogen storage disease type II3.5%
677Zellweger Syndrome3.3%
678Fragile X Syndrome3.3%
679Gaucher Disease3.1%
680Rubinstein-Taybi Syndrome3%
681Tay-Sachs Disease2.9%
682Niemann-Pick Disease, Type C2.7%
683Mucopolysaccharidosis II2.3%
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