MetaADEDB 2.0 @ LMMD
Behcet Syndrome
(UMLS:C0004943)
Definition:
Rare chronic inflammatory disease involving the small blood vessels. It is of unknown etiology and characterized by mucocutaneous ulceration in the mouth and genital region and uveitis with hypopyon. The neuro-ocular form may cause blindness and death. SYNOVITIS; THROMBOPHLEBITIS; gastrointestinal ulcerations; RETINAL VASCULITIS; and OPTIC ATROPHY may occur as well.
UMLS ID:
C0004943
MeSH ID:
D001528
Classification 1:
Name:
Stomatognathic Diseases
MeSH Tree Number(s):
C07.465.075
Classification 2:
Name:
Eye Diseases
MeSH Tree Number(s):
C11.941.879.780.880.200
Classification 3:
Name:
Cardiovascular Diseases
MeSH Tree Number(s):
C14.907.940.100
Classification 4:
Name:
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
MeSH Tree Number(s):
C16.320.382.250
Classification 5:
Name:
Skin and Connective Tissue Diseases
MeSH Tree Number(s):
C17.800.827.368.250|C17.800.862.150
Synonym(s)
1.
Behcet Syndrome
2.
ADAMANTIADES-BEHCET SYNDROME
3.
Adamantiades-Behcet disease
4.
BEHCET RECURRENT DISEASE
5.
BEHCET SYNDROME
6.
BEHCET TRIPLE SYMPTOM COMPLEX
7.
Behcet Disease
8.
Behcet syndrome
9.
Behcet's
10.
Behcet's Syndrome
11.
Behcet's disease
12.
Behcet's disease, NOS
13.
Behcet's syndrome
Associated Drug(s)
Similar ADE(s)
NameSemantic Similarity
1Pyoderma Gangrenosum29.2%
2Polyarteritis Nodosa29%
3Malignant Atrophic Papulosis28.5%
4Epidermolysis Bullosa27.5%
5Xeroderma Pigmentosum26.8%
6Dermatitis, Atopic26.3%
7Takayasu Arteritis24.6%
8Porokeratosis24.4%
9Keratoderma, Palmoplantar24.4%
10Mucocutaneous Lymph Node Syndrome24.2%
11Pseudoxanthoma Elasticum23.9%
12Ichthyosis, X-Linked22.6%
13Ectodermal Dysplasia22.4%
14Aplasia Cutis Congenita22.4%
15Giant Cell Arteritis22.2%
16Temporal Arteritis22.2%
17Albinism21.8%
18Cutis Laxa20.9%
19Sjogren-Larsson Syndrome19.6%
20Lupus Erythematosus, Cutaneous18.6%
21Panniculitis18.6%
22Systemic Scleroderma18.6%
23Morphea18.6%
24Livedo Reticularis18.1%
25Acne Vulgaris17.5%
26Contact Dermatitis17.5%
27Eczema17.5%
28Erythema Multiforme17.5%
29Intertrigo17.5%
30Neurodermatitis17.5%
31Rhinophyma17.5%
32Perioral Dermatitis17.5%
33Acne17.5%
34Xeroderma17.4%
35Angioedemas, Hereditary17.2%
36Toxic Epidermal Necrolysis17.2%
37Stevens-Johnson Syndrome17.2%
38Papillon-Lefevre Disease17.2%
39Acrodermatitis17%
40Gianotti-Crosti Syndrome17%
41Hyperkeratosis, Epidermolytic16.7%
42Angioedema16.6%
43Aortitis16.6%
44Periphlebitis16.6%
45Phlebitis16.6%
46Thromboangiitis Obliterans16.6%
47Skin Abnormalities16.5%
48Dermatitis, Phototoxic16.5%
49Pityriasis Lichenoides et Varioliformis Acuta16.5%
50Pityriasis Lichenoides16.5%
51Phototoxicity16.5%
52Iridocyclitis15.9%
53Iritis15.9%
54Panniculitis, Lupus Erythematosus15.9%
55Breast Diseases15.8%
56Dermatitis15.8%
57Exanthema15.8%
58Facial Dermatoses15.8%
59Hair Diseases15.8%
60Hand Dermatoses15.8%
61keratoacanthoma15.8%
62Keratosis15.8%
63Nail Diseases15.8%
64Photosensitivity Disorders15.8%
65Prurigo15.8%
66Pyoderma15.8%
67Rosacea15.8%
68Sebaceous Gland Diseases15.8%
69Skin Diseases, Vesiculobullous15.8%
70Skin Ulcer15.8%
71Sweat Gland Diseases15.8%
72Skin Diseases, Papulosquamous15.8%
73Acneiform Eruptions15.8%
74Ocular Rosacea15.8%
75Subcorneal pustular dermatosis15.8%
76Erythematotelangiectatic Rosacea15.8%
77Papulopustular Rosacea15.8%
78Chronic Actinic Dermatitis15.8%
79Dermatitis Herpetiformis15.6%
80Facial Hemiatrophy15.6%
81Melkersson-Rosenthal Syndrome15.6%
82Necrobiosis Lipoidica Diabeticorum15.6%
83Sebaceous Gland Neoplasms15.5%
84Erythema Induratum15.4%
85Urticaria15.4%
86Porphyrias, Hepatic15.1%
87Lichen Planus, Oral15%
88Foot Ulcer14.9%
89Dermatitis, Photoallergic14.8%
90Parotid Neoplasms14.8%
91Shwartzman Phenomenon14.7%
92Dermatomyositis14.7%
93Nail-Patella Syndrome14.5%
94Foot Diseases14.2%
95Bell Palsy14.1%
96Skin Diseases, Infectious14%
97Skin Neoplasms14%
98Pigmentation Disorders14%
99Lipomatosis13.8%
100Pruritus13.8%
101Erythema13.8%
102Necrolytic Migratory Erythema13.8%
103Cutaneous Fistula13.8%
104Nephrogenic Fibrosing Dermopathy13.8%
105Nephrogenic Systemic Fibrosis13.8%
106Thrombophlebitis13.7%
107Retinal Vasculitis13.6%
108Mouth Abnormalities13.5%
109Arteritis13.3%
110Familial Mediterranean Fever13.3%
111Systemic Vasculitis13.3%
112Salivary Gland Fistula13.3%
113Salivary Gland Neoplasms13.3%
114Tongue Neoplasms13.3%
115Urticaria Pigmentosa13.2%
116Gingival Recession12.4%
117Parotitis12.4%
118Dermatitis, Irritant12.4%
119Gingival Atrophy12.4%
120Acne Conglobata12.4%
121Mastocytosis12.2%
122Vasculitis, Central Nervous System12.1%
123Gingival Hemorrhage12.1%
124Erythema Infectiosum12%
125Exanthema Subitum12%
126Erythema Nodosum11.9%
127Lupus Erythematosus, Discoid11.6%
128Vasculitis, Leukocytoclastic, Cutaneous11.6%
129Scleroderma, Limited11.6%
130Menkes Kinky Hair Syndrome11.6%
131Burning Mouth Syndrome11.5%
132Lip Diseases11.5%
133Microglossia11.5%
134Oral Submucous Fibrosis11.5%
135Periodontal Diseases11.5%
136Salivary Gland Diseases11.5%
137Stomatitis11.5%
138Tongue Diseases11.5%
139Oral Ulcer11.5%
140Marfan Syndrome11.4%
141Dermatitis, Occupational11.3%
142CREST Syndrome11.2%
143Retinal Vein Occlusion11.2%
144Varicose Ulcer11.2%
145Dermatitis, Allergic Contact11%
146Lemierre Syndrome11%
147Tooth Loss10.9%
148Tinea Capitis10.8%
149Onychomycosis10.8%
150Ecthyma10.8%
151Pemphigoid, Benign Mucous Membrane10.7%
152Uveitis, Posterior10.6%
153Variegate Porphyria10.5%
154Acute intermittent porphyria10.5%
155Porphyria Cutanea Tarda10.5%
156Aicardi's syndrome10.5%
157Hereditary Angioedema Type III10.4%
158Hereditary Angioedema Types I and II10.4%
159Facial Nerve Diseases10.1%
160Myocardial Ischemia10.1%
161Granulomatosis, Orofacial10.1%
162Oral candidiasis10.1%
163Mouth Neoplasms10.1%
164Oral Fistula10.1%
165Aortic Aneurysm10%
166Leriche Syndrome10%
167Anhidrosis10%
168Cholesteatoma10%
169Pressure Ulcer10%
170Folliculitis10%
171Foot Dermatoses10%
172Gynecomastia10%
173Hypertrichosis10%
174Hypohidrosis10%
175Hypotrichosis10%
176Leg Ulcer10%
177Miliaria10%
178Parakeratosis10%
179Parapsoriasis10%
180Pityriasis10%
181Psoriasis10%
182Sweet Syndrome10%
183Hidradenitis10%
184Onycholysis10%
185Miliaria Rubra10%
186Hyperpigmentation10%
187Lichenoid Eruptions10%
188Chloracne10%
189Aniridia10%
190Macrostomia9.9%
191Microstomia9.9%
192Endarteritis9.9%
193Herpes Labialis9.9%
194Diaper Rash9.9%
195Myocardial Reperfusion Injury9.7%
196Granuloma Annulare9.6%
197Pars Planitis9.6%
198Mobius Syndrome9.4%
199Cleft Palate9.3%
200Choroiditis9.3%
201Connective Tissue Diseases9.3%
202Osteogenesis Imperfecta9.3%
203CHARGE Syndrome9.1%
204Retinal Dysplasia9.1%
205Erythema Chronicum Migrans9.1%
206Hidradenitis Suppurativa9%
207Aortic Rupture9%
208Fragile X Syndrome8.9%
209Facial paralysis8.9%
210Facial Paresis8.9%
211Arteriovenous fistula8.9%
212Hemifacial Spasm8.9%
213Mucopolysaccharidosis II8.8%
214Coronary Aneurysm8.8%
215Acantholysis8.8%
216Breast Cyst8.8%
217Actinic keratosis8.8%
218Pemphigus8.8%
219Piedra8.8%
220Sunburn8.8%
221Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis8.8%
222Argyria8.7%
223Hirsutism8.7%
224Lactation Disorder8.7%
225Mastitis8.7%
226Adiposis Dolorosa8.7%
227Postphlebitic Syndrome8.7%
228Pruritus Vulvae8.7%
229Mastocytoma8.7%
230Pruritus Ani8.7%
231Aneurysm8.6%
232Angiomatosis8.6%
233Aortic Diseases8.6%
234Arterial Occlusive Diseases8.6%
235Hyperemia8.6%
236Hypotension8.6%
237Superior Vena Cava Syndrome8.6%
238Telangiectasis8.6%
239Venous Insufficiency8.6%
240Peripheral Vascular Diseases8.6%
241Embolism and Thrombosis8.6%
242Angiodysplasia8.6%
243Capillary Leak Syndrome8.6%
244Prehypertension8.6%
245Cheilitis8.6%
246Drooling8.6%
247Gingival Diseases8.6%
248Glossitis8.6%
249Macroglossia8.6%
250Periodontitis8.6%
251Sialadenitis8.6%
252Sialometaplasia, Necrotizing8.6%
253Sialorrhea8.6%
254Aphthous Stomatitis8.6%
255Xerostomia8.6%
256Glossoptosis8.6%
257Peri-Implantitis8.6%
258Moyamoya Disease8.5%
259Optic Neuropathy, Ischemic8.4%
260Anterior Ischemic Optic Neuropathy8.4%
261Alstrom Syndrome8.4%
262Carotid Artery Thrombosis8.3%
263Kartagener Syndrome8.3%
264Cystic Fibrosis8.2%
265Scimitar Syndrome8.2%
266Tinea Pedis8%
267Anemia, Sickle Cell7.9%
268Thalassemia7.9%
269Muscular Dystrophy, Duchenne7.9%
270Diabetic Foot7.9%
271Dermatomycoses7.8%
272Skin Diseases, Bacterial7.8%
273Rheumatoid Vasculitis7.8%
274Drug Eruptions7.8%
275Lipodystrophy7.8%
276Cockayne Syndrome7.7%
277Neoplastic Syndromes, Hereditary7.7%
278Vascular System Injuries7.7%
279Blue Toe Syndrome7.7%
280Ataxia Telangiectasia7.7%
281Giant Cell Epulis7.7%
282Intracranial Embolism and Thrombosis7.7%
283Carotid Stenosis7.7%
284Intracranial Aneurysm7.7%
285Coronary Thrombosis7.7%
286Coronary Artery Disease7.7%
287Compartment syndromes7.6%
288Hepatic Veno-Occlusive Disease7.6%
289Peliosis Hepatis7.6%
290Varicocele7.6%
291Radicular Cyst7.6%
292Mycetoma7.6%
293Cerebrovascular Disorders7.5%
294Diabetic Angiopathies7.5%
295Multiple Epiphyseal Dysplasia7.5%
296Osteochondrodysplasias7.5%
297Pelger-Huet Anomaly7.5%
298Reperfusion Injury7.5%
299Splenic Infarction7.5%
300Werner Syndrome7.5%
301Cerebrovascular Insufficiency7.5%
302Vascular Neoplasms7.5%
303Myasthenic Syndromes, Congenital7.5%
304Spinal Cord Vascular Diseases7.5%
305Vasoplegia7.5%
306Hemorrhoids7.5%
307Thoracic Outlet Syndrome7.5%
308Facial Neuralgia7.5%
309Peutz-Jeghers Syndrome7.5%
310Dental Fistula7.5%
311Oroantral Fistula7.5%
312Aortic Aneurysm, Abdominal7.4%
313Aortic Aneurysm, Thoracic7.4%
314Beckwith-Wiedemann Syndrome7.4%
315Wolf-Hirschhorn Syndrome7.4%
316Fabry Disease7.4%
317Skin Diseases, Vascular7.2%
318Lupus Vasculitis, Central Nervous System7.1%
319Gingivitis7.1%
320Glossitis, Benign Migratory7.1%
321Lichen Planus7.1%
322Melanosis7.1%
323Chloasma7.1%
324Pericoronitis7.1%
325Aggressive Periodontitis7.1%
326Pityriasis Rosea7.1%
327Pityriasis Rubra Pilaris7.1%
328Vitiligo7.1%
329Lichen Nitidus7.1%
330Gingival Overgrowth7.1%
331Duane Retraction Syndrome7.1%
332May-Thurner Syndrome7%
333Homocystinuria6.9%
334Noonan Syndrome6.9%
335Retinal Artery Occlusion6.9%
336Hypertensive Retinopathy6.9%
337Cardiovascular Abnormalities6.9%
338Dwarfism6.9%
339Hand-Arm Vibration Syndrome6.9%
340Vesicular Stomatitis6.8%
341Uveal Neoplasms6.8%
342Mesenteric vascular insufficiency6.8%
343Smith-Magenis syndrome6.7%
344Muscular Dystrophy6.7%
345Retinitis Pigmentosa6.7%
346Pigmentary retinopathy6.7%
347Chorioretinitis6.7%
348Coronary heart disease6.7%
349Myocardial Infarction6.7%
350Acute Coronary Syndrome6.7%
351Colitis, Ischemic6.6%
352Cri-du-Chat Syndrome6.6%
353Down Syndrome6.6%
354Trisomy 216.6%
355Holoprosencephaly6.6%
356Wiskott-Aldrich Syndrome6.6%
357Palatal Neoplasms6.6%
358Intracranial Arteriosclerosis6.6%
359Cerebral Atherosclerosis6.6%
360Rett Syndrome6.6%
361Cerebral Arteriosclerosis6.6%
362Uveomeningoencephalitic Syndrome6.5%
363Choroid Diseases6.5%
364Iris Diseases6.5%
365Granulomatosis with polyangiitis6.4%
366Adrenoleukodystrophy6.4%
367Gingival Hyperplasia6.4%
368Gingival Hypertrophy6.4%
369Alopecia6.3%
370Sweating, Gustatory6.3%
371Androgenetic Alopecia6.3%
372Auriculotemporal Syndrome6.3%
373Eye Abnormalities6.2%
374Alveolar Bone Loss6.2%
375Lice Infestations6.2%
376Breast Neoplasms, Male6.2%
377Triple Negative Breast Neoplasms6.2%
378Sicca Syndrome6.2%
379Sjogren's Syndrome6.2%
380Trigeminal Nerve Disorder6.2%
381Galactorrhea6.2%
382Diabetic Retinopathy6.1%
383Williams Syndrome6.1%
384Myotonic Dystrophy6.1%
385Autoimmune Lymphoproliferative Syndrome6.1%
386Smith-Lemli-Opitz Syndrome6%
387Prader-Willi Syndrome6%
388Cerebral Thrombosis6%
389Intracranial Embolism6%
390Intracranial Thrombosis6%
391Herpes Zoster Oticus6%
392Subarachnoid Hemorrhage, Traumatic6%
393Carotid Artery, Internal, Dissection6%
394Leukoplakia, Oral6%
395Kounis Syndrome6%
396Tuberous Sclerosis6%
397Mucopolysaccharidosis III5.9%
398Sickle Cell Trait5.9%
399Brain Infarction5.9%
400Angina Pectoris5.9%
401Tooth Diseases5.9%
402Rubinstein-Taybi Syndrome5.8%
403Neuronal Ceroid-Lipofuscinoses5.8%
404Hepatolenticular Degeneration5.8%
405Refsum Disease5.8%
406Aneurysm, Dissecting5.7%
407Arteriosclerosis5.7%
408Embolism5.7%
409Erythromelalgia5.7%
410Fibromuscular Dysplasia5.7%
411Malignant Hypertension5.7%
412Raynaud Disease5.7%
413Thromboembolism5.7%
414Thrombosis5.7%
415Essential Hypertension5.7%
416Aneurysm, Ruptured5.7%
417Iliac Aneurysm5.7%
418Pulmonary artery stenosis5.7%
419White Coat Hypertension5.7%
420Embolus5.7%
421Acanthosis Nigricans5.7%
422Alopecia Areata5.7%
423Lentigo5.7%
424Infarction, Middle Cerebral Artery5.7%
425Infarction, Anterior Cerebral Artery5.7%
426Infarction, Posterior Cerebral Artery5.7%
427Kallmann Syndrome5.6%
428Embolism, Amniotic Fluid5.6%
429Larva Migrans5.6%
430Leishmaniasis5.6%
431Molluscum Contagiosum5.6%
432Optic Atrophy, Hereditary, Leber5.6%
433Mumps5.5%
434Trigeminal Neuralgia5.5%
435Onchocerciasis5.5%
436Dental Enamel Hypoplasia5.5%
437Hypodontia5.5%
438Chromoblastomycosis5.5%
439Dermatophytosis5.5%
440Sporotrichosis5.5%
441Tinea5.5%
442Tinea Versicolor5.5%
443Trichophytosis5.5%
444Hyalohyphomycosis5.5%
445Retrognathia5.5%
446Acute Generalized Exanthematous Pustulosis5.5%
447Jaw Abnormalities5.4%
448Facial Nerve Injuries5.4%
449Vertebral Artery Dissection5.4%
450Amyloid Neuropathies, Familial5.3%
451Leukomalacia, Periventricular5.3%
452Polycystic Kidney Diseases5.3%
453Collagen Diseases5.3%
454Mixed Connective Tissue Disease5.3%
455Mucinoses5.3%
456Jaw Diseases5.3%
457Pharyngeal Diseases5.3%
458Temporomandibular Joint Disorders5.2%
459Glycogen storage disease type II5.2%
460Primary Ciliary Dyskinesia5.2%
461Sinus Thrombosis, Intracranial5.2%
462Prognathism5.1%
463Warts5%
464Iridocorneal endothelial syndrome5%
465Maxillofacial Abnormalities5%
466Amino Acid Metabolism, Inborn Errors5%
467Anterior Compartment Syndrome5%
468Carbohydrate Metabolism, Inborn Errors5%
469Metal Metabolism, Inborn Errors5%
470Progeria5%
471Lysosomal Storage Diseases5%
472Gastric Antral Vascular Ectasia5%
473Cytochrome-c Oxidase Deficiency5%
474Peroxisomal Disorders5%
475Abdominal Compartment Syndrome5%
476Behcet Syndrome5%
477Acute Chest Syndrome5%
478Dextrocardia5%
479Tricuspid Atresia5%
480Arrhythmogenic Right Ventricular Dysplasia5%
481Ulcerative stomatitis5%
482Carotid Artery Diseases5%
483Brain Ischemia5%
484Hypotension, Orthostatic5%
485Cerebrovascular accident5%
486Vasospasm, Intracranial5%
487Spinal Cord Ischemia5%
488Intracranial Arterial Diseases5%
489Primary Graft Dysfunction5%
490Post-Exercise Hypotension5%
491Candidiasis, Chronic Mucocutaneous5%
492Cutaneous Candidiasis5%
493Coronary Occlusion4.9%
494Microvascular Angina4.9%
495Coronary Stenosis4.9%
496ST segment elevation myocardial infarction4.9%
497Erysipelas4.9%
498Serum Sickness4.9%
499Staphylococcal Skin Infections4.9%
500Erythrasma4.9%
501Carcinoma, Lobular4.9%
502Carotid Artery Injuries4.9%
503Arthritis, Psoriatic4.9%
504Galactosemias4.9%
505Urea Cycle Disorders, Inborn4.9%
506Tyrosinemias4.9%
507Heart Diseases4.9%
508Deformity4.9%
509Cerebral Infarction4.9%
510Brain Stem Infarctions4.9%
511Blepharophimosis4.9%
512Orbital Cellulitis4.8%
513Cavernous Sinus Thrombosis4.8%
514Sagittal Sinus Thrombosis4.8%
515Cartilage Diseases4.7%
516Rheumatism4.7%
517Chondromalacia4.7%
518Lupus Erythematosus, Systemic4.7%
519Overlap syndrome4.7%
520Basal Cell Nevus Syndrome4.6%
521Canavan Disease4.6%
522Alexander Disease4.6%
523Zellweger Syndrome4.5%
524Hyperphosphaturia4.5%
525Mesenteric Vascular Occlusion4.5%
526Basal Ganglia Hemorrhage4.5%
527Choroid Hemorrhage4.5%
528Sturge-Weber Syndrome4.5%
529Turner Syndrome4.4%
530Chronic granulomatous disease4.4%
531Renal hypertension4.4%
532Renal Artery Obstruction4.4%
533Renal Artery Stenosis4.4%
534Hemangioma, Cavernous4.4%
535Shock, Cardiogenic4.4%
536Basal Ganglia Cerebrovascular Disease4.4%
537Leishmaniasis, Cutaneous4.4%
538Vascular Headaches4.4%
539Welander Distal Myopathy4.4%
540Eczema Herpeticum4.4%
541Scurvy4.4%
542Lateral Medullary Syndrome4.4%
543Angina, Unstable4.4%
544Fusariosis4.4%
545Gaucher Disease4.3%
546Fetal Diseases4.3%
547Pregnancy Complications, Cardiovascular4.3%
548Micrognathism4.3%
549Pierre Robin Syndrome4.3%
550Arteriosclerosis Obliterans4.3%
551Atherosclerosis4.3%
552Air Embolism4.3%
553Venous Thrombosis4.3%
554Deep Vein Thrombosis4.3%
555Venous Thromboembolism4.3%
556Asthenopia4.2%
557Conjunctival Diseases4.2%
558Corneal Diseases4.2%
559Eyelid Diseases4.2%
560Lacrimal Apparatus Diseases4.2%
561Lens Diseases4.2%
562Ocular Hypertension4.2%
563Ocular Hypotension4.2%
564Retinal Diseases4.2%
565Scleral Diseases4.2%
566Vitreous Detachment4.2%
567Posterior Vitreous Detachment4.2%
568Leigh Disease4.1%
569Blastomycosis4.1%
570Coronary Restenosis4.1%
571HIV-Associated Lipodystrophy Syndrome4.1%
572Classical Lissencephalies and Subcortical Band Heterotopias4.1%
573Dupuytren Contracture4.1%
574Aortic coarctation4.1%
575Cor Triatriatum4.1%
576Coronary Vessel Anomalies4.1%
577Patent ductus arteriosus4.1%
578Ebstein Anomaly4.1%
579Heart Septal Defects4.1%
580Tetralogy of Fallot4.1%
581Transposition of Great Vessels4.1%
582Hypoplastic Left Heart Syndrome4.1%
583Ischemic contracture4%
584Myotonia Congenita4%
585Thrombasthenia4%
586Antithrombin III Deficiency4%
587Protein C Deficiency4%
588Brain Diseases, Metabolic, Inborn4%
589Tay-Sachs Disease4%
590Afibrinogenemia4%
591Cryoglobulinemia4%
592Dystonia Musculorum Deformans4%
593Factor VII Deficiency4%
594Factor X Deficiency4%
595Factor XII Deficiency4%
596Hemophilia A4%
597Activated Protein C Resistance4%
598Factor II deficiency4%
599Factor VIII Deficiency4%
600Factor V deficiency4%
601Factor XI Deficiency4%
602Hypoprothrombinemias4%
603Epidermodysplasia Verruciformis4%
604Fanconi Anemia4%
605Lafora Disease3.9%
606Unverricht-Lundborg Syndrome3.9%
607Anemia, Diamond-Blackfan3.9%
608Polycystic Kidney, Autosomal Dominant3.9%
609Staphylococcal Scalded Skin Syndrome3.9%
610MELAS Syndrome3.9%
611Rhinoscleroma3.9%
612Putaminal Hemorrhage3.8%
613Bruxism3.8%
614Dental Leakage3.8%
615Hypercementosis3.8%
616Malocclusion3.8%
617Tooth Crowding3.8%
618Tooth Discoloration3.8%
619Tooth Demineralization3.8%
620Tooth Ankylosis3.8%
621Niemann-Pick Disease, Type C3.8%
622Retinal Degeneration3.8%
623Dementia, Vascular3.8%
624Intermittent Claudication3.8%
625Pulmonary Embolism3.8%
626Carbamoyl-Phosphate Synthase I Deficiency Disease3.8%
627No-Reflow Phenomenon3.7%
628Alkaptonuria3.7%
629Glycogen Storage Disease3.7%
630Hypophosphatasia3.7%
631Propionic acidemia3.7%
632Dihydropyrimidine Dehydrogenase Deficiency3.7%
633Cystinosis3.7%
634Cerebral Arterial Diseases3.7%
635Vertebrobasilar Insufficiency3.7%
636Anterior Spinal Artery Syndrome3.7%
637Basilar Artery Stenosis3.7%
638Vertebral Artery Stenosis3.7%
639Intracranial Hemorrhage, Hypertensive3.7%
640Transient Cerebral Ischemia3.7%
641Meconium Aspiration Syndrome3.7%
642Multiple Endocrine Neoplasia3.7%
643Cellulitis3.7%
644Dural Arteriovenous Fistula3.7%
645Eye Infection3.7%
646Eye Manifestations3.7%
647Eye Neoplasms3.7%
648Optic Neuropathy3.7%
649Long QT Syndrome3.6%
650Congenital Hypothyroidism3.6%
651Angina Pectoris, Variant3.6%
652Nasopharyngitis3.6%
653Condylomata Acuminata3.6%
654Furunculosis3.6%
655Shy-Drager Syndrome3.6%
656furuncle3.6%
657Purpura, Hyperglobulinemic3.6%
658Charcot-Marie-Tooth Disease3.6%
659Antley-Bixler Syndrome Phenotype3.6%
660Anophthalmos3.6%
661Microphthalmos3.6%
662Retinopathy of Prematurity3.6%
663Exfoliation Syndrome3.6%
664Impetigo3.6%
665Temporomandibular Joint Dysfunction Syndrome3.4%
666Tooth Injuries3.4%
667carbuncle3.4%
668Laryngomalacia3.4%
669Panophthalmitis3.4%
670Maxillary Diseases3.4%
671Tooth Resorption3.4%
672Bacterial Endocarditis3.4%
673Pectus carinatum3.4%
674Eyelid Neoplasms3.4%
675Retinal Hemorrhage3.4%
676Toothache3.3%
677Aortic Valve Stenosis3.3%
678Cardiomyopathy, Dilated3.3%
679Pulmonary Valve Stenosis3.3%
680Scleromyxedema3.3%
681Nasopharyngeal Neoplasms3.3%
682Waldenstrom Macroglobulinemia3.3%
683Multiple Myeloma3.3%
684Hypolipoproteinemias3.3%
685Wolff-Parkinson-White Syndrome3.3%
686Hyperlipidemia, Familial Combined3.3%
687Hypertension, Renovascular3.3%
688Subarachnoid Hemorrhage3.3%
689Hypoxia-Ischemia, Brain3.3%
690Cerebral Hemorrhage3.3%
691Hyperlipoproteinemia Type III3.3%
692Ocular Motility Disorders3.3%
693Cyclophoria3.3%
694Pupil Disorders3.2%
695Eye Hemorrhage3.2%
696Vision Disorders3.2%
697Metamorphopsia3.2%
698Visual Impairment3.2%
699Eye Injuries3.2%
700Congenital nystagmus3.2%
701Klinefelter Syndrome3.1%
702Hepatic Vein Thrombosis3.1%
703Budd-Chiari Syndrome3.1%
704Choroidal Neovascularization3.1%
705Aortopulmonary Septal Defect3.1%
706Double Outlet Right Ventricle3.1%
707Endocardial Cushion Defects3.1%
708Myocardial bridging3.1%
709Aorticopulmonary Septal Defect3.1%
710Pulmonary Infarction3.1%
711Glycogen Storage Disease Type I3.1%
712Glycogen Storage Disease Type V3.1%
713Subclavian Steal Syndrome3.1%
714Huntington Disease3%
715Pharyngitis3%
716Corneal Scar3%
717Familial Periodic Paralysis3%
718Pituitary Apoplexy3%
719Lactose Intolerance3%
720Hyperhomocysteinemia3%
721Heart Block3%
722Tachycardia3%
723Tachyarrhythmia3%
724Renal Aminoacidurias3%
725Fanconi Syndrome3%
726Pseudohypoaldosteronism3%
727Liddle Syndrome3%
728Hyperlipoproteinemia Type IV2.9%
729Hyperlipoproteinemia Type V2.9%
730Mesenteric Panniculitis2.9%
731Panniculitis, Peritoneal2.9%
732Tietze's Syndrome2.9%
733Xerophthalmia2.9%
734Low Tension Glaucoma2.9%
735Myxoid cyst2.9%
736Hydrops Fetalis2.9%
737Myxedema2.9%
738Ectopia Cordis2.9%
739Single umbilical artery2.9%
740Abdominal Cramps2.9%
741Abnormalities, Drug-Induced2.9%
742Amniotic Band Syndrome2.9%
743Asphyxia Neonatorum2.9%
744Cardiac Tamponade2.9%
745Endocarditis2.9%
746Cardiac Arrest2.9%
747Heart failure2.9%
748Infant, Premature, Diseases2.9%
749Pericardial effusion2.9%
750Pericarditis2.9%
751Pneumopericardium2.9%
752Cor pulmonale2.9%
753Situs Inversus2.9%
754Ventricular Outflow Obstruction2.9%
755Ventricular Dysfunction2.9%
756Infantile Colic2.9%
757Cardiomyopathies2.9%
758Pleuropericarditis2.9%
759Dental caries2.9%
760Dental Plaque2.9%
761Dental Pulp Calcification2.9%
762Pulpitis2.9%
763Tooth Erosion2.9%
764Nephroblastoma2.8%
765Romano-Ward Syndrome2.8%
766Cerebral Amyloid Angiopathy2.7%
767Hypoalphalipoproteinemias2.7%
768Gout2.7%
769Pharyngeal Neoplasms2.7%
770Multiple Endocrine Neoplasia Type 12.7%
771Pseudohypoparathyroidism2.7%
772Friedreich Ataxia2.7%
773Hypertrophic Cardiomyopathy2.7%
774Hypertrophic obstructive cardiomyopathy2.7%
775Sick Sinus Syndrome2.7%
776Familial Hypophosphatemic Rickets2.7%
777Renal tubular acidosis2.7%
778Bronchomalacia2.6%
779Tracheomalacia2.6%
780Truncus Arteriosus, Persistent2.6%
781Osteochondritis2.6%
782Polymyalgia Rheumatica2.6%
783Adenomatous Polyposis Coli2.6%
784Corneal Ulcer2.6%
785Anencephaly2.6%
786Keloid2.6%
787Cardiac Output, High2.5%
788Myocardial Stunning2.5%
789Lymphatic Abnormalities2.5%
790Low Cardiac Output Syndrome2.5%
791Congenital Microtia2.5%
792Anemia, Neonatal2.5%
793Cardiomegaly2.5%
794Persistent Fetal Circulation Syndrome2.5%
795Postpericardiotomy Syndrome2.5%
796Tooth Avulsion2.5%
797Cardiac Hypertrophy2.5%
798Nasopharyngeal carcinoma2.5%
799Congenital diaphragmatic hernia2.5%
800Umbilical hernia2.5%
801Rheumatic Heart Disease2.5%
802Dental Pulp Necrosis2.5%
803Supravalvular aortic stenosis2.5%
804Lown-Ganong-Levine Syndrome2.5%
805Ophthalmia Neonatorum2.5%
806Hypokalemic periodic paralysis2.5%
807Cystinuria2.4%
808Retinoblastoma2.4%
809Rheumatoid Arthritis2.4%
810Juvenile arthritis2.4%
811Hordeolum2.3%
812Color blindness2.3%
813Lupus Nephritis2.3%
814Urogenital Abnormalities2.3%
815Neonatal Abstinence Syndrome2.3%
816Glycosuria, Renal2.3%
817Arthritis, Gouty2.2%
818Fetal Growth Retardation2.2%
819Fetal Hypoxia2.2%
820Fetal Alcohol Spectrum Disorders2.2%
821Tonsillitis2.2%
822Sleep Bruxism2.2%
823Toxoplasmosis, Congenital2.2%
824Syphilis, Congenital2.2%
825Adams-Stokes Syndrome2.2%
826Atrioventricular Block2.2%
827Bundle-Branch Block2.2%
828Atrial Premature Complexes2.2%
829Sinoatrial Block2.2%
830Tachycardia, Paroxysmal2.2%
831Supraventricular tachycardia2.2%
832Tachycardia, Ventricular2.2%
833Tachycardia, Reciprocating2.2%
834Angioid Streaks2.2%
835Anisometropia2.2%
836Aphakia2.2%
837Astigmatism2.2%
838Blepharitis2.2%
839Blepharoptosis2.2%
840Blepharospasm2.2%
841Conjunctivitis2.2%
842Corneal edema2.2%
843Corneal Opacity2.2%
844Dacryocystitis2.2%
845Dry Eye Syndromes2.2%
846Ectropion2.2%
847Enophthalmos2.2%
848Entropion2.2%
849Episcleritis2.2%
850Exophthalmos2.2%
851Glaucoma2.2%
852Keratitis2.2%
853Keratoconus2.2%
854Lacrimal Duct Obstruction2.2%
855Lens dislocation2.2%
856Lens Subluxation2.2%
857Mydriasis2.2%
858Myopia2.2%
859Presbyopia2.2%
860Pterygium2.2%
861Retinal Detachment2.2%
862Retinitis2.2%
863Scleritis2.2%
864Corneal Neovascularization2.2%
865Orbital Pseudotumor2.2%
866Cataract2.2%
867Pinguecula2.2%
868Trichiasis2.2%
869Subacute Bacterial Endocarditis2.1%
870Keratoconjunctivitis2.1%
871Denys-Drash Syndrome2.1%
872Trachoma2.1%
873Hematoma, Subdural2%
874Hematoma, Epidural, Cranial2%
875Acrocephalosyndactylia2%
876Keratoconjunctivitis Sicca2%
877Congenital Hyperinsulinism2%
878Chorioamnionitis2%
879Retropharyngeal Abscess2%
880Hypopharyngeal Neoplasms2%
881Hypopharyngeal Cancer2%
882Carcinoid Heart Disease2%
883Aortic Valve Insufficiency1.9%
884Restrictive cardiomyopathy1.9%
885Endocardial Fibroelastosis1.9%
886Heart Rupture, Post-Infarction1.9%
887Mitral Valve Insufficiency1.9%
888Mitral Valve Stenosis1.9%
889Myocarditis1.9%
890Pericarditis, Constrictive1.9%
891Prune Belly Syndrome1.9%
892Pulmonary Valve Insufficiency1.9%
893Tricuspid Valve Insufficiency1.9%
894Tricuspid Valve Stenosis1.9%
895Twins, Conjoined1.9%
896Ventricular Dysfunction, Left1.9%
897Right Ventricular Dysfunction1.9%
898Endomyocardial Fibrosis1.9%
899Carditis1.9%
900Heart Failure, Systolic1.9%
901Heart Failure, Diastolic1.9%
902Waardenburg Syndrome1.9%
903Endophthalmitis1.9%
904Optic Atrophy1.9%
905Optic Neuritis1.9%
906Papilledema1.9%
907Strabismus1.9%
908Tolosa-Hunt Syndrome1.9%
909Retrobulbar Hemorrhage1.9%
910Corneal Endothelial Cell Loss1.9%
911Brain Hemorrhage, Traumatic1.9%
912Hyphema1.9%
913Retinal Neovascularization1.9%
914Vitreous Hemorrhage1.9%
915Rheumatoid Nodule1.8%
916Hematoma, Subdural, Intracranial1.8%
917Hematoma, Subdural, Chronic1.8%
918Hematoma, Subdural, Acute1.8%
919Tachycardia, Atrioventricular Nodal Reentry1.8%
920Tachycardia, Ectopic Atrial1.8%
921Tachycardia, Ectopic Junctional1.8%
922Sinus Tachycardia1.8%
923Torsades de Pointes1.8%
924Accelerated Idioventricular Rhythm1.8%
925Abnormalities, Radiation-Induced1.8%
926Microcephaly1.8%
927Macrocephaly1.8%
928Craniosynostosis1.8%
929Syndactyly1.8%
930Brachycephaly1.8%
931Anus, Imperforate1.7%
932Hydranencephaly1.7%
933Neural Tube Defects1.7%
934Paralysis, Obstetric1.7%
935Tethered Cord Syndrome1.7%
936Iniencephaly1.7%
937Craniorachischisis1.7%
938Limb Deformities, Congenital1.7%
939Exencephaly1.7%
940Septo-Optic Dysplasia1.7%
941Craniofacial Abnormalities1.7%
942Cortical Dysplasia1.7%
943Malformations of Cortical Development1.7%
944Anorectal Malformations1.7%
945Acanthamoeba Keratitis1.7%
946Anisocoria1.7%
947Tonic Pupil1.7%
948Eye pain1.7%
949Orbital Myositis1.7%
950Keratitis, Herpetic1.7%
951Cytomegalovirus Retinitis1.7%
952Sinus Arrhythmia1.7%
953Atrial Fibrillation1.7%
954Atrial Flutter1.7%
955Bloom Syndrome1.7%
956Edema, Cardiac1.7%
957Ventricular Fibrillation1.7%
958Ventricular Flutter1.7%
959Parasystole1.7%
960Paroxysmal atrial fibrillation1.7%
961Bradycardia1.7%
962Diabetic Cardiomyopathies1.7%
963Diplopia1.7%
964Scotoma1.7%
965Photophobia1.7%
966Amaurosis1.7%
967Blindness1.7%
968Bacterial conjunctivitis1.7%
969Bronchopulmonary Dysplasia1.7%
970Cardiomyopathy, Alcoholic1.7%
971Sudden Cardiac Death1.7%
972Left Ventricular Hypertrophy1.7%
973Right Ventricular Hypertrophy1.7%
974Chagas Cardiomyopathy1.7%
975Felty Syndrome1.7%
976Corneal Perforation1.6%
977Peritonsillar Abscess1.6%
978Mandibulofacial Dysostosis1.6%
979Tonsillar Neoplasms1.6%
980Porencephaly1.6%
981Ophthalmoplegia1.5%
982External Ophthalmoplegia1.5%
983Laryngostenosis1.5%
984Respiratory Distress Syndrome, Newborn1.5%
985Amblyopia1.5%
986Esophageal Atresia1.5%
987Intestinal Atresia1.5%
988Horseshoe Kidney1.5%
989Pectus excavatum1.5%
990Klippel-Feil Syndrome1.5%
991Gastroschisis1.5%
992Synostosis1.5%
993Poland Syndrome1.5%
994Lymphangiectasis, Intestinal1.5%
995Dyspnea, Paroxysmal1.5%
996Aortic Valve Prolapse1.4%
997Tricuspid Valve Prolapse1.4%
998Takotsubo Cardiomyopathy1.4%
999Arthrogryposis1.4%
1000Choanal Atresia1.4%
1001Tracheobronchomegaly1.4%
1002Laryngocele1.4%
1003Choledochal Cyst1.3%
1004Hermaphroditism1.3%
1005Disorders of Sex Development1.3%
1006Cryptorchidism1.3%
1007Hypospadias1.3%
1008Central Nervous System Cysts1.3%
1009Dandy-Walker Syndrome1.3%
1010POEMS Syndrome1.3%
1011Kearns-Sayre syndrome1.3%
1012Nesidioblastosis1.3%
1013Amelia1.2%
1014Arachnodactyly1.2%
1015Ectromelia1.2%
1016Hemimelia1.2%
1017Meningomyelocele1.2%
1018Phocomelia1.2%
1019Sirenomelia1.2%
1020Spina Bifida1.2%
1021Polydactyly1.2%
1022Brachydactyly1.2%
1023Plagiocephaly1.2%
1024Lower Extremity Deformities, Congenital1.2%
1025Upper Extremity Deformities, Congenital1.2%
1026Sinus Arrest, Cardiac1.2%
1027Bladder Exstrophy1.2%
1028Epispadias1.2%
1029Multicystic Dysplastic Kidney1.2%
1030Angle Closure Glaucoma1.2%
1031Glaucoma, Open-Angle1.2%
1032Macular degeneration1.2%
1033Retinal Drusen1.2%
1034Retinal Necrosis Syndrome, Acute1.2%
1035Retinoschisis1.2%
1036Hyperandrogenism1.2%
1037Opsoclonus-Myoclonus Syndrome1.2%
1038Kernicterus1.1%
1039Hyaline Membrane Disease1.1%
1040Meningocele1.1%
1041Encephalocele1.1%
1042Craniofacial Dysostosis1.1%
1043Miller Fisher Syndrome1.1%
1044Esotropia1%
1045Exotropia1%
1046Dermal Sinus1%
1047Spina Bifida Cystica1%
1048Spina Bifida Occulta1%
1049Lissencephaly1%
1050Polymicrogyria1%
1051Pachygyria1%
1052Schizencephaly1%
1053Periventricular Nodular Heterotopia1%
1054Platybasia1%
1055Gonadal Dysgenesis1%
1056Adrenogenital Syndrome1%
1057Ovotesticular Disorders of Sex Development1%
1058Herpes Zoster Ophthalmicus0.9%
1059Hemianopsia0.9%
1060Amaurosis Fugax0.9%
1061Blindness, Cortical0.9%
1062Graves Disease0.8%
1063Horner Syndrome0.8%
1064Goldenhar Syndrome0.8%
1065Talipes0.7%
1066Congenital clubfoot0.7%
1067Vertical Talus0.7%
1068Ophthalmoplegic Migraine0.6%
1069Progressive supranuclear palsy0.6%
1070Neuromyelitis Optica0.6%
1071Optic Nerve Glioma0.5%
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