MetaADEDB 2.0 @ LMMD
Retinoblastoma
(UMLS:C0035335)
Definition:
A malignant tumor arising from the nuclear layer of the retina that is the most common primary tumor of the eye in children. The tumor tends to occur in early childhood or infancy and may be present at birth. The majority are sporadic, but the condition may be transmitted as an autosomal dominant trait. Histologic features include dense cellularity, small round polygonal cells, and areas of calcification and necrosis. An abnormal pupil reflex (leukokoria); NYSTAGMUS, PATHOLOGIC; STRABISMUS; and visual loss represent common clinical characteristics of this condition. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2104)
UMLS ID:
C0035335
MeSH ID:
D012175
Classification 1:
Name:
Neoplasms
MeSH Tree Number(s):
C04.557.465.625.600.725|C04.557.470.670.725|C04.557.580.625.600.725|C04.588.364.818.760
Classification 2:
Name:
Eye Diseases
MeSH Tree Number(s):
C11.270.862|C11.319.475.760|C11.768.717.760
Synonym(s)
1.
Retinoblastoma
2.
Neuroblastoma of Retina
3.
Neuroblastoma of the Retina
4.
RB
5.
RB - Retinoblastoma
6.
RETINA, GLIOMA
7.
RETINOBLASTOMA
8.
RETINOBLASTOMA, MALIGNANT
9.
Retinal Neuroblastoma
10.
Retinoblastoma - morphology
Associated Drug(s)
NameNumber of ReportsReference(s)Data Source
1CarboplatinFAERS: 3

View details

CTD
US FAERS
2Estrogens, Conjugated (USP)FAERS: 1US FAERS
3OctreotideFAERS: 1US FAERS
4VerteporfinFAERS: 1US FAERS
5ZidovudineFAERS: 1US FAERS
6Calcitriol3355424
10088815
CTD
7Cyclophosphamide9616283CTD
8DidanosineOFFSIDES
9Etoposide9616283CTD
10Methylnitrosourea11555667CTD
11NevirapineOFFSIDES
12Ro 23-755310088815
15364716
CTD
13TopotecanCanada Vigilance: 1Canada Vigilance
Similar ADE(s)
NameSemantic Similarity
1Medulloblastoma45.2%
2Ganglioneuroma39.4%
3Glioma39.4%
4Malignant Glioma39.4%
5Astrocytoma29.5%
6Ependymoma29.5%
7oligodendroglioma29.5%
8Ganglioglioma29.5%
9gliosarcoma29.5%
10Anaplastic astrocytoma29.5%
11Anaplastic Oligodendroglioma29.5%
12Uveal Neoplasms27.1%
13Craniopharyngioma25.5%
14Neuroectodermal Tumor, Melanotic25.5%
15Neuroendocrine Tumors25.5%
16Retinal Degeneration25.3%
17Retinal Dysplasia24.6%
18Glioblastoma24.6%
19Neuroblastoma24.6%
20Glioblastoma Multiforme24.6%
21melanoma24.5%
22Adenoma, Acidophil23.8%
23Optic Nerve Glioma22.7%
24Ganglioneuroblastoma22.2%
25Carcinoid Tumor21.5%
26Meningioma21.5%
27Eyelid Neoplasms21%
28Neurilemmoma20.8%
29Melanoma, Experimental19.9%
30leukemia19.5%
31Aniridia19.5%
32Trophoblastic Neoplasms18.6%
33Basal cell carcinoma18.2%
34Carcinoma, Papillary18.2%
35Squamous cell carcinoma18.2%
36Cystadenoma18.2%
37Mesothelioma18.2%
38Carcinoma, Basal Cell18.2%
39Carcinoma, Lobular17.8%
40Hutchinson's Melanotic Freckle17.6%
41Melanoma, Amelanotic17.6%
42Retinitis Pigmentosa17.5%
43Pigmentary retinopathy17.5%
44Paraganglioma17.4%
45Histiocytic Disorders, Malignant17.3%
46Retinal Hemorrhage17.3%
47Duane Retraction Syndrome17%
48Malignant Carcinoid Syndrome16.7%
49Carcinoma, Ehrlich Tumor16.2%
50Carcinoma, Lewis Lung16.2%
51Composite Lymphoma16.1%
52Carcinosarcoma16.1%
53Hemangiosarcoma16.1%
54lymphangiosarcoma16.1%
55Adenoma16%
56Carcinoma16%
57Epithelioma16%
58Carcinoma 256, Walker15.8%
59Lymphoma15.6%
60Cystadenocarcinoma15.6%
61Mucoepidermoid Carcinoma15.6%
62Retinoblastoma15.5%
63Choriocarcinoma15.5%
64Dermoid Cyst15.4%
65Multiple Endocrine Neoplasia15.4%
66Acanthoma15.3%
67Leukemia, Experimental15.2%
68Chordoma15.2%
69Teratoma15.2%
70Germinoma15.2%
71Teratocarcinoma15.2%
72Hamartoma14.8%
73Neoplasms, Hormone-Dependent14.8%
74Neoplasms, Multiple Primary14.8%
75Paraneoplastic Syndromes14.8%
76Precancerous Conditions14.8%
77Neoplasms, Second Primary14.8%
78Leukemia, Plasma Cell14.4%
79Neuroectodermal Tumors14.3%
80Neoplasms, Neuroepithelial14.1%
81Gliomatosis cerebri14.1%
82Acoustic Neuroma14%
83Leukemia, Radiation-Induced13.9%
84Neoplasms, Germ Cell and Embryonal13.9%
85Germ Cell Cancer13.9%
86Color blindness13.8%
87Chorioretinitis13.7%
88Eye Neoplasms13.6%
89Asthenopia13.5%
90Conjunctival Diseases13.5%
91Corneal Diseases13.5%
92Eyelid Diseases13.5%
93Lacrimal Apparatus Diseases13.5%
94Lens Diseases13.5%
95Ocular Hypertension13.5%
96Ocular Hypotension13.5%
97Scleral Diseases13.5%
98Vitreous Detachment13.5%
99Posterior Vitreous Detachment13.5%
100Pheochromocytoma13.4%
101Blepharophimosis13.4%
102Angioid Streaks13.3%
103Neoplasms, Glandular and Epithelial13.3%
104Retinal Detachment13.3%
105Retinitis13.3%
106Cyst13.2%
107Neoplastic Processes13.2%
108Neoplastic Syndromes, Hereditary13.2%
109Pregnancy Complications, Neoplastic13.2%
110Carcinoid Heart Disease13.1%
111Neoplasms, Experimental13.1%
112Bowen's Disease13%
113Carcinoma, Pancreatic Ductal12.7%
114Xerophthalmia12.5%
115Low Tension Glaucoma12.5%
116Iridocorneal endothelial syndrome12.5%
117Adenofibroma12.5%
118Fibroadenoma12.5%
119Thymoma12.5%
120Chondrosarcoma12.4%
121leiomyosarcoma12.4%
122liposarcoma12.4%
123synovial sarcoma12.4%
124Angiomyolipoma12.4%
125Clear Cell Sarcoma of Soft Tissue12.4%
126Alveolar Soft Part Sarcoma12.4%
127Sarcoma, Myeloid12.4%
128Basal Cell Nevus Syndrome12.3%
129Eye Abnormalities12.1%
130Eye Infection12.1%
131Eye Manifestations12.1%
132Optic Neuropathy12.1%
133Corneal Scar12%
134Paraneoplastic Encephalomyelitis12%
135Abdominal Neoplasms12%
136Head and Neck Neoplasms12%
137Soft Tissue Neoplasms12%
138Thoracic Neoplasms12%
139Tuberous Sclerosis11.9%
140Mammary Neoplasms, Experimental11.9%
141Sarcoma, Experimental11.9%
142Neoplasms, Radiation-Induced11.8%
143Retinal Artery Occlusion11.8%
144Retinopathy of Prematurity11.8%
145Retinal Vasculitis11.8%
146Hypertensive Retinopathy11.8%
147Keratoconjunctivitis Sicca11.8%
148Nephroblastoma11.8%
149Retinal Neovascularization11.8%
150Endometrial Stromal Sarcoma11.5%
151Vipoma11.3%
152Corneal Ulcer11.3%
153Choroid Hemorrhage11.3%
154Ameloblastoma11.1%
155Angiokeratoma11.1%
156Hemangioma11.1%
157hemangiopericytoma11.1%
158Lymphangioma11.1%
159Mesenchymoma11.1%
160Nevus11.1%
161Hepatoblastoma11.1%
162Mixed Tumor, Mullerian11.1%
163Angiofibroma11.1%
164Sarcoma11.1%
165Digestive System Neoplasms10.9%
166Endocrine Gland Neoplasms10.9%
167Nervous System Neoplasms10.9%
168Ocular Motility Disorders10.9%
169Cyclophoria10.9%
170Pupil Disorders10.8%
171Cytomegalovirus Retinitis10.8%
172Bone neoplasms10.8%
173Skin Neoplasms10.8%
174Hematologic Neoplasms10.8%
175Eye Hemorrhage10.8%
176Hepatocellular Adenoma10.7%
177Vision Disorders10.7%
178Metamorphopsia10.7%
179Visual Impairment10.7%
180Eye Injuries10.7%
181Splenic Neoplasms10.7%
182Retinal Vein Occlusion10.6%
183Diabetic Retinopathy10.6%
184Trachoma10.6%
185Fibrosarcoma10.5%
186Osteosarcoma10.5%
187Parathyroid Neoplasms10.3%
188Peritoneal Neoplasms10.3%
189Thyroid Neoplasm10.3%
190Thyroid carcinoma10.3%
191Keratoconjunctivitis10.3%
192Adenocarcinoma10.2%
193Carcinoma in Situ10.2%
194Carcinoma, Transitional Cell10.2%
195Papilloma10.2%
196Pseudomyxoma Peritonei10.2%
197Papillomatosis10.2%
198Adenomatosis, Pulmonary10.2%
199Adenomatous Polyps10.2%
200Carcinoma, Large Cell10.2%
201Carcinoma, Small Cell10.2%
202Hordeolum10.2%
203Leukemia L121010.2%
204Leukemia P38810.2%
205Neurofibrosarcoma10.1%
206Lymphangioleiomyomatosis10.1%
207Pars Planitis10%
208Opsoclonus-Myoclonus Syndrome9.9%
209Plasmacytoma9.9%
210Malignant histiocytosis9.9%
211Histiocytic sarcoma9.9%
212Prolactinoma9.8%
213Growth Hormone-Secreting Pituitary Adenoma9.8%
214Malignant Fibrous Histiocytoma9.6%
215Pancreatic Neoplasm9.5%
216Dysgerminoma9.4%
217Neuroma9.4%
218Seminoma9.4%
219Retinal Diseases9.3%
220Aicardi's syndrome9.2%
221Lymphomatoid Granulomatosis9.2%
222Macular degeneration9.1%
223Retinal Drusen9.1%
224Retinal Necrosis Syndrome, Acute9.1%
225Retinoschisis9.1%
226Multiple Endocrine Neoplasia Type 19%
227Carcinoma, Ovarian Epithelial9%
228Adenomatous Polyposis Coli8.9%
229Hodgkin Disease8.9%
230Lymphoma, Non-Hodgkin8.9%
231Mesoblastic Nephroma8.8%
232Rhabdomyosarcoma8.7%
233Giant Cell Tumor of Bone8.7%
234CHARGE Syndrome8.6%
235Optic Atrophy, Hereditary, Leber8.6%
236Choroiditis8.6%
237Iridocyclitis8.6%
238Iritis8.6%
239Albinism8.5%
240insulinoma8.5%
241Tracheal Neoplasms8.5%
242Acanthamoeba Keratitis8.5%
243Keratitis, Herpetic8.4%
244Bacterial conjunctivitis8.4%
245Sarcoma 1808.4%
246Corneal Perforation8.3%
247Anisometropia8.3%
248Aphakia8.3%
249Astigmatism8.3%
250Blepharitis8.3%
251Blepharoptosis8.3%
252Blepharospasm8.3%
253Choroid Diseases8.3%
254Conjunctivitis8.3%
255Corneal edema8.3%
256Corneal Opacity8.3%
257Dacryocystitis8.3%
258Dry Eye Syndromes8.3%
259Ectropion8.3%
260Enophthalmos8.3%
261Entropion8.3%
262Episcleritis8.3%
263Exophthalmos8.3%
264Glaucoma8.3%
265Iris Diseases8.3%
266Keratitis8.3%
267Keratoconus8.3%
268Lacrimal Duct Obstruction8.3%
269Lens dislocation8.3%
270Lens Subluxation8.3%
271Mydriasis8.3%
272Myopia8.3%
273Presbyopia8.3%
274Pterygium8.3%
275Scleritis8.3%
276Uveitis8.3%
277Corneal Neovascularization8.3%
278Orbital Pseudotumor8.3%
279Cataract8.3%
280Pinguecula8.3%
281Trichiasis8.3%
282Liver Neoplasms, Experimental8.3%
283Primary amyloidosis8.1%
284Erythroplasia7.9%
285Follicular cyst7.9%
286Mucocele7.9%
287Pilonidal Cyst7.9%
288Thyroglossal Cyst7.9%
289Synovial Cyst7.9%
290Aberrant Crypt Foci7.9%
291Dermatofibrosarcoma7.8%
292Dermatofibrosarcoma Protuberans7.8%
293Mandibulofacial Dysostosis7.7%
294Esophageal Neoplasms7.7%
295Panophthalmitis7.7%
296Gastrinoma7.6%
297Glucagonoma7.6%
298neurofibroma7.5%
299Hydatidiform Mole7.5%
300Anophthalmos7.4%
301Endophthalmitis7.4%
302Microphthalmos7.4%
303Optic Atrophy7.4%
304Optic Neuritis7.4%
305Papilledema7.4%
306Pemphigoid, Benign Mucous Membrane7.4%
307Strabismus7.4%
308Tolosa-Hunt Syndrome7.4%
309Orbital Cellulitis7.4%
310Retrobulbar Hemorrhage7.4%
311Corneal Endothelial Cell Loss7.4%
312Adenoid Cystic Carcinoma7.4%
313Adenocarcinoma, Clear Cell7.4%
314Cholangiocarcinoma7.4%
315Cervical Intraepithelial Neoplasia7.4%
316Hyphema7.4%
317Vitreous Hemorrhage7.4%
318Nasopharyngeal carcinoma7.3%
319Testicular Neoplasms7.1%
320Leukoplakia7.1%
321Lymphocele7.1%
322Pancreatic Cyst7.1%
323Adrenocortical carcinoma7%
324granulosa cell tumor7%
325Barrett Esophagus7%
326Breast Cyst7%
327Actinic keratosis7%
328Mediastinal Cyst7%
329Neoplasm Invasiveness7%
330Neoplasm Metastasis7%
331Neoplasm Recurrence, Local7%
332Parovarian Cyst7%
333Pericardial Cyst7%
334Thymic Cyst7%
335Carcinogenesis7%
336Myxoid cyst7%
337Metastasis7%
338Retroperitoneal Neoplasms7%
339Phyllodes Tumor7%
340Hemangioendothelioma7%
341Lipoma7%
342Myoma7%
343Myxoma7%
344Angiolipoma7%
345Myelolipoma7%
346Neoplasms, Bone Tissue7%
347Neoplasms, Fibrous Tissue7%
348Smooth Muscle Tumor7%
349Desmoplastic Small Round Cell Tumor7%
350Chondroma7%
351Enchondroma7%
352Alveolar rhabdomyosarcoma6.9%
353Waldenstrom Macroglobulinemia6.8%
354Multiple Myeloma6.8%
355Optic Neuropathy, Ischemic6.7%
356Anterior Ischemic Optic Neuropathy6.7%
357Anisocoria6.6%
358Tonic Pupil6.6%
359Eye pain6.6%
360Orbital Myositis6.6%
361Diplopia6.6%
362Scotoma6.6%
363Photophobia6.6%
364Amaurosis6.6%
365Blindness6.6%
366Leukoplakia, Oral6.6%
367Thyroid Nodule6.6%
368Paraneoplastic Cerebellar Degeneration6.6%
369Renal Cell Carcinoma6.5%
370Papillary Renal Cell Carcinoma6.5%
371Corpus Luteum Cyst6.3%
372Ovarian Cysts6.3%
373Mouth Neoplasms6.3%
374Central Nervous System Neoplasms6.3%
375Vascular Neoplasms6.3%
376Thymus Neoplasms6.3%
377Genital Neoplasms, Female6.2%
378Breast Neoplasms, Male6.2%
379Triple Negative Breast Neoplasms6.2%
380Leukemia, Myelomonocytic, Chronic6.2%
381Leukemia, Myeloid, Chronic, Atypical, BCR-ABL Negative6.2%
382Leydig Cell Tumor6.1%
383Carcinoma, Endometrioid6.1%
384Ophthalmoplegia6%
385External Ophthalmoplegia6%
386Limbic Encephalitis6%
387Amblyopia6%
388Klatskin Tumor5.9%
389Denys-Drash Syndrome5.9%
390Choledochal Cyst5.8%
391Angle Closure Glaucoma5.8%
392Glaucoma, Open-Angle5.8%
393Panuveitis5.8%
394Exfoliation Syndrome5.8%
395Peutz-Jeghers Syndrome5.7%
396Adrenal Gland Neoplasms5.7%
397Gastrointestinal Neoplasms5.7%
398Genital Neoplasms, Male5.7%
399Liver neoplasms5.7%
400Urologic Neoplasms5.6%
401Mastocytosis5.6%
402Sturge-Weber Syndrome5.6%
403Lambert-Eaton Myasthenic Syndrome5.6%
404Sebaceous Gland Neoplasms5.6%
405Spinal Neoplasms5.6%
406Bone Marrow Neoplasms5.6%
407Gastrointestinal Stromal Tumors5.6%
408Hemangioma, Cavernous5.6%
409Leukemia, T-Cell5.6%
410Leukemia, B-Cell5.6%
411Ophthalmia Neonatorum5.5%
412Lymphoma, Follicular5.5%
413T-Cell Lymphoma5.5%
414Mantle cell lymphoma5.5%
415Alstrom Syndrome5.3%
416Nose Neoplasms5.3%
417Esotropia5.1%
418Exotropia5.1%
419Choroidal Neovascularization5.1%
420Pituitary Adenoma5%
421Pituitary Neoplasms5%
422fibroma4.9%
423Fibromatosis4.9%
424Osteoblastoma4.9%
425Osteoma4.9%
426Rhabdomyoma4.9%
427Chondromatosis4.9%
428Hemangioblastoma4.9%
429Lymphoma, Extranodal NK-T-Cell4.9%
430Kearns-Sayre syndrome4.9%
431Myelitis, Transverse4.8%
432Palatal Neoplasms4.8%
433ovarian neoplasm4.7%
434Uveomeningoencephalitic Syndrome4.7%
435Congenital nystagmus4.6%
436Herpes Zoster Ophthalmicus4.6%
437Hemianopsia4.6%
438Amaurosis Fugax4.6%
439Blindness, Cortical4.6%
440Anterior uveitis4.5%
441Uveitis, Posterior4.5%
442Mastocytoma4.4%
443Miller Fisher Syndrome4.4%
444Mastocytosis, Systemic4.4%
445Leukemia, Myeloid, Chronic-Phase4.3%
446Graves Disease4.2%
447Xeroderma Pigmentosum4.2%
448Horner Syndrome4.2%
449Pancreatic Pseudocyst4%
450Lymphatic Metastasis4%
451Meningeal Neoplasms4%
452Neoplasms, Unknown Primary4%
453Leukemic Infiltration4%
454Neoplasm Micrometastasis4%
455Precursor B-Cell Lymphoblastic Leukemia-Lymphoma3.9%
456Leukemia, Large Granular Lymphocytic3.9%
457Precursor T-Cell Lymphoblastic Leukemia-Lymphoma3.9%
458Lymphoma, T-Cell, Cutaneous3.9%
459Lymphoma, AIDS-Related3.9%
460Enteropathy-Associated T-Cell Lymphoma3.9%
461Primary Effusion Lymphoma3.9%
462Fibromatosis, Aggressive3.9%
463Fibromatosis, Abdominal3.9%
464Ear Neoplasms3.7%
465Lung Neoplasms3.7%
466Pleural Neoplasms3.7%
467Brain Neoplasms3.6%
468Salivary Gland Neoplasms3.6%
469Spinal Cord Neoplasms3.6%
470Tongue Neoplasms3.6%
471Polycystic Ovary Syndrome3.6%
472Uterine Neoplasms3.6%
473Vaginal Neoplasms3.6%
474Vulvar Neoplasms3.6%
475Uterine Cancer3.6%
476Fallopian Tube Neoplasms3.6%
477Sicca Syndrome3.5%
478Sjogren's Syndrome3.5%
479Pharyngeal Neoplasms3.4%
480Central Nervous System Cysts3.3%
481Ophthalmoplegic Migraine3.3%
482Bile Duct Neoplasms3.3%
483gallbladder neoplasm3.3%
484Intestinal Neoplasms3.3%
485Penile Neoplasms3.3%
486Prostatic Neoplasms3.3%
487Stomach Neoplasms3.3%
488Progressive supranuclear palsy3.3%
489Polycythemia Vera3.3%
490Burkitt Lymphoma3.3%
491Dupuytren Contracture3.1%
492Urticaria Pigmentosa3.1%
493Laryngeal neoplasm3.1%
494Mycosis Fungoides3.1%
495Lymphomatoid Papulosis3.1%
496Plasmablastic lymphoma3.1%
497Neuromyelitis Optica3.1%
498Bladder Neoplasm3%
499Kidney Neoplasm3%
500Ureteral Neoplasms3%
501Urethral Neoplasms3%
502Meningeal Carcinomatosis2.9%
503Bronchial Neoplasms2.6%
504Multiple Pulmonary Nodules2.6%
505Supratentorial Neoplasms2.6%
506Endometrial Neoplasms2.6%
507Zollinger-Ellison syndrome2.6%
508Sezary Syndrome2.6%
509Behcet Syndrome2.4%
510Hypopharyngeal Neoplasms2.4%
511Pleural Effusion, Malignant2.4%
512Hypopharyngeal Cancer2.4%
513Parotid Neoplasms2.4%
514Prostatic Neoplasms, Castration-Resistant2.4%
515Nelson Syndrome2.4%
516Cell Transformation, Viral2.3%
517Cecal Neoplasms2.2%
518Duodenal Neoplasms2.2%
519Brain Stem Neoplasms2.1%
520Nasopharyngeal Neoplasms2%
521Colorectal Neoplasms2%
522Tonsillar Neoplasms1.9%
523Cerebellar Neoplasms1.9%
524Paranasal Sinus Neoplasms1.9%
525Choroid Plexus Papilloma1.9%
526Appendiceal Neoplasms1.8%
527Colonic Neoplasms1.8%
528Rectal Neoplasms1.8%
529Maxillary Sinus Neoplasms1.5%
530Anus Neoplasms1.4%
531Sigmoid Neoplasms1.4%
532Radicular Cyst1.1%
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