MetaADEDB 2.0 @ LMMD
Hamman-Rich syndrome
(UMLS:C0085786)
Definition:
Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
UMLS ID:
C0085786
MeSH ID:
D011658
Classification:
Name:
Respiratory Tract Diseases
MeSH Tree Number(s):
C08.381.765
Synonym(s)
1.
Hamman-Rich syndrome
2.
DIPF - Diffuse interstitial pulmonary fibrosis
3.
Diffuse idiopathic pulmonary fibrosis
4.
Diffuse interstitial pulmonary fibrosis
5.
Fibrosing alveolitis
6.
Hamman Rich syndrome
7.
IDIOPATHIC FIBROSING ALVEOLITIS
8.
Idiopathic fibrosing alveolitis
9.
Idiopathic interstitial fibrosis of lung syndrome
10.
Idiopathic interstitial pneumonia
11.
UIP - Usual interstitial pneumonitis
12.
Usual interstitial pneumonitis
13.
hamman rich syndrome
14.
hamman-Rich syndrome
15.
hamman-rich syndrome
16.
idiopathic fibrosing alveolitis
Associated Drug(s)
NameNumber of ReportsReference(s)Data Source
1AmiodaroneSIDER
2BleomycinSIDER
3MesalamineSIDER
4SulfasalazineSIDER
5ValsartanSIDER
Similar ADE(s)
NameSemantic Similarity
1Atelectasis42.9%
2Pulmonary Hypertension42.9%
3Pulmonary Alveolar Proteinosis42.9%
4Pulmonary Edema42.9%
5Lung Diseases, Interstitial42.9%
6Lung Diseases, Obstructive42.9%
7Pneumonia38.1%
8Lobar Pneumonia38.1%
9Respiratory Distress Syndrome, Adult38.1%
10Pneumonitis38.1%
11Pneumoconiosis32.1%
12Chronic Obstructive Airway Disease31%
13Middle Lobe Syndrome31%
14Acute Lung Injury31%
15Bronchitis29.8%
16Lung Diseases, Fungal28.6%
17Lung Injury28.6%
18Hepatopulmonary Syndrome28.6%
19Respiratory Distress Syndrome, Newborn28.1%
20Bronchitis, Chronic28%
21Lung Abscess27.8%
22Lung Neoplasms27.8%
23Tuberculosis, Pulmonary27.6%
24Bronchopneumonia27.6%
25Pulmonary Embolism27.6%
26Pulmonary Eosinophilia27.4%
27Eosinophilic Pneumonia27.4%
28Aspiration Pneumonia27.3%
29Asbestosis25.4%
30Berylliosis25.4%
31Pulmonary Emphysema25.4%
32Silicosis25.4%
33Radiation Pneumonitis24.5%
34Radiation Fibrosis24.5%
35Pleuropneumonia24.3%
36Asthma23.4%
37Bronchial Diseases23.1%
38Pleural Diseases23.1%
39Respiration Disorders23.1%
40Thoracic Diseases23.1%
41Tracheal Diseases23.1%
42Bronchiolitis22.7%
43Pneumonia, Lipid22.2%
44Pneumonia, Viral21.4%
45Persistent Fetal Circulation Syndrome20.9%
46Pneumonia, Bacterial20.7%
47Hemoptysis20.7%
48Histiocytosis, Langerhans-Cell20.5%
49Pulmonary Aspergillosis20.5%
50Bronchopulmonary Aspergillosis20.5%
51Bronchiolitis Obliterans20.4%
52Sarcoidosis, Pulmonary20.2%
53Hyaline Membrane Disease20.2%
54Pulmonary Infarction20.1%
55Multiple Pulmonary Nodules20.1%
56Pleurisy19%
57Tracheitis19%
58Cystic Fibrosis17.1%
59Tracheobronchomegaly16.9%
60Bronchopulmonary Dysplasia16.9%
61Idiopathic Pulmonary Fibrosis16.9%
62Aspergillosis, Allergic Bronchopulmonary16.2%
63Laryngeal Diseases15.8%
64Nose Diseases15.8%
65Scimitar Syndrome15.8%
66Acute Chest Syndrome15.3%
67Meconium Aspiration Syndrome15.1%
68Granulomatosis with polyangiitis15.1%
69Respiratory Tract Infections15%
70Granuloma, Respiratory Tract14.6%
71Respiratory Hypersensitivity14.6%
72Respiratory Tract Fistula14.6%
73Altitude Sickness14.3%
74Bronchospasm14.3%
75Bronchiectasis14.3%
76Chylothorax14.3%
77Hydropneumothorax14.3%
78Hydrothorax14.3%
79Laryngitis14.3%
80Pneumothorax14.3%
81Respiratory Insufficiency14.3%
82Rhinitis14.3%
83Tracheal Stenosis14.3%
84Bronchial Hyperreactivity14.3%
85Respiratory Depression14.3%
86Vocal Cord Dysfunction14.3%
87Respiratory Failure14.3%
88Farmer's Lung14.1%
89Bronchial Fistula13.9%
90Pleural Neoplasms13.9%
91Transfusion-Related Acute Lung Injury12.8%
92Granuloma, Laryngeal12.7%
93Invasive Pulmonary Aspergillosis12.5%
94Sinusitis12.1%
95Anti-Glomerular Basement Membrane Disease12.1%
96Pleural Effusion, Malignant12%
97Bronchial Neoplasms11.9%
98Blastomycosis11.4%
99Choanal Atresia11.3%
100Laryngocele11.3%
101Tracheal Neoplasms11%
102Airway Obstruction10.3%
103Choking10.3%
104Epiglottitis10.3%
105Mediastinitis10.3%
106Laryngospasm10.2%
107Asthma, Exercise-Induced10%
108Status Asthmaticus10%
109Granuloma, Lethal Midline9.5%
110Laryngeal Edema9.5%
111Nose Deformities, Acquired9.5%
112Respiratory Aspiration9.5%
113Laryngeal neoplasm9.4%
114Apnea9.3%
115Cheyne-Stokes Respiration9.3%
116Common Cold9.3%
117Dyspnea9.3%
118Hemothorax9.3%
119Hyperventilation9.3%
120Influenza9.3%
121Mouth Breathing9.3%
122Tachypnea9.3%
123Catarrh9.3%
124Severe Acute Respiratory Syndrome9.1%
125Laryngopharyngeal Reflux9.1%
126Primary Ciliary Dyskinesia8.8%
127Eosinophilic Granuloma8.4%
128Asthma, Occupational8.4%
129Paranasal Sinus Neoplasms7.5%
130Hay fever7.3%
131Rhinitis, Allergic, Perennial7.3%
132Pharyngitis7.1%
133Laryngostenosis7%
134Nasal Polyps7%
135Mediastinal Cyst7%
136Pericardial Cyst7%
137Thymic Cyst7%
138Nose Neoplasms6.9%
139Pertussis6.8%
140Croup6.8%
141Mediastinal Emphysema6.8%
142Rhinitis, Vasomotor6.8%
143Hypoventilation6.8%
144Rhinoscleroma6.8%
145Hoarseness6.8%
146Acidosis, Respiratory6.7%
147Alkalosis, Respiratory6.7%
148Sleep Apnea Syndromes6.7%
149Asthma, Aspirin-Induced6.7%
150Maxillary Sinus Neoplasms6.1%
151Kartagener Syndrome5.7%
152Voice Disorders5.6%
153Voice Disturbance5.6%
154Epistaxis5.6%
155Sleep Apnea, Obstructive5.5%
156Sleep Apnea, Central5.5%
157Tonsillitis5.1%
158Dyspnea, Paroxysmal5%
159Respiratory Paralysis5%
160Laryngomalacia4.7%
161Vocal Cord Paralysis4.6%
162Aphonia4%
163Retropharyngeal Abscess4%
164Dysphonia4%
165Bronchomalacia4%
166Tracheomalacia4%
167Nasopharyngitis3.4%
168Peritonsillar Abscess3.3%
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